A case of amyloid light amyloidosis involving multiorgan with hepatomegaly as the main manifestation

Amyloid light (AL) amyloidosis, also known as primary systemic amyloidosis, is a protein conformation disease, and is a clinical syndrome of functional failure of affected organs due to abnormal folding and deposition of insoluble fibrin in the extracellular region of organs or tissues. The diagnosi...

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Bibliographic Details
Main Authors: Ya-Nan CHEN, Jia-Long LIU, Yi-Zhang LI, Ji-Xia ZHANG, Xian-Yan SHI, Jing LIU
Format: Article
Language:zho
Published: Editorial Office of New Medicine 2023-08-01
Series:Yixue xinzhi zazhi
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Online Access:https://yxxz.whuznhmedj.com/futureApi/storage/attach/2308/f2cqkUDC8STeHiQiEMfgyLPId0oQtRXyAYTQQLGe.pdf
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Summary:Amyloid light (AL) amyloidosis, also known as primary systemic amyloidosis, is a protein conformation disease, and is a clinical syndrome of functional failure of affected organs due to abnormal folding and deposition of insoluble fibrin in the extracellular region of organs or tissues. The diagnosis of AL-type amyloidosis is challenging because of its low incidence and complex clinical manifestations, and cases of multiple organ involvement are even rarer. We reported a case of AL-type amyloidosis with multiple organ involvement in order to provide refference for related diagnosis, treatment and prognosis.
ISSN:1004-5511