Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count

Inflammatory bowel disease (IBD)-like colitis is a known entity in glycogen storage disease (GSD) type 1b patients. The mean age of the reported cases with IBD-like colitis was 12 +/- 5 years, and all had absolute neutrophil count (ANC) less than 1,000 cells/microl. We report a three-year-old...

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Main Authors: Inci Nur Saltik-Temizel, Nurten Koçak, Hasan Ozen, Aysel Yüce, Figen Gürakan, Hülya Demir
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2005-04-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/2710
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author Inci Nur Saltik-Temizel
Nurten Koçak
Hasan Ozen
Aysel Yüce
Figen Gürakan
Hülya Demir
author_facet Inci Nur Saltik-Temizel
Nurten Koçak
Hasan Ozen
Aysel Yüce
Figen Gürakan
Hülya Demir
author_sort Inci Nur Saltik-Temizel
collection DOAJ
description Inflammatory bowel disease (IBD)-like colitis is a known entity in glycogen storage disease (GSD) type 1b patients. The mean age of the reported cases with IBD-like colitis was 12 +/- 5 years, and all had absolute neutrophil count (ANC) less than 1,000 cells/microl. We report a three-year-old girl with GSD type 1b that was dignosed by mutation analysis. The patient was hospitalized with fever, diarrhea, and perioral and anal ulcers. Colonoscopy was performed and IBD-like colitis was diagnosed. The patient had elevated platelet count beyond the age of three months, but IBD-like colitis was diagnosed at three years of age. An elevated platelet count may be a warning sign for the IBD-like colitis in young patients with GSD type 1b.
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institution DOAJ
issn 0041-4301
2791-6421
language English
publishDate 2005-04-01
publisher Hacettepe University Institute of Child Health
record_format Article
series The Turkish Journal of Pediatrics
spelling doaj-art-bfaec0de197d49ea8d39dcad757b95b52025-08-20T02:55:24ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212005-04-01472Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet countInci Nur Saltik-Temizel0Nurten KoçakHasan OzenAysel YüceFigen GürakanHülya DemirSection of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara, Turkey. Inflammatory bowel disease (IBD)-like colitis is a known entity in glycogen storage disease (GSD) type 1b patients. The mean age of the reported cases with IBD-like colitis was 12 +/- 5 years, and all had absolute neutrophil count (ANC) less than 1,000 cells/microl. We report a three-year-old girl with GSD type 1b that was dignosed by mutation analysis. The patient was hospitalized with fever, diarrhea, and perioral and anal ulcers. Colonoscopy was performed and IBD-like colitis was diagnosed. The patient had elevated platelet count beyond the age of three months, but IBD-like colitis was diagnosed at three years of age. An elevated platelet count may be a warning sign for the IBD-like colitis in young patients with GSD type 1b. https://turkjpediatr.org/article/view/2710
spellingShingle Inci Nur Saltik-Temizel
Nurten Koçak
Hasan Ozen
Aysel Yüce
Figen Gürakan
Hülya Demir
Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count
The Turkish Journal of Pediatrics
title Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count
title_full Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count
title_fullStr Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count
title_full_unstemmed Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count
title_short Inflammatory bowel disease-like colitis in a young Turkish child with glycogen storage disease type 1b and elevated platelet count
title_sort inflammatory bowel disease like colitis in a young turkish child with glycogen storage disease type 1b and elevated platelet count
url https://turkjpediatr.org/article/view/2710
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