Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia

Monoclonal gammopathy can be seen at an early age in patients with warts-hypogammaglobulinemia, infections, and myelokathexis syndrome and can mask the presence of hypogammaglobulinemia.

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Main Authors: Julia Lew, MD, Adil Adatia, MD
Format: Article
Language:English
Published: Elsevier 2025-08-01
Series:Journal of Allergy and Clinical Immunology: Global
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2772829325001274
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author Julia Lew, MD
Adil Adatia, MD
author_facet Julia Lew, MD
Adil Adatia, MD
author_sort Julia Lew, MD
collection DOAJ
description Monoclonal gammopathy can be seen at an early age in patients with warts-hypogammaglobulinemia, infections, and myelokathexis syndrome and can mask the presence of hypogammaglobulinemia.
format Article
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institution Kabale University
issn 2772-8293
language English
publishDate 2025-08-01
publisher Elsevier
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series Journal of Allergy and Clinical Immunology: Global
spelling doaj-art-af4ba25f40494ad98e7dc4a02edf5d352025-08-20T03:57:39ZengElsevierJournal of Allergy and Clinical Immunology: Global2772-82932025-08-014310052610.1016/j.jacig.2025.100526Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemiaJulia Lew, MD0Adil Adatia, MD1Department of Pediatrics, University of Toronto, Toronto, OntarioDivision of Pulmonary Medicine, Department of Medicine, University of Alberta, Edmonton, Alberta, Canada; Corresponding author: Adil Adatia, MD, Division of Pulmonary Medicine, Department of Medicine, University of Alberta, 3D-11400 University Ave, Edmonton, AB, Canada T6G 1Z1.Monoclonal gammopathy can be seen at an early age in patients with warts-hypogammaglobulinemia, infections, and myelokathexis syndrome and can mask the presence of hypogammaglobulinemia.http://www.sciencedirect.com/science/article/pii/S2772829325001274WHIM syndromesecondary hypogammaglobulinemiainborn error of immunitymonoclonal gammopathyimmunoparesis
spellingShingle Julia Lew, MD
Adil Adatia, MD
Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia
Journal of Allergy and Clinical Immunology: Global
WHIM syndrome
secondary hypogammaglobulinemia
inborn error of immunity
monoclonal gammopathy
immunoparesis
title Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia
title_full Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia
title_fullStr Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia
title_full_unstemmed Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia
title_short Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia
title_sort monoclonal gammopathy in whim syndrome can mask hypogammaglobulinemia
topic WHIM syndrome
secondary hypogammaglobulinemia
inborn error of immunity
monoclonal gammopathy
immunoparesis
url http://www.sciencedirect.com/science/article/pii/S2772829325001274
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