Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation

Juvenile Dermatomyositis (JDM) is a rare autoimmune disease in children and adolescents. In these patients calcinosis might be the most characteristic symptom. However there are only few reported cases of intramuscular calcinosis in Dermatomyositis. We report a case of calcinosis universalis (CU) of...

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Main Authors: Sebastian Philipp Boelch, Thomas Barthel, Sascha Goebel, Maximilian Rudert, Piet Plumhoff
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Orthopedics
Online Access:http://dx.doi.org/10.1155/2015/505420
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author Sebastian Philipp Boelch
Thomas Barthel
Sascha Goebel
Maximilian Rudert
Piet Plumhoff
author_facet Sebastian Philipp Boelch
Thomas Barthel
Sascha Goebel
Maximilian Rudert
Piet Plumhoff
author_sort Sebastian Philipp Boelch
collection DOAJ
description Juvenile Dermatomyositis (JDM) is a rare autoimmune disease in children and adolescents. In these patients calcinosis might be the most characteristic symptom. However there are only few reported cases of intramuscular calcinosis in Dermatomyositis. We report a case of calcinosis universalis (CU) of the elbow in JDM successfully treated with broaching. The patient, a 24-year-old woman, suffered from a long history of JDM. On examination she presented with a fistula lateral to the olecranon and pain of the right elbow joint. Plain X-rays displayed a diffuse pattern of multiple periarticular, subcutaneous, and intramuscular calcifications. The patient underwent surgery for histological and microbiological sampling as well as broaching. Intraoperatively sinus formation and subfascial hard calcium deposition were found. Due to the risk of collateral tissue damage, incomplete broaching was performed. A local infection with Staphylococcus was diagnosed and treated with antibiotics. On six-week and 30-month follow-up the patient was free of pain and had very good function. Calcifications on standard radiographs had almost resolved entirely. This case report gives a summary on calcinosis in Dermatomyositis and adds a new case of recalcitrant CU to the literature. Broaching surgery proved to be a reliable treatment option in symptomatic calcinosis.
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spelling doaj-art-acc28f8a45264b9586188790f4920c242025-02-03T01:02:27ZengWileyCase Reports in Orthopedics2090-67492090-67572015-01-01201510.1155/2015/505420505420Calcinosis Universalis of the Elbow: A Rare Case with Classical PresentationSebastian Philipp Boelch0Thomas Barthel1Sascha Goebel2Maximilian Rudert3Piet Plumhoff4Department of Orthopaedic Surgery, The University of Würzburg, König Ludwig Haus, Brettreichstrasse 11, 97074 Würzburg, GermanyDepartment of Orthopaedic Surgery, The University of Würzburg, König Ludwig Haus, Brettreichstrasse 11, 97074 Würzburg, GermanyHelios Klinik Volkach, Schaubmühlstrasse 2, 97332 Volkach, GermanyDepartment of Orthopaedic Surgery, The University of Würzburg, König Ludwig Haus, Brettreichstrasse 11, 97074 Würzburg, GermanyDepartment of Orthopaedic Surgery, The University of Würzburg, König Ludwig Haus, Brettreichstrasse 11, 97074 Würzburg, GermanyJuvenile Dermatomyositis (JDM) is a rare autoimmune disease in children and adolescents. In these patients calcinosis might be the most characteristic symptom. However there are only few reported cases of intramuscular calcinosis in Dermatomyositis. We report a case of calcinosis universalis (CU) of the elbow in JDM successfully treated with broaching. The patient, a 24-year-old woman, suffered from a long history of JDM. On examination she presented with a fistula lateral to the olecranon and pain of the right elbow joint. Plain X-rays displayed a diffuse pattern of multiple periarticular, subcutaneous, and intramuscular calcifications. The patient underwent surgery for histological and microbiological sampling as well as broaching. Intraoperatively sinus formation and subfascial hard calcium deposition were found. Due to the risk of collateral tissue damage, incomplete broaching was performed. A local infection with Staphylococcus was diagnosed and treated with antibiotics. On six-week and 30-month follow-up the patient was free of pain and had very good function. Calcifications on standard radiographs had almost resolved entirely. This case report gives a summary on calcinosis in Dermatomyositis and adds a new case of recalcitrant CU to the literature. Broaching surgery proved to be a reliable treatment option in symptomatic calcinosis.http://dx.doi.org/10.1155/2015/505420
spellingShingle Sebastian Philipp Boelch
Thomas Barthel
Sascha Goebel
Maximilian Rudert
Piet Plumhoff
Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation
Case Reports in Orthopedics
title Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation
title_full Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation
title_fullStr Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation
title_full_unstemmed Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation
title_short Calcinosis Universalis of the Elbow: A Rare Case with Classical Presentation
title_sort calcinosis universalis of the elbow a rare case with classical presentation
url http://dx.doi.org/10.1155/2015/505420
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AT saschagoebel calcinosisuniversalisoftheelbowararecasewithclassicalpresentation
AT maximilianrudert calcinosisuniversalisoftheelbowararecasewithclassicalpresentation
AT pietplumhoff calcinosisuniversalisoftheelbowararecasewithclassicalpresentation