Is immunotherapy safe and effective in patients with VEXAS syndrome?

The use of immune checkpoint inhibitors in VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome is unknown. Concerns are particularly about their safety, due to their potential capacity to exacerbate inflammatory symptoms. Further, there is a lack of data about their role in con...

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Main Authors: Chiara Marvisi, Francesco Muratore, Carlo Salvarani, Davide Nicoli, Enrico Farnetti, Lucia Spaggiari, Vincenza Ylenia Cusenza, Orsola Bonanno, Maria Banzi, Caterina Longo
Format: Article
Language:English
Published: BMJ Publishing Group 2025-07-01
Series:Journal for ImmunoTherapy of Cancer
Online Access:https://jitc.bmj.com/content/13/7/e012410.full
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author Chiara Marvisi
Francesco Muratore
Carlo Salvarani
Davide Nicoli
Enrico Farnetti
Lucia Spaggiari
Vincenza Ylenia Cusenza
Orsola Bonanno
Maria Banzi
Caterina Longo
author_facet Chiara Marvisi
Francesco Muratore
Carlo Salvarani
Davide Nicoli
Enrico Farnetti
Lucia Spaggiari
Vincenza Ylenia Cusenza
Orsola Bonanno
Maria Banzi
Caterina Longo
author_sort Chiara Marvisi
collection DOAJ
description The use of immune checkpoint inhibitors in VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome is unknown. Concerns are particularly about their safety, due to their potential capacity to exacerbate inflammatory symptoms. Further, there is a lack of data about their role in controlling the UBA1 clones. In this clinical case, we report a successful use of cemiplimab in a patient with VEXAS syndrome and a concomitant diagnosis of metastatic squamous cell carcinoma.
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institution DOAJ
issn 2051-1426
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publishDate 2025-07-01
publisher BMJ Publishing Group
record_format Article
series Journal for ImmunoTherapy of Cancer
spelling doaj-art-b82e2cb72f4b4eb991351d48fdf2f0eb2025-08-20T02:47:35ZengBMJ Publishing GroupJournal for ImmunoTherapy of Cancer2051-14262025-07-0113710.1136/jitc-2025-012410Is immunotherapy safe and effective in patients with VEXAS syndrome?Chiara Marvisi0Francesco Muratore1Carlo Salvarani2Davide Nicoli3Enrico Farnetti4Lucia Spaggiari5Vincenza Ylenia Cusenza6Orsola Bonanno7Maria Banzi8Caterina Longo9Azienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyAzienda USL - IRCCS di Reggio Emilia, Reggio Emilia, ItalyThe use of immune checkpoint inhibitors in VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome is unknown. Concerns are particularly about their safety, due to their potential capacity to exacerbate inflammatory symptoms. Further, there is a lack of data about their role in controlling the UBA1 clones. In this clinical case, we report a successful use of cemiplimab in a patient with VEXAS syndrome and a concomitant diagnosis of metastatic squamous cell carcinoma.https://jitc.bmj.com/content/13/7/e012410.full
spellingShingle Chiara Marvisi
Francesco Muratore
Carlo Salvarani
Davide Nicoli
Enrico Farnetti
Lucia Spaggiari
Vincenza Ylenia Cusenza
Orsola Bonanno
Maria Banzi
Caterina Longo
Is immunotherapy safe and effective in patients with VEXAS syndrome?
Journal for ImmunoTherapy of Cancer
title Is immunotherapy safe and effective in patients with VEXAS syndrome?
title_full Is immunotherapy safe and effective in patients with VEXAS syndrome?
title_fullStr Is immunotherapy safe and effective in patients with VEXAS syndrome?
title_full_unstemmed Is immunotherapy safe and effective in patients with VEXAS syndrome?
title_short Is immunotherapy safe and effective in patients with VEXAS syndrome?
title_sort is immunotherapy safe and effective in patients with vexas syndrome
url https://jitc.bmj.com/content/13/7/e012410.full
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