A Rare Diagnosis of Caroli Syndrome in a Young Patient
ABSTRACT Caroli syndrome is a rare but serious congenital disorder associated with portal hypertension and polycystic kidney disease. Early diagnosis via imaging, particularly MRCP, is crucial to prevent life‐threatening complications such as cholangitis and biliary cirrhosis. Timely intervention an...
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| Format: | Article |
| Language: | English |
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Wiley
2025-06-01
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| Series: | Clinical Case Reports |
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| Online Access: | https://doi.org/10.1002/ccr3.70555 |
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| author | Elaheh Karimzadeh‐Soureshjani Farab Pourhasan Pouria Ahmadi Simab Sajjad Shojaei Yasaman Mohammadian |
| author_facet | Elaheh Karimzadeh‐Soureshjani Farab Pourhasan Pouria Ahmadi Simab Sajjad Shojaei Yasaman Mohammadian |
| author_sort | Elaheh Karimzadeh‐Soureshjani |
| collection | DOAJ |
| description | ABSTRACT Caroli syndrome is a rare but serious congenital disorder associated with portal hypertension and polycystic kidney disease. Early diagnosis via imaging, particularly MRCP, is crucial to prevent life‐threatening complications such as cholangitis and biliary cirrhosis. Timely intervention and close monitoring can significantly improve patient outcomes. |
| format | Article |
| id | doaj-art-ac3d3137122b4eb698f85992d8ad100e |
| institution | DOAJ |
| issn | 2050-0904 |
| language | English |
| publishDate | 2025-06-01 |
| publisher | Wiley |
| record_format | Article |
| series | Clinical Case Reports |
| spelling | doaj-art-ac3d3137122b4eb698f85992d8ad100e2025-08-20T03:23:06ZengWileyClinical Case Reports2050-09042025-06-01136n/an/a10.1002/ccr3.70555A Rare Diagnosis of Caroli Syndrome in a Young PatientElaheh Karimzadeh‐Soureshjani0Farab Pourhasan1Pouria Ahmadi Simab2Sajjad Shojaei3Yasaman Mohammadian4Department of Clinical Sciences Abadan University of Medical Sciences Abadan IranDepartment of Clinical Sciences Abadan University of Medical Sciences Abadan IranUniversal Scientific Education and Research Network (USERN) Tehran IranDepartment of Radiology Taleghani Hospital, Abadan University of Medical Sciences Abadan IranAbadan University of Medical Sciences Abadan IranABSTRACT Caroli syndrome is a rare but serious congenital disorder associated with portal hypertension and polycystic kidney disease. Early diagnosis via imaging, particularly MRCP, is crucial to prevent life‐threatening complications such as cholangitis and biliary cirrhosis. Timely intervention and close monitoring can significantly improve patient outcomes.https://doi.org/10.1002/ccr3.70555autosomal recessive polycystic kidney diseaseCaroli syndromeliver cystsmedullary sponge kidneyMRCP |
| spellingShingle | Elaheh Karimzadeh‐Soureshjani Farab Pourhasan Pouria Ahmadi Simab Sajjad Shojaei Yasaman Mohammadian A Rare Diagnosis of Caroli Syndrome in a Young Patient Clinical Case Reports autosomal recessive polycystic kidney disease Caroli syndrome liver cysts medullary sponge kidney MRCP |
| title | A Rare Diagnosis of Caroli Syndrome in a Young Patient |
| title_full | A Rare Diagnosis of Caroli Syndrome in a Young Patient |
| title_fullStr | A Rare Diagnosis of Caroli Syndrome in a Young Patient |
| title_full_unstemmed | A Rare Diagnosis of Caroli Syndrome in a Young Patient |
| title_short | A Rare Diagnosis of Caroli Syndrome in a Young Patient |
| title_sort | rare diagnosis of caroli syndrome in a young patient |
| topic | autosomal recessive polycystic kidney disease Caroli syndrome liver cysts medullary sponge kidney MRCP |
| url | https://doi.org/10.1002/ccr3.70555 |
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