Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report

BackgroundBehcet’s disease (BD) is a lifelong multi-systemic vasculitis disorder that can affect almost any organ. The frequency of involvement of each organ varies depending on demographic and geographical factors. The commonly affected systems include mucosal, articular, ocular, vascular, neurolog...

Full description

Saved in:
Bibliographic Details
Main Authors: Yucan Zheng, Guiping Kong, Hongmei Guo, Zhifeng Liu, Kunlong Yan
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Immunology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2025.1550551/full
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850136191128567808
author Yucan Zheng
Guiping Kong
Hongmei Guo
Zhifeng Liu
Kunlong Yan
author_facet Yucan Zheng
Guiping Kong
Hongmei Guo
Zhifeng Liu
Kunlong Yan
author_sort Yucan Zheng
collection DOAJ
description BackgroundBehcet’s disease (BD) is a lifelong multi-systemic vasculitis disorder that can affect almost any organ. The frequency of involvement of each organ varies depending on demographic and geographical factors. The commonly affected systems include mucosal, articular, ocular, vascular, neurological, and gastrointestinal. Common gastrointestinal manifestations include mucosal ulcers, hemorrhage, and perforation while other phenotypes are very rare.Case presentationWe describe the case of a 3-year-old boy suffering from BD phenotype with multiple aseptic abscesses (AAs) and interstitial lung disease. Over the past four years since onset, the boy has presented a series of symptoms, including fever, skin necrosis, multiple ulcers in the intestines, multiple aseptic abscesses in the spleen, interstitial lung disease and an isolated abscess in the gastric wall. Through a regimen involving steroids, mercaptopurine, thalidomide endoscopic drainage of the gastric wall abscess, the child’s condition has been effectively managed and improved.ConclusionTo our knowledge, this is the first reported case of BD phenotype with a gastric wall abscess treated with endoscopic drainage and steroids. Multiple AAs and interstitial lung disease may be the early signs of a BD phenotype in childhood which can respond effectively to glucocorticoids.
format Article
id doaj-art-bbc99c56d5234ab5a429a9c03e0033f1
institution OA Journals
issn 1664-3224
language English
publishDate 2025-06-01
publisher Frontiers Media S.A.
record_format Article
series Frontiers in Immunology
spelling doaj-art-bbc99c56d5234ab5a429a9c03e0033f12025-08-20T02:31:12ZengFrontiers Media S.A.Frontiers in Immunology1664-32242025-06-011610.3389/fimmu.2025.15505511550551Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case reportYucan ZhengGuiping KongHongmei GuoZhifeng LiuKunlong YanBackgroundBehcet’s disease (BD) is a lifelong multi-systemic vasculitis disorder that can affect almost any organ. The frequency of involvement of each organ varies depending on demographic and geographical factors. The commonly affected systems include mucosal, articular, ocular, vascular, neurological, and gastrointestinal. Common gastrointestinal manifestations include mucosal ulcers, hemorrhage, and perforation while other phenotypes are very rare.Case presentationWe describe the case of a 3-year-old boy suffering from BD phenotype with multiple aseptic abscesses (AAs) and interstitial lung disease. Over the past four years since onset, the boy has presented a series of symptoms, including fever, skin necrosis, multiple ulcers in the intestines, multiple aseptic abscesses in the spleen, interstitial lung disease and an isolated abscess in the gastric wall. Through a regimen involving steroids, mercaptopurine, thalidomide endoscopic drainage of the gastric wall abscess, the child’s condition has been effectively managed and improved.ConclusionTo our knowledge, this is the first reported case of BD phenotype with a gastric wall abscess treated with endoscopic drainage and steroids. Multiple AAs and interstitial lung disease may be the early signs of a BD phenotype in childhood which can respond effectively to glucocorticoids.https://www.frontiersin.org/articles/10.3389/fimmu.2025.1550551/fullBehcet’s disease phenotypeaseptic abscessesinterstitial lung diseasecase reportautoimmune diseases
spellingShingle Yucan Zheng
Guiping Kong
Hongmei Guo
Zhifeng Liu
Kunlong Yan
Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report
Frontiers in Immunology
Behcet’s disease phenotype
aseptic abscesses
interstitial lung disease
case report
autoimmune diseases
title Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report
title_full Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report
title_fullStr Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report
title_full_unstemmed Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report
title_short Multiple aseptic abscesses and pulmonary involvement in a child with Behcet’s disease phenotype: a case report
title_sort multiple aseptic abscesses and pulmonary involvement in a child with behcet s disease phenotype a case report
topic Behcet’s disease phenotype
aseptic abscesses
interstitial lung disease
case report
autoimmune diseases
url https://www.frontiersin.org/articles/10.3389/fimmu.2025.1550551/full
work_keys_str_mv AT yucanzheng multipleasepticabscessesandpulmonaryinvolvementinachildwithbehcetsdiseasephenotypeacasereport
AT guipingkong multipleasepticabscessesandpulmonaryinvolvementinachildwithbehcetsdiseasephenotypeacasereport
AT hongmeiguo multipleasepticabscessesandpulmonaryinvolvementinachildwithbehcetsdiseasephenotypeacasereport
AT zhifengliu multipleasepticabscessesandpulmonaryinvolvementinachildwithbehcetsdiseasephenotypeacasereport
AT kunlongyan multipleasepticabscessesandpulmonaryinvolvementinachildwithbehcetsdiseasephenotypeacasereport