Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature

The occurrence of benign nerve sheath tumors within the neuroaxis is uncommon. Even rarer is the finding within brain parenchyma, termed malignant intracerebral nerve sheath tumors (MINST). We present a case of MINST which occurred in the frontal lobe of an 18-year-old male that recurred almost 4 ye...

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Main Authors: Faris Shweikeh, Doniel Drazin, Sergei I. Bannykh
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Case Reports in Surgery
Online Access:http://dx.doi.org/10.1155/2013/384076
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author Faris Shweikeh
Doniel Drazin
Sergei I. Bannykh
author_facet Faris Shweikeh
Doniel Drazin
Sergei I. Bannykh
author_sort Faris Shweikeh
collection DOAJ
description The occurrence of benign nerve sheath tumors within the neuroaxis is uncommon. Even rarer is the finding within brain parenchyma, termed malignant intracerebral nerve sheath tumors (MINST). We present a case of MINST which occurred in the frontal lobe of an 18-year-old male that recurred almost 4 years later. Imaging demonstrated a 4.0 cm lesion with an associated mass effect. He underwent a right fronto-parietal craniotomy for gross total resection. Pathology was inconclusive with a Glioblastoma Multiforme (GBM) as the most likely diagnosis, though gliosarcoma and MINST were also highly considered. Postoperatively, he was treated with chemotherapy and radiation and followed for almost 4 years, when an MRI indicated a recurrence. Resection of the recurrence was highly suggestive of MINST. Surgery was followed by radiation and chemotherapy, but, less than 7 months later, he was readmitted for a surgical-site infection, and, after multiple surgeries, and his family terminated care. Recognizing this unusual tumor in the differential diagnosis of a heterogeneously enhancing intracerebral mass can help surgeons diagnose and treat it. This report also exhaustively reviews the literature and presents diagnostic and treatment strategies.
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spelling doaj-art-af4cd3ab3554432994f52b4dc1c835932025-08-20T02:19:07ZengWileyCase Reports in Surgery2090-69002090-69192013-01-01201310.1155/2013/384076384076Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the LiteratureFaris Shweikeh0Doniel Drazin1Sergei I. Bannykh2Department of Neurosurgery, Cedars-Sinai Medical Center, Maxine Dunitz Neurosurgical Institute, Los Angeles, CA 90048, USADepartment of Neurosurgery, Cedars-Sinai Medical Center, Maxine Dunitz Neurosurgical Institute, Los Angeles, CA 90048, USADepartment of Pathology and Laboratory Medicine, Cedars-Sinai Medical Center, Los Angeles, CA 90048, USAThe occurrence of benign nerve sheath tumors within the neuroaxis is uncommon. Even rarer is the finding within brain parenchyma, termed malignant intracerebral nerve sheath tumors (MINST). We present a case of MINST which occurred in the frontal lobe of an 18-year-old male that recurred almost 4 years later. Imaging demonstrated a 4.0 cm lesion with an associated mass effect. He underwent a right fronto-parietal craniotomy for gross total resection. Pathology was inconclusive with a Glioblastoma Multiforme (GBM) as the most likely diagnosis, though gliosarcoma and MINST were also highly considered. Postoperatively, he was treated with chemotherapy and radiation and followed for almost 4 years, when an MRI indicated a recurrence. Resection of the recurrence was highly suggestive of MINST. Surgery was followed by radiation and chemotherapy, but, less than 7 months later, he was readmitted for a surgical-site infection, and, after multiple surgeries, and his family terminated care. Recognizing this unusual tumor in the differential diagnosis of a heterogeneously enhancing intracerebral mass can help surgeons diagnose and treat it. This report also exhaustively reviews the literature and presents diagnostic and treatment strategies.http://dx.doi.org/10.1155/2013/384076
spellingShingle Faris Shweikeh
Doniel Drazin
Sergei I. Bannykh
Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature
Case Reports in Surgery
title Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature
title_full Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature
title_fullStr Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature
title_full_unstemmed Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature
title_short Malignant Intracerebral Nerve Sheath Tumors: A Case Report with Review of the Literature
title_sort malignant intracerebral nerve sheath tumors a case report with review of the literature
url http://dx.doi.org/10.1155/2013/384076
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AT sergeiibannykh malignantintracerebralnervesheathtumorsacasereportwithreviewoftheliterature