Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis

Introduction. Myocarditis is not a rare diagnosis, but its etiology often remains unknown as it requires extensive diagnostic work. Eosinophilic granulomatosis with polyangiitis (EGPA) or Churg-Strauss syndrome is a very rare systemic disease that is not easy to diagnose. Myocarditis in EGPA is unco...

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Main Authors: Đorđević-Radojković Danijela, Apostolović Svetlana, Damjanović Miodrag, Kostić Tomislav, Fejsa-Levakov Aleksandra, Dimitrijević Marko, Janković-Tomašević Ružica, Dakić Sonja, Božinović Nenad, Pavićević Milena
Format: Article
Language:English
Published: Ministry of Defence of the Republic of Serbia, University of Defence, Belgrade 2023-01-01
Series:Vojnosanitetski Pregled
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Online Access:https://doiserbia.nb.rs/img/doi/0042-8450/2023/0042-84502300026D.pdf
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author Đorđević-Radojković Danijela
Apostolović Svetlana
Damjanović Miodrag
Kostić Tomislav
Fejsa-Levakov Aleksandra
Dimitrijević Marko
Janković-Tomašević Ružica
Dakić Sonja
Božinović Nenad
Pavićević Milena
author_facet Đorđević-Radojković Danijela
Apostolović Svetlana
Damjanović Miodrag
Kostić Tomislav
Fejsa-Levakov Aleksandra
Dimitrijević Marko
Janković-Tomašević Ružica
Dakić Sonja
Božinović Nenad
Pavićević Milena
author_sort Đorđević-Radojković Danijela
collection DOAJ
description Introduction. Myocarditis is not a rare diagnosis, but its etiology often remains unknown as it requires extensive diagnostic work. Eosinophilic granulomatosis with polyangiitis (EGPA) or Churg-Strauss syndrome is a very rare systemic disease that is not easy to diagnose. Myocarditis in EGPA is uncommon and usually occurs in the late stages of the disease. Case report. A 22-year-old man was admitted with acute coronary syndrome. Using coronary angiography, the presence of stenoses on the epicardial coronary arteries was ruled out, and a working diagnosis of myocardial infarction with non-obstructive coronary arteries (MINOCA) was established. Then, we found inflammatory syndrome, eosinophilia, and a lot of systemic symptoms and signs. The diagnostic work included extensive laboratory tests, which ruled out infectious agents. Then, immunological tests, a computed tomography scan of the chest, cardiac magnetic reso-nance imaging (MRI) and a biopsy of the bone marrow, nasal mucosa, and skin were performed. We managed to establish the diagnosis of myopericarditis by cardiac MRI. The cause of myocarditis – EGPA, was found only after the histopathological finding of the skin biopsy, which enabled ad-equate immunosuppressive therapy. Conclusion. The accurate diagnosis was crucial for the correct, causal treatment of the patient, especially because he needed life-long immunosuppressive therapy. In order for such complex patients to receive adequate treatment, a multidisciplinary approach and perseverance in the diagnostic evaluation of the etiology of myocarditis are necessary.
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spelling doaj-art-b62a63b7e1d54701b36f1ea9997453b82025-08-20T02:00:17ZengMinistry of Defence of the Republic of Serbia, University of Defence, BelgradeVojnosanitetski Pregled0042-84502406-07202023-01-01801194294810.2298/VSP230218026D0042-84502300026DMyocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitisĐorđević-Radojković Danijela0Apostolović Svetlana1https://orcid.org/0000-0001-9015-297XDamjanović Miodrag2Kostić Tomislav3https://orcid.org/0000-0002-5402-5153Fejsa-Levakov Aleksandra4Dimitrijević Marko5Janković-Tomašević Ružica6Dakić Sonja7Božinović Nenad8https://orcid.org/0000-0003-0515-7923Pavićević Milena9University Clinical Center Niš, Cardiology Clinic, Niš, Serbia + University of Niš, Faculty of Medicine, Niš, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, Serbia + University of Niš, Faculty of Medicine, Niš, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, Serbia + University of Niš, Faculty of Medicine, Niš, SerbiaUniversity of Novi Sad, Faculty of Medicine, Novi Sad, Serbia + University Clinical Center of Vojvodina, Novi Sad, SerbiaGeneral Hospital Zaječar, Zaječar, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, Serbia + University of Niš, Faculty of Medicine, Niš, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, Serbia + University of Niš, Faculty of Medicine, Niš, SerbiaUniversity Clinical Center Niš, Cardiology Clinic, Niš, SerbiaIntroduction. Myocarditis is not a rare diagnosis, but its etiology often remains unknown as it requires extensive diagnostic work. Eosinophilic granulomatosis with polyangiitis (EGPA) or Churg-Strauss syndrome is a very rare systemic disease that is not easy to diagnose. Myocarditis in EGPA is uncommon and usually occurs in the late stages of the disease. Case report. A 22-year-old man was admitted with acute coronary syndrome. Using coronary angiography, the presence of stenoses on the epicardial coronary arteries was ruled out, and a working diagnosis of myocardial infarction with non-obstructive coronary arteries (MINOCA) was established. Then, we found inflammatory syndrome, eosinophilia, and a lot of systemic symptoms and signs. The diagnostic work included extensive laboratory tests, which ruled out infectious agents. Then, immunological tests, a computed tomography scan of the chest, cardiac magnetic reso-nance imaging (MRI) and a biopsy of the bone marrow, nasal mucosa, and skin were performed. We managed to establish the diagnosis of myopericarditis by cardiac MRI. The cause of myocarditis – EGPA, was found only after the histopathological finding of the skin biopsy, which enabled ad-equate immunosuppressive therapy. Conclusion. The accurate diagnosis was crucial for the correct, causal treatment of the patient, especially because he needed life-long immunosuppressive therapy. In order for such complex patients to receive adequate treatment, a multidisciplinary approach and perseverance in the diagnostic evaluation of the etiology of myocarditis are necessary.https://doiserbia.nb.rs/img/doi/0042-8450/2023/0042-84502300026D.pdfdiagnosishistological techniquesmyocarditiseosinophiliachurg-strauss syndrome
spellingShingle Đorđević-Radojković Danijela
Apostolović Svetlana
Damjanović Miodrag
Kostić Tomislav
Fejsa-Levakov Aleksandra
Dimitrijević Marko
Janković-Tomašević Ružica
Dakić Sonja
Božinović Nenad
Pavićević Milena
Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
Vojnosanitetski Pregled
diagnosis
histological techniques
myocarditis
eosinophilia
churg-strauss syndrome
title Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
title_full Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
title_fullStr Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
title_full_unstemmed Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
title_short Myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
title_sort myocarditis as the first manifestation of eosinophilic granulomatosis with polyangiitis
topic diagnosis
histological techniques
myocarditis
eosinophilia
churg-strauss syndrome
url https://doiserbia.nb.rs/img/doi/0042-8450/2023/0042-84502300026D.pdf
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