Pemphigus herpetiformis : A rare clinical variant of pemphigus

Pemphigus herpetiformis is an autoimmune blistering disease. We report a case of pemphigus herpetiformis, a generalized form, manifested as pruritic grouped vesicles at extremities and trunk, in a seventy years old man. Neutrophil dominant inflammatory substrate was seen in histopathology. Direct i...

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Main Authors: P Shrestha, R B Tajhya, A Pokharel
Format: Article
Language:English
Published: Society of Dermatologists, Venereologists and Leprologists of Nepal (SODVELON) 2016-01-01
Series:Nepal Journal of Dermatology, Venereology & Leprology
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Online Access:https://nepjol.info/index.php/NJDVL/article/view/14308
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author P Shrestha
R B Tajhya
A Pokharel
author_facet P Shrestha
R B Tajhya
A Pokharel
author_sort P Shrestha
collection DOAJ
description Pemphigus herpetiformis is an autoimmune blistering disease. We report a case of pemphigus herpetiformis, a generalized form, manifested as pruritic grouped vesicles at extremities and trunk, in a seventy years old man. Neutrophil dominant inflammatory substrate was seen in histopathology. Direct immunofluorescene revealed IgG reactivity in net like pattern at upper epidermis, confirming pemphigus. The patient responded well to prednisolone and colchicine combination initially and maintained remission later on colchicine alone. Colchicine has anti-mitotic, anti-inflammatory and immunosuppressive mechanism of actions and proven benefits in neutrophilic dermatoses. Therefore we recommend colchicine as mono therapy or in combination with immunosuppressive, for the treatment of pemphigus herpetiformis where neutrophil is predominant inflammatory infiltrate histologically. NJDVL Vol. 13, No. 1, 2015 Page: 61-65
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institution Kabale University
issn 2091-0231
2091-167X
language English
publishDate 2016-01-01
publisher Society of Dermatologists, Venereologists and Leprologists of Nepal (SODVELON)
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series Nepal Journal of Dermatology, Venereology & Leprology
spelling doaj-art-bb707d5c29644e09b49949a9df0eb2572025-08-24T10:06:38ZengSociety of Dermatologists, Venereologists and Leprologists of Nepal (SODVELON)Nepal Journal of Dermatology, Venereology & Leprology2091-02312091-167X2016-01-01131Pemphigus herpetiformis : A rare clinical variant of pemphigusP Shrestha0R B Tajhya1A Pokharel2Department of Dermatology, Vayodha Hospital Pvt. Ltd, Balkhu, KathmanduDepartment of Dermatology, Vayodha Hospital Pvt. Ltd, Balkhu, KathmanduDepartment of Dermatology, Chitwan Medical College, Bharatpur Pemphigus herpetiformis is an autoimmune blistering disease. We report a case of pemphigus herpetiformis, a generalized form, manifested as pruritic grouped vesicles at extremities and trunk, in a seventy years old man. Neutrophil dominant inflammatory substrate was seen in histopathology. Direct immunofluorescene revealed IgG reactivity in net like pattern at upper epidermis, confirming pemphigus. The patient responded well to prednisolone and colchicine combination initially and maintained remission later on colchicine alone. Colchicine has anti-mitotic, anti-inflammatory and immunosuppressive mechanism of actions and proven benefits in neutrophilic dermatoses. Therefore we recommend colchicine as mono therapy or in combination with immunosuppressive, for the treatment of pemphigus herpetiformis where neutrophil is predominant inflammatory infiltrate histologically. NJDVL Vol. 13, No. 1, 2015 Page: 61-65 https://nepjol.info/index.php/NJDVL/article/view/14308PemphigusHerpetiformPruriticVesicles
spellingShingle P Shrestha
R B Tajhya
A Pokharel
Pemphigus herpetiformis : A rare clinical variant of pemphigus
Nepal Journal of Dermatology, Venereology & Leprology
Pemphigus
Herpetiform
Pruritic
Vesicles
title Pemphigus herpetiformis : A rare clinical variant of pemphigus
title_full Pemphigus herpetiformis : A rare clinical variant of pemphigus
title_fullStr Pemphigus herpetiformis : A rare clinical variant of pemphigus
title_full_unstemmed Pemphigus herpetiformis : A rare clinical variant of pemphigus
title_short Pemphigus herpetiformis : A rare clinical variant of pemphigus
title_sort pemphigus herpetiformis a rare clinical variant of pemphigus
topic Pemphigus
Herpetiform
Pruritic
Vesicles
url https://nepjol.info/index.php/NJDVL/article/view/14308
work_keys_str_mv AT pshrestha pemphigusherpetiformisarareclinicalvariantofpemphigus
AT rbtajhya pemphigusherpetiformisarareclinicalvariantofpemphigus
AT apokharel pemphigusherpetiformisarareclinicalvariantofpemphigus