Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report

This case report discusses a rare instance of Nerve Sheath Myxoma (NSM), a benign tumour originating from peripheral nerve Schwann cells. While typically found in the distal extremities, this case involved a 10-year-old girl with a mass in the parotid region, presenting a unique challenge in diagnos...

Full description

Saved in:
Bibliographic Details
Main Authors: Vandana Malik, Geetika Khanna, Priyadharshini Bargunam, Rohit Bhardwaj
Format: Article
Language:English
Published: Istanbul University Press 2025-03-01
Series:The Turkish Journal of Ear Nose and Throat
Subjects:
Online Access:https://cdn.istanbul.edu.tr/file/JTA6CLJ8T5/00029E8D453B4FE7B40094FDD0C6B428
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850193220785405952
author Vandana Malik
Geetika Khanna
Priyadharshini Bargunam
Rohit Bhardwaj
author_facet Vandana Malik
Geetika Khanna
Priyadharshini Bargunam
Rohit Bhardwaj
author_sort Vandana Malik
collection DOAJ
description This case report discusses a rare instance of Nerve Sheath Myxoma (NSM), a benign tumour originating from peripheral nerve Schwann cells. While typically found in the distal extremities, this case involved a 10-year-old girl with a mass in the parotid region, presenting a unique challenge in diagnosis. Initial clinical assessments suggested a benign salivary gland tumour, but inconclusive FNAC results and conflicting CE-MRI findings led to the excision of the lesion. Histopathological examination revealed a well-circumscribed, multinodular hypocellular myxoid tumour consistent with NSM. Immunohistochem istry confirmed the diagnosis, showing positivity for S100, EMA, Vimentin, and CD34. This study highlights the importance of immunohistochemistry in differentiating NSM from other entities, particularly neu rothekeoma. The treatment of choice is wide local excision with tumour-free margins, and while local recurrences are reported, malignant transformation is undocumented. In conclusion, clinical and imaging techniques may struggle to accurately identify NSM, necessitating reliance on histopathology and immunohistochemistry for diagnosis.
format Article
id doaj-art-bf3b831db4704f6db3a2de64fb8e3d9b
institution OA Journals
issn 2602-4837
language English
publishDate 2025-03-01
publisher Istanbul University Press
record_format Article
series The Turkish Journal of Ear Nose and Throat
spelling doaj-art-bf3b831db4704f6db3a2de64fb8e3d9b2025-08-20T02:14:19ZengIstanbul University PressThe Turkish Journal of Ear Nose and Throat2602-48372025-03-01351596310.26650/Tr-ENT.2025.1472626123456Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case ReportVandana Malik0https://orcid.org/0009-0000-6637-6228Geetika Khanna1https://orcid.org/0000-0002-6021-1171Priyadharshini Bargunam2https://orcid.org/0000-0001-6146-5344Rohit Bhardwajhttps://orcid.org/0000-0003-4005-4719Vardhman Mahavir Medical College and Safdarjung Hospital, New-Delhi, IndiaVardhman Mahavir Medical College and Safdarjung Hospital, New-Delhi, IndiaVardhman Mahavir Medical College and Safdarjung Hospital, New-Delhi, IndiaThis case report discusses a rare instance of Nerve Sheath Myxoma (NSM), a benign tumour originating from peripheral nerve Schwann cells. While typically found in the distal extremities, this case involved a 10-year-old girl with a mass in the parotid region, presenting a unique challenge in diagnosis. Initial clinical assessments suggested a benign salivary gland tumour, but inconclusive FNAC results and conflicting CE-MRI findings led to the excision of the lesion. Histopathological examination revealed a well-circumscribed, multinodular hypocellular myxoid tumour consistent with NSM. Immunohistochem istry confirmed the diagnosis, showing positivity for S100, EMA, Vimentin, and CD34. This study highlights the importance of immunohistochemistry in differentiating NSM from other entities, particularly neu rothekeoma. The treatment of choice is wide local excision with tumour-free margins, and while local recurrences are reported, malignant transformation is undocumented. In conclusion, clinical and imaging techniques may struggle to accurately identify NSM, necessitating reliance on histopathology and immunohistochemistry for diagnosis.https://cdn.istanbul.edu.tr/file/JTA6CLJ8T5/00029E8D453B4FE7B40094FDD0C6B428nerve sheath myxomaneurothekeomaimmunohistochemistryparotid regionhistopathologys100 protein
spellingShingle Vandana Malik
Geetika Khanna
Priyadharshini Bargunam
Rohit Bhardwaj
Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report
The Turkish Journal of Ear Nose and Throat
nerve sheath myxoma
neurothekeoma
immunohistochemistry
parotid region
histopathology
s100 protein
title Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report
title_full Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report
title_fullStr Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report
title_full_unstemmed Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report
title_short Nerve Sheath Myxoma Masquerading as a Parotid Tumor-A Clinical Case Report
title_sort nerve sheath myxoma masquerading as a parotid tumor a clinical case report
topic nerve sheath myxoma
neurothekeoma
immunohistochemistry
parotid region
histopathology
s100 protein
url https://cdn.istanbul.edu.tr/file/JTA6CLJ8T5/00029E8D453B4FE7B40094FDD0C6B428
work_keys_str_mv AT vandanamalik nervesheathmyxomamasqueradingasaparotidtumoraclinicalcasereport
AT geetikakhanna nervesheathmyxomamasqueradingasaparotidtumoraclinicalcasereport
AT priyadharshinibargunam nervesheathmyxomamasqueradingasaparotidtumoraclinicalcasereport
AT rohitbhardwaj nervesheathmyxomamasqueradingasaparotidtumoraclinicalcasereport