YAP1::KMT2A fusion-positive sarcoma: An emerging soft tissue tumor entity with morphological features resembling a sclerosing epithelioid fibrosarcoma

YAP1::KMT2A fusion-positive sarcoma: An emerging soft tissue tumor entity with morphological features resembling a sclerosing epithelioid fibrosarcoma

Sclerosing epithelioid fibrosarcoma (SEF) and low-grade fibromyxoid sarcoma (LGFMS) constitute a morphological continuum with certain overlapping histopathological features and MUC 4 immunopositivity. SEF is characterized by EWSR1 gene rearrangement, is relatively more aggressive and shows a limited...

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Bibliographic Details
Main Authors:	Ayush Agarwal, Bharat Rekhi, Vineeta Goel, Jyoti Bajpai, Sameer Rastogi
Format:	Article
Language:	English
Published:	Wolters Kluwer Medknow Publications 2024-12-01
Series:	Indian Journal of Pathology and Microbiology
Subjects:	kmt2a low-grade fibromyxoid sarcoma muc4 sclerosing epithelioid fibrosarcoma yap1
Online Access:	https://journals.lww.com/10.4103/ijpm.ijpm_275_24
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