Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review

Renal cell carcinoma (RCC) associated with XP11.2 translocation is an exceedingly rare subtype of RCC. A 27-year-old female presented with a 6.7cm mass and underwent a robotic-assisted left radical nephrectomy with uneventful recovery. Pathology revealed clear cell carcinoma with papillary and gland...

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Main Authors: Bader Alsaikhan, Saud AlHussayen, Ebtesam Almajed, Abdullah Alghuraibi, Khaled Almodeth, Noura Al Oudah, Abdulrahman K. Alabdulsalam
Format: Article
Language:English
Published: Elsevier 2025-07-01
Series:Urology Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2214442025001287
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author Bader Alsaikhan
Saud AlHussayen
Ebtesam Almajed
Abdullah Alghuraibi
Khaled Almodeth
Noura Al Oudah
Abdulrahman K. Alabdulsalam
author_facet Bader Alsaikhan
Saud AlHussayen
Ebtesam Almajed
Abdullah Alghuraibi
Khaled Almodeth
Noura Al Oudah
Abdulrahman K. Alabdulsalam
author_sort Bader Alsaikhan
collection DOAJ
description Renal cell carcinoma (RCC) associated with XP11.2 translocation is an exceedingly rare subtype of RCC. A 27-year-old female presented with a 6.7cm mass and underwent a robotic-assisted left radical nephrectomy with uneventful recovery. Pathology revealed clear cell carcinoma with papillary and glandular features, positive for Melan-A, consistent with MIT family translocation renal cell carcinoma. The infrequent occurrence and its nonspecific clinical and radiological presentation results in a considerable diagnostic challenge. Given the potentially more aggressive behavior of Xp11.2 translocation RCC, particularly in adults, a thorough understanding of the tumor's genetic profile is critical for optimizing patient management and improving outcomes.
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issn 2214-4420
language English
publishDate 2025-07-01
publisher Elsevier
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series Urology Case Reports
spelling doaj-art-b7209f234d474c14ac7db992030cb2a92025-08-20T02:48:07ZengElsevierUrology Case Reports2214-44202025-07-016110305710.1016/j.eucr.2025.103057Renal cell carcinoma associated with XP11.2 translocation: A case report and literature reviewBader Alsaikhan0Saud AlHussayen1Ebtesam Almajed2Abdullah Alghuraibi3Khaled Almodeth4Noura Al Oudah5Abdulrahman K. Alabdulsalam6College of Medicine, King Saud Bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia; Department of Surgery, Division of Urology, Ministry of National Guard - Health Affairs, Riyadh, Saudi Arabia; King Abdullah International Medical Research Center, Riyadh, Saudi Arabia; Corresponding author. King Saud bin Abdulaziz University for Health Sciences King Abdullah International Medical Research Centre, National Guard Health Affairs (MNGHA), Riyadh, Saudi ArabiaCollege of Medicine, King Saud Bin Abdulaziz University for Health Sciences, Riyadh, Saudi ArabiaDepartment of Clinical Sciences, College of Medicine, Princess Nourah Bint Abdulrahman University, Riyadh, Saudi ArabiaCollege of Medicine, King Saud Bin Abdulaziz University for Health Sciences, Riyadh, Saudi ArabiaCollege of Medicine, Imam Mohammad Ibn Saud Islamic University, Riyadh, Saudi ArabiaConsultant Pathologist and Nephropathologist, Department of Pathology and Laboratory Medicine, Ministry of National Guard - Health Affairs, Riyadh, Saudi ArabiaAnatomic and Renal Pathologist, Department of Pathology and Laboratory Medicine, Ministry of National Guard - Health Affairs, Riyadh, Saudi ArabiaRenal cell carcinoma (RCC) associated with XP11.2 translocation is an exceedingly rare subtype of RCC. A 27-year-old female presented with a 6.7cm mass and underwent a robotic-assisted left radical nephrectomy with uneventful recovery. Pathology revealed clear cell carcinoma with papillary and glandular features, positive for Melan-A, consistent with MIT family translocation renal cell carcinoma. The infrequent occurrence and its nonspecific clinical and radiological presentation results in a considerable diagnostic challenge. Given the potentially more aggressive behavior of Xp11.2 translocation RCC, particularly in adults, a thorough understanding of the tumor's genetic profile is critical for optimizing patient management and improving outcomes.http://www.sciencedirect.com/science/article/pii/S2214442025001287Xp11.2 translocationRenal cell carcinomaTranscription factor E3 gene fusionCase report
spellingShingle Bader Alsaikhan
Saud AlHussayen
Ebtesam Almajed
Abdullah Alghuraibi
Khaled Almodeth
Noura Al Oudah
Abdulrahman K. Alabdulsalam
Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review
Urology Case Reports
Xp11.2 translocation
Renal cell carcinoma
Transcription factor E3 gene fusion
Case report
title Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review
title_full Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review
title_fullStr Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review
title_full_unstemmed Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review
title_short Renal cell carcinoma associated with XP11.2 translocation: A case report and literature review
title_sort renal cell carcinoma associated with xp11 2 translocation a case report and literature review
topic Xp11.2 translocation
Renal cell carcinoma
Transcription factor E3 gene fusion
Case report
url http://www.sciencedirect.com/science/article/pii/S2214442025001287
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AT abdullahalghuraibi renalcellcarcinomaassociatedwithxp112translocationacasereportandliteraturereview
AT khaledalmodeth renalcellcarcinomaassociatedwithxp112translocationacasereportandliteraturereview
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