A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks

One of the leading thrombocytopenia occasions in childhood is immune thrombocytopenia (ITP). Small number of these patients do not respond to treatment methods known to be effective for ITP such as corticosteroids, intravenous immunoglobulin and thrombopoietin receptor agonists (eltrombopag, romiplo...

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Main Authors: Elif Habibe Aktekin, Serdar Ceylaner, Şeyda Beşen, Ayşe Erbay, Nalan Yazıcı
Format: Article
Language:English
Published: Taylor & Francis Group 2025-12-01
Series:Platelets
Subjects:
Online Access:https://www.tandfonline.com/doi/10.1080/09537104.2025.2500499
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author Elif Habibe Aktekin
Serdar Ceylaner
Şeyda Beşen
Ayşe Erbay
Nalan Yazıcı
author_facet Elif Habibe Aktekin
Serdar Ceylaner
Şeyda Beşen
Ayşe Erbay
Nalan Yazıcı
author_sort Elif Habibe Aktekin
collection DOAJ
description One of the leading thrombocytopenia occasions in childhood is immune thrombocytopenia (ITP). Small number of these patients do not respond to treatment methods known to be effective for ITP such as corticosteroids, intravenous immunoglobulin and thrombopoietin receptor agonists (eltrombopag, romiplostim, etc.) and have serious bleeding symptoms. We present a case in which a molecular genetic analysis was performed due to challenging responses to medical treatment for severe systemic bleeding symptoms which were similar to ITP. A hemizygous variant was detected in the GATA1 gene and a homozygous variant in the ATP2A1 gene for Brody myopathy. Eltrombopag, romiplostim, IVIG and corticosteroid were applied to resistant thrombocytopenia of the patient without knowing the cause. Patient had response in platelet counts in some occasions. This situation attracted our attention after the detection of this GATA variant in the etiopathogenesis of thrombocytopenia. Further investigations should be performed for much more rare causes of thrombocytopenia in patients with refractory thrombocytopenia attacks.
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institution Kabale University
issn 0953-7104
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publishDate 2025-12-01
publisher Taylor & Francis Group
record_format Article
series Platelets
spelling doaj-art-bedabf8ce500428281e98fc6bcadeb702025-08-20T03:48:42ZengTaylor & Francis GroupPlatelets0953-71041369-16352025-12-0136110.1080/09537104.2025.2500499A case with a novel GATA1 variant mimicking immune thrombocytopenia attacksElif Habibe Aktekin0Serdar Ceylaner1Şeyda Beşen2Ayşe Erbay3Nalan Yazıcı4Department of Pediatrics Division of Pediatric Hematology Oncology, Faculty of Medicine, Baskent University, Adana, TürkiyeDepartment of Medical Genetics, Faculty of Medicine, Lokman Hekim University, Ankara, TürkiyeDepartment of Pediatrics Division of Pediatric Neurology, Faculty of Medicine, Baskent University, Adana, TürkiyeDepartment of Pediatrics Division of Pediatric Hematology Oncology, Faculty of Medicine, Baskent University, Adana, TürkiyeDepartment of Pediatrics Division of Pediatric Hematology Oncology, Faculty of Medicine, Baskent University, Adana, TürkiyeOne of the leading thrombocytopenia occasions in childhood is immune thrombocytopenia (ITP). Small number of these patients do not respond to treatment methods known to be effective for ITP such as corticosteroids, intravenous immunoglobulin and thrombopoietin receptor agonists (eltrombopag, romiplostim, etc.) and have serious bleeding symptoms. We present a case in which a molecular genetic analysis was performed due to challenging responses to medical treatment for severe systemic bleeding symptoms which were similar to ITP. A hemizygous variant was detected in the GATA1 gene and a homozygous variant in the ATP2A1 gene for Brody myopathy. Eltrombopag, romiplostim, IVIG and corticosteroid were applied to resistant thrombocytopenia of the patient without knowing the cause. Patient had response in platelet counts in some occasions. This situation attracted our attention after the detection of this GATA variant in the etiopathogenesis of thrombocytopenia. Further investigations should be performed for much more rare causes of thrombocytopenia in patients with refractory thrombocytopenia attacks.https://www.tandfonline.com/doi/10.1080/09537104.2025.2500499Brody myopathyGATA1 variantimmune thrombocytopeniarefractory thrombocytopeniathrombopoietin receptor agonists
spellingShingle Elif Habibe Aktekin
Serdar Ceylaner
Şeyda Beşen
Ayşe Erbay
Nalan Yazıcı
A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks
Platelets
Brody myopathy
GATA1 variant
immune thrombocytopenia
refractory thrombocytopenia
thrombopoietin receptor agonists
title A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks
title_full A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks
title_fullStr A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks
title_full_unstemmed A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks
title_short A case with a novel GATA1 variant mimicking immune thrombocytopenia attacks
title_sort case with a novel gata1 variant mimicking immune thrombocytopenia attacks
topic Brody myopathy
GATA1 variant
immune thrombocytopenia
refractory thrombocytopenia
thrombopoietin receptor agonists
url https://www.tandfonline.com/doi/10.1080/09537104.2025.2500499
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