Ewing Sarcoma of the Kidney: A Rare Entity

Ewing sarcoma and primitive peripheral neuroectodermal tumor (PNET) are high-grade malignant tumors typically found in children and adolescents. These tumors belong to the family of small round cell tumors and are of neuroectodermal origin. Primary Ewing sarcoma of the kidney is rare and because of...

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Main Authors: Maria Fernanda Arruda Almeida, Madhavi Patnana, Brinda Rao Korivi, Neda Kalhor, Leonardo Marcal
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Radiology
Online Access:http://dx.doi.org/10.1155/2014/283902
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author Maria Fernanda Arruda Almeida
Madhavi Patnana
Brinda Rao Korivi
Neda Kalhor
Leonardo Marcal
author_facet Maria Fernanda Arruda Almeida
Madhavi Patnana
Brinda Rao Korivi
Neda Kalhor
Leonardo Marcal
author_sort Maria Fernanda Arruda Almeida
collection DOAJ
description Ewing sarcoma and primitive peripheral neuroectodermal tumor (PNET) are high-grade malignant tumors typically found in children and adolescents. These tumors belong to the family of small round cell tumors and are of neuroectodermal origin. Primary Ewing sarcoma of the kidney is rare and because of that is an infrequent differential diagnosis in urologic malignancies. Renal PNET mostly presents with nonspecific symptoms such as hematuria and abdominal pain. The imaging findings are uncharacteristic. The diagnosis is based on the histology, immunohistochemistry, and molecular pathologic findings. Once PNET has been diagnosed, multimodal treatment is indicated. Despite all treatment options, the prognosis of those with metastatic disease is poor.
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institution DOAJ
issn 2090-6862
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language English
publishDate 2014-01-01
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series Case Reports in Radiology
spelling doaj-art-bd7ed3547f4b4a509493132bbb7bc3552025-08-20T03:23:31ZengWileyCase Reports in Radiology2090-68622090-68702014-01-01201410.1155/2014/283902283902Ewing Sarcoma of the Kidney: A Rare EntityMaria Fernanda Arruda Almeida0Madhavi Patnana1Brinda Rao Korivi2Neda Kalhor3Leonardo Marcal4Diagnostic Radiology Resident, A. C. Camargo Hospital, Sao Paulo, SP, BrazilDepartment of Diagnostic Radiology, The University of Texas M. D. Anderson Cancer Center, 1515 Holcombe Boulevard, Houston, TX 77030, USADepartment of Diagnostic Radiology, The University of Texas M. D. Anderson Cancer Center, 1515 Holcombe Boulevard, Houston, TX 77030, USADepartment of Diagnostic Radiology, The University of Texas M. D. Anderson Cancer Center, 1515 Holcombe Boulevard, Houston, TX 77030, USADepartment of Diagnostic Radiology, The University of Texas M. D. Anderson Cancer Center, 1515 Holcombe Boulevard, Houston, TX 77030, USAEwing sarcoma and primitive peripheral neuroectodermal tumor (PNET) are high-grade malignant tumors typically found in children and adolescents. These tumors belong to the family of small round cell tumors and are of neuroectodermal origin. Primary Ewing sarcoma of the kidney is rare and because of that is an infrequent differential diagnosis in urologic malignancies. Renal PNET mostly presents with nonspecific symptoms such as hematuria and abdominal pain. The imaging findings are uncharacteristic. The diagnosis is based on the histology, immunohistochemistry, and molecular pathologic findings. Once PNET has been diagnosed, multimodal treatment is indicated. Despite all treatment options, the prognosis of those with metastatic disease is poor.http://dx.doi.org/10.1155/2014/283902
spellingShingle Maria Fernanda Arruda Almeida
Madhavi Patnana
Brinda Rao Korivi
Neda Kalhor
Leonardo Marcal
Ewing Sarcoma of the Kidney: A Rare Entity
Case Reports in Radiology
title Ewing Sarcoma of the Kidney: A Rare Entity
title_full Ewing Sarcoma of the Kidney: A Rare Entity
title_fullStr Ewing Sarcoma of the Kidney: A Rare Entity
title_full_unstemmed Ewing Sarcoma of the Kidney: A Rare Entity
title_short Ewing Sarcoma of the Kidney: A Rare Entity
title_sort ewing sarcoma of the kidney a rare entity
url http://dx.doi.org/10.1155/2014/283902
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AT madhavipatnana ewingsarcomaofthekidneyarareentity
AT brindaraokorivi ewingsarcomaofthekidneyarareentity
AT nedakalhor ewingsarcomaofthekidneyarareentity
AT leonardomarcal ewingsarcomaofthekidneyarareentity