The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies

Antiphospholipid syndrome (APS) is an autoimmune disease mainly characterised by vascular thrombosis and pregnancy morbidity. APS has broad spectrum of clinical manifestations. The digestive system involvement of antiphospholipid syndrome is a critical but under-recognised condition. Digestive syste...

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Main Authors: Jin Zhang, Cheng Li, Xiaorong Han, Zhongbo Chen, Binay Kumar Adhikari, Yinghui Wang, Yonggang Wang, Jian Sun
Format: Article
Language:English
Published: Taylor & Francis Group 2021-01-01
Series:Annals of Medicine
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Online Access:https://www.tandfonline.com/doi/10.1080/07853890.2021.1962964
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author Jin Zhang
Cheng Li
Xiaorong Han
Zhongbo Chen
Binay Kumar Adhikari
Yinghui Wang
Yonggang Wang
Jian Sun
author_facet Jin Zhang
Cheng Li
Xiaorong Han
Zhongbo Chen
Binay Kumar Adhikari
Yinghui Wang
Yonggang Wang
Jian Sun
author_sort Jin Zhang
collection DOAJ
description Antiphospholipid syndrome (APS) is an autoimmune disease mainly characterised by vascular thrombosis and pregnancy morbidity. APS has broad spectrum of clinical manifestations. The digestive system involvement of antiphospholipid syndrome is a critical but under-recognised condition. Digestive system involvement may be the result of direct (autoimmune-mediated) or indirect (thrombotic) mechanisms. Liver is the most commonly involved organ, followed by intestines, oesophagus, stomach, pancreas and spleen. This review describes possible digestive system manifestations in APS patients, and illustrates the epidemiology and possible pathophysiology of APS. The role of different treatment strategies in the management of digestive system manifestations of APS were also discussed.Key messagesAntiphospholipid syndrome is a multi-organ, multi-system disease and its clinical manifestation spectrum is gradually expanding. Since the first diagnosis of APS, the clinical manifestations of digestive system have been reported successively. This narrative review describes the major digestive system manifestations of APS and illustrates the epidemiology, pathophysiology and the role of therapeutic strategies of these patients.
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publishDate 2021-01-01
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record_format Article
series Annals of Medicine
spelling doaj-art-b68218ae8b0a4070b797f88e8dab3c992025-08-20T03:43:57ZengTaylor & Francis GroupAnnals of Medicine0785-38901365-20602021-01-015311328133910.1080/07853890.2021.1962964The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategiesJin Zhang0Cheng Li1Xiaorong Han2Zhongbo Chen3Binay Kumar Adhikari4Yinghui Wang5Yonggang Wang6Jian Sun7Department of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaDepartment of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaDepartment of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaDepartment of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaDepartment of Medicine, Nepal Armed Police Force Command and Staff hospital, Kathmandu, NepalDepartment of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaDepartment of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaDepartment of Cardiovascular Center, Jilin University First Hospital, Changchun, ChinaAntiphospholipid syndrome (APS) is an autoimmune disease mainly characterised by vascular thrombosis and pregnancy morbidity. APS has broad spectrum of clinical manifestations. The digestive system involvement of antiphospholipid syndrome is a critical but under-recognised condition. Digestive system involvement may be the result of direct (autoimmune-mediated) or indirect (thrombotic) mechanisms. Liver is the most commonly involved organ, followed by intestines, oesophagus, stomach, pancreas and spleen. This review describes possible digestive system manifestations in APS patients, and illustrates the epidemiology and possible pathophysiology of APS. The role of different treatment strategies in the management of digestive system manifestations of APS were also discussed.Key messagesAntiphospholipid syndrome is a multi-organ, multi-system disease and its clinical manifestation spectrum is gradually expanding. Since the first diagnosis of APS, the clinical manifestations of digestive system have been reported successively. This narrative review describes the major digestive system manifestations of APS and illustrates the epidemiology, pathophysiology and the role of therapeutic strategies of these patients.https://www.tandfonline.com/doi/10.1080/07853890.2021.1962964Antiphospholipid syndromeantiphospholipid antibodiesautoimmunethrombosisdigestive system
spellingShingle Jin Zhang
Cheng Li
Xiaorong Han
Zhongbo Chen
Binay Kumar Adhikari
Yinghui Wang
Yonggang Wang
Jian Sun
The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies
Annals of Medicine
Antiphospholipid syndrome
antiphospholipid antibodies
autoimmune
thrombosis
digestive system
title The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies
title_full The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies
title_fullStr The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies
title_full_unstemmed The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies
title_short The digestive system involvement of antiphospholipid syndrome: pathophysiology, clinical characteristics, and treatment strategies
title_sort digestive system involvement of antiphospholipid syndrome pathophysiology clinical characteristics and treatment strategies
topic Antiphospholipid syndrome
antiphospholipid antibodies
autoimmune
thrombosis
digestive system
url https://www.tandfonline.com/doi/10.1080/07853890.2021.1962964
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