A case-based review of adult-onset craniopharyngioma

Craniopharyngiomas are histologically benign central nervous system tumors derived from embryonic epithelial cells of Rathke’s pouch. The disease demonstrates a bimodal age distribution, occurring most often in patients 5-14 and 50-74 years of age. Common comorbidities include hypopituitarism, hypot...

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Main Authors: Scott Meyer, Shruti N. Shah, Kristen Dancel-Manning, Yuxiu Wang, Matthew Young, Nidhi Agrawal
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-05-01
Series:Frontiers in Endocrinology
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Online Access:https://www.frontiersin.org/articles/10.3389/fendo.2025.1527161/full
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author Scott Meyer
Shruti N. Shah
Kristen Dancel-Manning
Yuxiu Wang
Matthew Young
Nidhi Agrawal
author_facet Scott Meyer
Shruti N. Shah
Kristen Dancel-Manning
Yuxiu Wang
Matthew Young
Nidhi Agrawal
author_sort Scott Meyer
collection DOAJ
description Craniopharyngiomas are histologically benign central nervous system tumors derived from embryonic epithelial cells of Rathke’s pouch. The disease demonstrates a bimodal age distribution, occurring most often in patients 5-14 and 50-74 years of age. Common comorbidities include hypopituitarism, hypothalamic obesity, sleep apnea, visual impairment and neurocognitive disturbances. There are several key differences in the presentation, tumor characteristics and clinical outcomes between age groups. Childhood craniopharyngiomas are mostly adamantinomatous and often present as larger tumors with worse functional outcomes such as rates of obesity and neurological deficits. Adults experience similar but slightly adjusted rates of comorbidity with both the adamantinomatous and papillary subtypes. This review presents a case-based discussion of adult craniopharyngiomas, focusing on recent literature regarding their presentation, pathology and pathogenesis, diagnosis, treatment and long-term sequelae.
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spelling doaj-art-bac8a7d37a214d45933a7397f092c8412025-08-20T03:49:45ZengFrontiers Media S.A.Frontiers in Endocrinology1664-23922025-05-011610.3389/fendo.2025.15271611527161A case-based review of adult-onset craniopharyngiomaScott Meyer0Shruti N. Shah1Kristen Dancel-Manning2Yuxiu Wang3Matthew Young4Nidhi Agrawal5Department of Medicine, NYU Langone Health, New York, NY, United StatesDepartment of Medicine, NYU Langone Health, New York, NY, United StatesDepartment of Endocrinology, NYU Langone Health, New York, NY, United StatesDepartment of Pathology, NYU Langone Health, New York, NY, United StatesDepartment of Radiology, NYU Langone Health, New York, NY, United StatesDepartment of Endocrinology, NYU Langone Health, New York, NY, United StatesCraniopharyngiomas are histologically benign central nervous system tumors derived from embryonic epithelial cells of Rathke’s pouch. The disease demonstrates a bimodal age distribution, occurring most often in patients 5-14 and 50-74 years of age. Common comorbidities include hypopituitarism, hypothalamic obesity, sleep apnea, visual impairment and neurocognitive disturbances. There are several key differences in the presentation, tumor characteristics and clinical outcomes between age groups. Childhood craniopharyngiomas are mostly adamantinomatous and often present as larger tumors with worse functional outcomes such as rates of obesity and neurological deficits. Adults experience similar but slightly adjusted rates of comorbidity with both the adamantinomatous and papillary subtypes. This review presents a case-based discussion of adult craniopharyngiomas, focusing on recent literature regarding their presentation, pathology and pathogenesis, diagnosis, treatment and long-term sequelae.https://www.frontiersin.org/articles/10.3389/fendo.2025.1527161/fullcraniopharyngiomaadult craniopharyngiomapapillary craniopharyngioma (PCP)adamantinomatous craniopharyngiomamini reviewliterature review
spellingShingle Scott Meyer
Shruti N. Shah
Kristen Dancel-Manning
Yuxiu Wang
Matthew Young
Nidhi Agrawal
A case-based review of adult-onset craniopharyngioma
Frontiers in Endocrinology
craniopharyngioma
adult craniopharyngioma
papillary craniopharyngioma (PCP)
adamantinomatous craniopharyngioma
mini review
literature review
title A case-based review of adult-onset craniopharyngioma
title_full A case-based review of adult-onset craniopharyngioma
title_fullStr A case-based review of adult-onset craniopharyngioma
title_full_unstemmed A case-based review of adult-onset craniopharyngioma
title_short A case-based review of adult-onset craniopharyngioma
title_sort case based review of adult onset craniopharyngioma
topic craniopharyngioma
adult craniopharyngioma
papillary craniopharyngioma (PCP)
adamantinomatous craniopharyngioma
mini review
literature review
url https://www.frontiersin.org/articles/10.3389/fendo.2025.1527161/full
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