Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report

Background. The Vein of Galen aneurysmal malformation (VGAM) is a rare congenital, cerebral, arteriovenous deformity. Good cross-discipline cooperation is in demand because of associated complications and high mortality. The recognition of the optimal therapeutic window is useful to allow proper man...

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Main Authors: S. Stephan, G. Rodesch, E. Elolf, D. Wiemann, G. Jorch
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Pediatrics
Online Access:http://dx.doi.org/10.1155/2012/824284
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author S. Stephan
G. Rodesch
E. Elolf
D. Wiemann
G. Jorch
author_facet S. Stephan
G. Rodesch
E. Elolf
D. Wiemann
G. Jorch
author_sort S. Stephan
collection DOAJ
description Background. The Vein of Galen aneurysmal malformation (VGAM) is a rare congenital, cerebral, arteriovenous deformity. Good cross-discipline cooperation is in demand because of associated complications and high mortality. The recognition of the optimal therapeutic window is useful to allow proper management. Case Report. We report on the successful treatment of a 2-week-old, healthy girl with a VGAM, which came across in the context of the newborn ultrasonographic screening. After interdisciplinary discussion, 2 embolizations of the VGAM followed without complications—the first in the age of 6 months and the second at 12 months of life. Before and after the intervention, the patient had an age-appropriate development without neurological deficits. Conclusion. The endovascular transarterial embolization is described as the treatment of choice. Time and method of intervention depend on clinical signs of the patient. In our case the patient was asymptomatic. So the arteriovenous abnormality was an incidental finding by ultrasound. Because of the natural history of the disease, and the potential severe neurocognitive consequences at long-term followup if left untreated, it was decided to embolize the lesion. Thanks to embolization with glue, good therapeutical and clinical results could be obtained with normal neurological development.
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spelling doaj-art-abcfff555e324d1b83dc482a3a0d4a062025-02-03T01:10:09ZengWileyCase Reports in Pediatrics2090-68032090-68112012-01-01201210.1155/2012/824284824284Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case ReportS. Stephan0G. Rodesch1E. Elolf2D. Wiemann3G. Jorch4Department of Pediatrics, Otto-von-Guericke-University Magdeburg, 39120 Magdeburg, GermanyService de Neuroradiologie Diagnostique et Thérapeutique, Hôpital Foch, Suresnes, FranceDepartment of Radiology and Neuroradiology, International Neuroscience Institute, Hannover, GermanyDepartment of Pediatrics, Otto-von-Guericke-University Magdeburg, 39120 Magdeburg, GermanyDepartment of Pediatrics, Otto-von-Guericke-University Magdeburg, 39120 Magdeburg, GermanyBackground. The Vein of Galen aneurysmal malformation (VGAM) is a rare congenital, cerebral, arteriovenous deformity. Good cross-discipline cooperation is in demand because of associated complications and high mortality. The recognition of the optimal therapeutic window is useful to allow proper management. Case Report. We report on the successful treatment of a 2-week-old, healthy girl with a VGAM, which came across in the context of the newborn ultrasonographic screening. After interdisciplinary discussion, 2 embolizations of the VGAM followed without complications—the first in the age of 6 months and the second at 12 months of life. Before and after the intervention, the patient had an age-appropriate development without neurological deficits. Conclusion. The endovascular transarterial embolization is described as the treatment of choice. Time and method of intervention depend on clinical signs of the patient. In our case the patient was asymptomatic. So the arteriovenous abnormality was an incidental finding by ultrasound. Because of the natural history of the disease, and the potential severe neurocognitive consequences at long-term followup if left untreated, it was decided to embolize the lesion. Thanks to embolization with glue, good therapeutical and clinical results could be obtained with normal neurological development.http://dx.doi.org/10.1155/2012/824284
spellingShingle S. Stephan
G. Rodesch
E. Elolf
D. Wiemann
G. Jorch
Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report
Case Reports in Pediatrics
title Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report
title_full Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report
title_fullStr Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report
title_full_unstemmed Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report
title_short Vein of Galen Aneurysmal Malformations: An Ultrasonographic Incidental Finding—A Case Report
title_sort vein of galen aneurysmal malformations an ultrasonographic incidental finding a case report
url http://dx.doi.org/10.1155/2012/824284
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