1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium

Primary cardiac sarcomas are extremely rare. Echocardiography provides initial information about tumor location and size. However, due to the frequent resemblance to benign myxomas or thrombotic formations, the correct diagnosis often requires a multimodal approach. We report a case of undifferentia...

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Main Authors: Isabella Fumarulo, MD, Massimiliano Camilli, MD, Irma Bisceglia, MD, Massimo Massetti, MD, Antonella Lombardo, MD, Nadia Aspromonte, MD
Format: Article
Language:English
Published: Elsevier 2025-07-01
Series:JACC: Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2666084925006394
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author Isabella Fumarulo, MD
Massimiliano Camilli, MD
Irma Bisceglia, MD
Massimo Massetti, MD
Antonella Lombardo, MD
Nadia Aspromonte, MD
author_facet Isabella Fumarulo, MD
Massimiliano Camilli, MD
Irma Bisceglia, MD
Massimo Massetti, MD
Antonella Lombardo, MD
Nadia Aspromonte, MD
author_sort Isabella Fumarulo, MD
collection DOAJ
description Primary cardiac sarcomas are extremely rare. Echocardiography provides initial information about tumor location and size. However, due to the frequent resemblance to benign myxomas or thrombotic formations, the correct diagnosis often requires a multimodal approach. We report a case of undifferentiated cardiac sarcoma in a 46-year-old woman who underwent surgical resection. One month after the operation, echocardiography revealed disease recurrence. The patient underwent chemotherapy and hypofractionated radiotherapy with significant reduction of mass size. Primary cardiac sarcomas may be suspected by multimodality imaging tests, but the definitive diagnosis is histologic. There is still no international agreement about imaging criteria to define these tumors or optimal treatment. Radical surgery is potentially the best therapeutic option, but it is still burdened by high recurrence rates; radiotherapy, chemotherapy and immunotherapy appear promising, especially when used in combination.
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series JACC: Case Reports
spelling doaj-art-b0d601b942d04e5a843c745e21f496bf2025-08-20T03:29:10ZengElsevierJACC: Case Reports2666-08492025-07-01301710386110.1016/j.jaccas.2025.1038611-Month Relapse of Undifferentiated Sarcoma in the Left AtriumIsabella Fumarulo, MD0Massimiliano Camilli, MD1Irma Bisceglia, MD2Massimo Massetti, MD3Antonella Lombardo, MD4Nadia Aspromonte, MD5Department of Cardiovascular Sciences, A. Gemelli University Policlinic Foundation IRCCS, Rome, Italy; Department of Cardiovascular Sciences, Catholic University of the Sacred Heart, Rome, ItalyDepartment of Cardiovascular Sciences, A. Gemelli University Policlinic Foundation IRCCS, Rome, Italy; Department of Cardiovascular Sciences, Catholic University of the Sacred Heart, Rome, ItalyIntegrated Cardiology Services, Department of Cardio–Thoracic–Vascular, Azienda Ospedaliera San Camillo Forlanini, Rome, ItalyDepartment of Cardiovascular Sciences, A. Gemelli University Policlinic Foundation IRCCS, Rome, Italy; Department of Cardiovascular Sciences, Catholic University of the Sacred Heart, Rome, ItalyDepartment of Cardiovascular Sciences, A. Gemelli University Policlinic Foundation IRCCS, Rome, Italy; Department of Cardiovascular Sciences, Catholic University of the Sacred Heart, Rome, Italy; Address for correspondence: Dr Antonella Lombardo, A. Gemelli University Policlinic Foundation IRCCS, Largo F. Vito 1, Rome 00168, Italy.Department of Cardiovascular Sciences, A. Gemelli University Policlinic Foundation IRCCS, Rome, Italy; Department of Cardiovascular Sciences, Catholic University of the Sacred Heart, Rome, ItalyPrimary cardiac sarcomas are extremely rare. Echocardiography provides initial information about tumor location and size. However, due to the frequent resemblance to benign myxomas or thrombotic formations, the correct diagnosis often requires a multimodal approach. We report a case of undifferentiated cardiac sarcoma in a 46-year-old woman who underwent surgical resection. One month after the operation, echocardiography revealed disease recurrence. The patient underwent chemotherapy and hypofractionated radiotherapy with significant reduction of mass size. Primary cardiac sarcomas may be suspected by multimodality imaging tests, but the definitive diagnosis is histologic. There is still no international agreement about imaging criteria to define these tumors or optimal treatment. Radical surgery is potentially the best therapeutic option, but it is still burdened by high recurrence rates; radiotherapy, chemotherapy and immunotherapy appear promising, especially when used in combination.http://www.sciencedirect.com/science/article/pii/S2666084925006394cardiac surgerycase reportechocardiographyhypofractionated radiotherapymultimodal imagingprimary cardiac sarcoma
spellingShingle Isabella Fumarulo, MD
Massimiliano Camilli, MD
Irma Bisceglia, MD
Massimo Massetti, MD
Antonella Lombardo, MD
Nadia Aspromonte, MD
1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium
JACC: Case Reports
cardiac surgery
case report
echocardiography
hypofractionated radiotherapy
multimodal imaging
primary cardiac sarcoma
title 1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium
title_full 1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium
title_fullStr 1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium
title_full_unstemmed 1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium
title_short 1-Month Relapse of Undifferentiated Sarcoma in the Left Atrium
title_sort 1 month relapse of undifferentiated sarcoma in the left atrium
topic cardiac surgery
case report
echocardiography
hypofractionated radiotherapy
multimodal imaging
primary cardiac sarcoma
url http://www.sciencedirect.com/science/article/pii/S2666084925006394
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