Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report

Autosomal recessive woolly hair/hypotrichosis (ARWH/H) is a hereditary hair disorder characterized by sparse, short, and curly hair. Mutations in the Lipase H (LIPH) gene, LPAR6, or other genes cause this hereditary hair condition. We report a case of an 11-month-old Saudi boy who presented to our...

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Main Authors: Khalid Alwunais, Jamal Alqahtani, Abdullah Ali N Aljalfan, Hadeel Alotaibi
Format: Article
Language:English
Published: PAGEPress Publications 2025-05-01
Series:Dermatology Reports
Subjects:
Online Access:https://www.pagepress.org/journals/dr/article/view/10177
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author Khalid Alwunais
Jamal Alqahtani
Abdullah Ali N Aljalfan
Hadeel Alotaibi
author_facet Khalid Alwunais
Jamal Alqahtani
Abdullah Ali N Aljalfan
Hadeel Alotaibi
author_sort Khalid Alwunais
collection DOAJ
description Autosomal recessive woolly hair/hypotrichosis (ARWH/H) is a hereditary hair disorder characterized by sparse, short, and curly hair. Mutations in the Lipase H (LIPH) gene, LPAR6, or other genes cause this hereditary hair condition. We report a case of an 11-month-old Saudi boy who presented to our dermatology clinic at King Fahad University Hospital in Al-Khobar (Saudi Arabia) with short, non-growing hair since birth. DNA sequencing revealed a homozygous mutation in the LIPH gene at c.280_369dup. Our patient was diagnosed with ARWH/H resulting from a homozygous mutation in LIPH.
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publishDate 2025-05-01
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series Dermatology Reports
spelling doaj-art-b9eb3a535dcd4535b550eaad163b4d0d2025-08-20T02:35:32ZengPAGEPress PublicationsDermatology Reports2036-73922036-74062025-05-0110.4081/dr.2025.10177Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case reportKhalid Alwunais0Jamal Alqahtani1Abdullah Ali N Aljalfan2Hadeel Alotaibi3https://orcid.org/0000-0003-1150-9788Dermatology Department, College of Medicine, Imam Abdulrahman Bin Faisal University, DammamDermatology Department, College of Medicine, Imam Abdulrahman Bin Faisal University, DammamDermatology Department, College of Medicine, Imam Abdulrahman Bin Faisal University, DammamDermatology Department, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam Autosomal recessive woolly hair/hypotrichosis (ARWH/H) is a hereditary hair disorder characterized by sparse, short, and curly hair. Mutations in the Lipase H (LIPH) gene, LPAR6, or other genes cause this hereditary hair condition. We report a case of an 11-month-old Saudi boy who presented to our dermatology clinic at King Fahad University Hospital in Al-Khobar (Saudi Arabia) with short, non-growing hair since birth. DNA sequencing revealed a homozygous mutation in the LIPH gene at c.280_369dup. Our patient was diagnosed with ARWH/H resulting from a homozygous mutation in LIPH. https://www.pagepress.org/journals/dr/article/view/10177HypotrichosisLipase Hwoolly hairautosomal recessive
spellingShingle Khalid Alwunais
Jamal Alqahtani
Abdullah Ali N Aljalfan
Hadeel Alotaibi
Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report
Dermatology Reports
Hypotrichosis
Lipase H
woolly hair
autosomal recessive
title Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report
title_full Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report
title_fullStr Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report
title_full_unstemmed Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report
title_short Autosomal recessive woolly hair/hypotrichosis with homozygous mutation in the LIPH gene: a case report
title_sort autosomal recessive woolly hair hypotrichosis with homozygous mutation in the liph gene a case report
topic Hypotrichosis
Lipase H
woolly hair
autosomal recessive
url https://www.pagepress.org/journals/dr/article/view/10177
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AT abdullahalinaljalfan autosomalrecessivewoollyhairhypotrichosiswithhomozygousmutationintheliphgeneacasereport
AT hadeelalotaibi autosomalrecessivewoollyhairhypotrichosiswithhomozygousmutationintheliphgeneacasereport