The diagnosis and management of porphyria cutanea tarda (PCT)
The porphyrias are a group of disorders in which excessive quantities of porphyrins or their precursors are produced. They are due to abnormalities in the control of the porphyrin-haem metabolic pathway. The porphyrias are classified into acute and chronic. The acute porphyrias are acute intermitten...
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AOSIS
2009-06-01
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| Series: | South African Family Practice |
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| Online Access: | https://safpj.co.za/index.php/safpj/article/view/957 |
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| author | Mojakgomo H. Motswaledi |
| author_facet | Mojakgomo H. Motswaledi |
| author_sort | Mojakgomo H. Motswaledi |
| collection | DOAJ |
| description | The porphyrias are a group of disorders in which excessive quantities of porphyrins or their precursors are produced. They are due to abnormalities in the control of the porphyrin-haem metabolic pathway. The porphyrias are classified into acute and chronic. The acute porphyrias are acute intermittent porphyria (AIP), porphyria variegata (PV) and hereditary coproporphyria (HCP). The chronic porphyrias are porphyria cutanea tarda (PCT), erythropoietic protoporphyria (EPP) and congenital erythropoietic porphyria (CEP). They are further classified as hepatic or erythropoietic, depending on the major site of abnormal metabolism. This article is about PCT, which is more common in South Africa than the other porphyrias and is classified as chronic and hepatic. |
| format | Article |
| id | doaj-art-b5dad53f01a54d60991ded5e2fd40a74 |
| institution | Kabale University |
| issn | 2078-6190 2078-6204 |
| language | English |
| publishDate | 2009-06-01 |
| publisher | AOSIS |
| record_format | Article |
| series | South African Family Practice |
| spelling | doaj-art-b5dad53f01a54d60991ded5e2fd40a742025-08-20T03:47:10ZengAOSISSouth African Family Practice2078-61902078-62042009-06-0151310.1080/20786204.2009.108738431101The diagnosis and management of porphyria cutanea tarda (PCT)Mojakgomo H. Motswaledi0Department of Dermatology, University of LimpopoThe porphyrias are a group of disorders in which excessive quantities of porphyrins or their precursors are produced. They are due to abnormalities in the control of the porphyrin-haem metabolic pathway. The porphyrias are classified into acute and chronic. The acute porphyrias are acute intermittent porphyria (AIP), porphyria variegata (PV) and hereditary coproporphyria (HCP). The chronic porphyrias are porphyria cutanea tarda (PCT), erythropoietic protoporphyria (EPP) and congenital erythropoietic porphyria (CEP). They are further classified as hepatic or erythropoietic, depending on the major site of abnormal metabolism. This article is about PCT, which is more common in South Africa than the other porphyrias and is classified as chronic and hepatic.https://safpj.co.za/index.php/safpj/article/view/957porphyriaporphyria cutanea tardaskin fragility |
| spellingShingle | Mojakgomo H. Motswaledi The diagnosis and management of porphyria cutanea tarda (PCT) South African Family Practice porphyria porphyria cutanea tarda skin fragility |
| title | The diagnosis and management of porphyria cutanea tarda (PCT) |
| title_full | The diagnosis and management of porphyria cutanea tarda (PCT) |
| title_fullStr | The diagnosis and management of porphyria cutanea tarda (PCT) |
| title_full_unstemmed | The diagnosis and management of porphyria cutanea tarda (PCT) |
| title_short | The diagnosis and management of porphyria cutanea tarda (PCT) |
| title_sort | diagnosis and management of porphyria cutanea tarda pct |
| topic | porphyria porphyria cutanea tarda skin fragility |
| url | https://safpj.co.za/index.php/safpj/article/view/957 |
| work_keys_str_mv | AT mojakgomohmotswaledi thediagnosisandmanagementofporphyriacutaneatardapct AT mojakgomohmotswaledi diagnosisandmanagementofporphyriacutaneatardapct |