The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations

Thoracic aortic disease (TAD) poses substantial risks during pregnancy, particularly for women with genetic conditions such as Marfan syndrome, Loeys-Dietz syndrome, and vascular Ehlers-Danlos syndrome. This review examines the epidemiology, risk assessment, and management of TAD in pregnancy. Preco...

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Main Authors: Valeria E. Duarte, Jessica N. Richardson, Michael N. Singh
Format: Article
Language:English
Published: Houston Methodist DeBakey Heart & Vascular Center 2024-03-01
Series:Methodist DeBakey Cardiovascular Journal
Subjects:
Online Access:https://account.journal.houstonmethodist.org/index.php/up-j-mdbcj/article/view/1371
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author Valeria E. Duarte
Jessica N. Richardson
Michael N. Singh
author_facet Valeria E. Duarte
Jessica N. Richardson
Michael N. Singh
author_sort Valeria E. Duarte
collection DOAJ
description Thoracic aortic disease (TAD) poses substantial risks during pregnancy, particularly for women with genetic conditions such as Marfan syndrome, Loeys-Dietz syndrome, and vascular Ehlers-Danlos syndrome. This review examines the epidemiology, risk assessment, and management of TAD in pregnancy. Preconception counseling is vital considering the hereditary nature of TAD and potential pregnancy-related complications. Genetic testing and imaging surveillance aid in risk assessment. Medical management, including beta-blockade and strict blood pressure control, is essential throughout pregnancy. Surgical interventions may be necessary in certain cases. A multidisciplinary approach involving cardiologists, obstetricians, cardiac surgeons, anesthesiologists, and other specialists with expertise in cardio-obstetrics is essential for optimal outcomes. Patient education and shared decision-making play vital roles in navigating the complexities of TAD in pregnancy and improving maternal and neonatal outcomes.
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series Methodist DeBakey Cardiovascular Journal
spelling doaj-art-bef67205322c405f938d625d25bea45f2025-08-20T03:25:30ZengHouston Methodist DeBakey Heart & Vascular CenterMethodist DeBakey Cardiovascular Journal1947-61082024-03-01202515810.14797/mdcvj.13711348The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management ConsiderationsValeria E. Duarte0https://orcid.org/0000-0001-6616-5412Jessica N. Richardson1https://orcid.org/0009-0006-9960-1261Michael N. Singh2https://orcid.org/0000-0002-8667-9872Houston Methodist DeBakey Heart & Vascular Center, Houston, Texas; Boston Children’s Hospital, Harvard Medical School, Boston, MassachusettsHouston Methodist DeBakey Heart & Vascular Center, Houston, TexasBoston Children’s Hospital, Harvard Medical School, Boston, Massachusetts; Brigham and Women’s Hospital, Harvard Medical School, Boston, MassachusettsThoracic aortic disease (TAD) poses substantial risks during pregnancy, particularly for women with genetic conditions such as Marfan syndrome, Loeys-Dietz syndrome, and vascular Ehlers-Danlos syndrome. This review examines the epidemiology, risk assessment, and management of TAD in pregnancy. Preconception counseling is vital considering the hereditary nature of TAD and potential pregnancy-related complications. Genetic testing and imaging surveillance aid in risk assessment. Medical management, including beta-blockade and strict blood pressure control, is essential throughout pregnancy. Surgical interventions may be necessary in certain cases. A multidisciplinary approach involving cardiologists, obstetricians, cardiac surgeons, anesthesiologists, and other specialists with expertise in cardio-obstetrics is essential for optimal outcomes. Patient education and shared decision-making play vital roles in navigating the complexities of TAD in pregnancy and improving maternal and neonatal outcomes.https://account.journal.houstonmethodist.org/index.php/up-j-mdbcj/article/view/1371pregnancyaortopathymarfancardiovascular genetics
spellingShingle Valeria E. Duarte
Jessica N. Richardson
Michael N. Singh
The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations
Methodist DeBakey Cardiovascular Journal
pregnancy
aortopathy
marfan
cardiovascular genetics
title The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations
title_full The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations
title_fullStr The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations
title_full_unstemmed The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations
title_short The Impact of Pregnancy in Patients with Thoracic Aortic Disease: Epidemiology, Risk Assessment, and Management Considerations
title_sort impact of pregnancy in patients with thoracic aortic disease epidemiology risk assessment and management considerations
topic pregnancy
aortopathy
marfan
cardiovascular genetics
url https://account.journal.houstonmethodist.org/index.php/up-j-mdbcj/article/view/1371
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