A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation
Amyloid light (AL) amyloidosis, also known as primary systemic amyloidosis, is a protein conformation disease, and is a clinical syndrome of functional failure of affected organs due to abnormal folding and deposition of insoluble fibrin in the extracellular region of organs or tissues. The diagnosi...
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| Format: | Article |
| Language: | zho |
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Editorial Office of New Medicine
2023-08-01
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| Series: | Yixue xinzhi zazhi |
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| Online Access: | https://yxxz.whuznhmedj.com/futureApi/storage/attach/2308/f2cqkUDC8STeHiQiEMfgyLPId0oQtRXyAYTQQLGe.pdf |
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| _version_ | 1850242747873624064 |
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| author | Ya-Nan CHEN Jia-Long LIU Yi-Zhang LI Ji-Xia ZHANG Xian-Yan SHI Jing LIU |
| author_facet | Ya-Nan CHEN Jia-Long LIU Yi-Zhang LI Ji-Xia ZHANG Xian-Yan SHI Jing LIU |
| author_sort | Ya-Nan CHEN |
| collection | DOAJ |
| description | Amyloid light (AL) amyloidosis, also known as primary systemic amyloidosis, is a protein conformation disease, and is a clinical syndrome of functional failure of affected organs due to abnormal folding and deposition of insoluble fibrin in the extracellular region of organs or tissues. The diagnosis of AL-type amyloidosis is challenging because of its low incidence and complex clinical manifestations, and cases of multiple organ involvement are even rarer. We reported a case of AL-type amyloidosis with multiple organ involvement in order to provide refference for related diagnosis, treatment and prognosis. |
| format | Article |
| id | doaj-art-bff432fb98d14d9cb71b14ff1fcd0a67 |
| institution | OA Journals |
| issn | 1004-5511 |
| language | zho |
| publishDate | 2023-08-01 |
| publisher | Editorial Office of New Medicine |
| record_format | Article |
| series | Yixue xinzhi zazhi |
| spelling | doaj-art-bff432fb98d14d9cb71b14ff1fcd0a672025-08-20T02:00:13ZzhoEditorial Office of New MedicineYixue xinzhi zazhi1004-55112023-08-0133428529010.12173/j.issn.1004-5511.2022090546404A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestationYa-Nan CHENJia-Long LIUYi-Zhang LIJi-Xia ZHANGXian-Yan SHIJing LIUAmyloid light (AL) amyloidosis, also known as primary systemic amyloidosis, is a protein conformation disease, and is a clinical syndrome of functional failure of affected organs due to abnormal folding and deposition of insoluble fibrin in the extracellular region of organs or tissues. The diagnosis of AL-type amyloidosis is challenging because of its low incidence and complex clinical manifestations, and cases of multiple organ involvement are even rarer. We reported a case of AL-type amyloidosis with multiple organ involvement in order to provide refference for related diagnosis, treatment and prognosis.https://yxxz.whuznhmedj.com/futureApi/storage/attach/2308/f2cqkUDC8STeHiQiEMfgyLPId0oQtRXyAYTQQLGe.pdfamyloidosislight chain amyloidosismultiple organ involvement |
| spellingShingle | Ya-Nan CHEN Jia-Long LIU Yi-Zhang LI Ji-Xia ZHANG Xian-Yan SHI Jing LIU A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation Yixue xinzhi zazhi amyloidosis light chain amyloidosis multiple organ involvement |
| title | A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation |
| title_full | A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation |
| title_fullStr | A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation |
| title_full_unstemmed | A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation |
| title_short | A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation |
| title_sort | case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation |
| topic | amyloidosis light chain amyloidosis multiple organ involvement |
| url | https://yxxz.whuznhmedj.com/futureApi/storage/attach/2308/f2cqkUDC8STeHiQiEMfgyLPId0oQtRXyAYTQQLGe.pdf |
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