Peutz–Jeghers syndrome: review of the literature and clinical case presentation

The aim of publication. To show complexities of diagnostics and treatment at hereditary multiple gastrointestinal polyposis by the example of clinical case.Features of clinical case. At the patient with PeutzJeghers syndrome, despite of well-timed diagnosis, annual screening and treatment, it was no...

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Main Authors: V. O. Kaybysheva, V. T. Ivashkin, Ye. K. Baranskaya, O. S. Shifrin, K. V. Pyurveyeva, A. Ye. Leonovich, O. A. Sklyanskaya, A. A. Sheptulin
Format: Article
Language:Russian
Published: Gastro LLC 2011-03-01
Series:Российский журнал гастроэнтерологии, гепатологии, колопроктологии
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Online Access:https://www.gastro-j.ru/jour/article/view/1392
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author V. O. Kaybysheva
V. T. Ivashkin
Ye. K. Baranskaya
O. S. Shifrin
K. V. Pyurveyeva
A. Ye. Leonovich
O. A. Sklyanskaya
A. A. Sheptulin
author_facet V. O. Kaybysheva
V. T. Ivashkin
Ye. K. Baranskaya
O. S. Shifrin
K. V. Pyurveyeva
A. Ye. Leonovich
O. A. Sklyanskaya
A. A. Sheptulin
author_sort V. O. Kaybysheva
collection DOAJ
description The aim of publication. To show complexities of diagnostics and treatment at hereditary multiple gastrointestinal polyposis by the example of clinical case.Features of clinical case. At the patient with PeutzJeghers syndrome, despite of well-timed diagnosis, annual screening and treatment, it was not possible to avoid development of serious complications. Recurrent bleedings from polyps and intestinal obstruction became the cause of four extensive resections of the small and large intestine that resulted in development of short bowel syndrome and disability of the patient.Conclusion. Now there is no pathogenically proved treatment of Peutz-Jeghers syndrome. The main management approach consists in dynamic observation and the prevention of fatal complications.
format Article
id doaj-art-abb6c9e7fee440e29c5f8739652198bb
institution Kabale University
issn 1382-4376
2658-6673
language Russian
publishDate 2011-03-01
publisher Gastro LLC
record_format Article
series Российский журнал гастроэнтерологии, гепатологии, колопроктологии
spelling doaj-art-abb6c9e7fee440e29c5f8739652198bb2025-02-10T16:14:31ZrusGastro LLCРоссийский журнал гастроэнтерологии, гепатологии, колопроктологии1382-43762658-66732011-03-012125461945Peutz–Jeghers syndrome: review of the literature and clinical case presentationV. O. Kaybysheva0V. T. Ivashkin1Ye. K. Baranskaya2O. S. Shifrin3K. V. Pyurveyeva4A. Ye. Leonovich5O. A. Sklyanskaya6A. A. Sheptulin7ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»ГОУ ВПО «1-й Московский государственный медицинский университет им. И.М. Сеченова Росздрава»The aim of publication. To show complexities of diagnostics and treatment at hereditary multiple gastrointestinal polyposis by the example of clinical case.Features of clinical case. At the patient with PeutzJeghers syndrome, despite of well-timed diagnosis, annual screening and treatment, it was not possible to avoid development of serious complications. Recurrent bleedings from polyps and intestinal obstruction became the cause of four extensive resections of the small and large intestine that resulted in development of short bowel syndrome and disability of the patient.Conclusion. Now there is no pathogenically proved treatment of Peutz-Jeghers syndrome. The main management approach consists in dynamic observation and the prevention of fatal complications.https://www.gastro-j.ru/jour/article/view/1392peutz-jeghers syndromemultiple polyposis of gastro-intestinal tract
spellingShingle V. O. Kaybysheva
V. T. Ivashkin
Ye. K. Baranskaya
O. S. Shifrin
K. V. Pyurveyeva
A. Ye. Leonovich
O. A. Sklyanskaya
A. A. Sheptulin
Peutz–Jeghers syndrome: review of the literature and clinical case presentation
Российский журнал гастроэнтерологии, гепатологии, колопроктологии
peutz-jeghers syndrome
multiple polyposis of gastro-intestinal tract
title Peutz–Jeghers syndrome: review of the literature and clinical case presentation
title_full Peutz–Jeghers syndrome: review of the literature and clinical case presentation
title_fullStr Peutz–Jeghers syndrome: review of the literature and clinical case presentation
title_full_unstemmed Peutz–Jeghers syndrome: review of the literature and clinical case presentation
title_short Peutz–Jeghers syndrome: review of the literature and clinical case presentation
title_sort peutz jeghers syndrome review of the literature and clinical case presentation
topic peutz-jeghers syndrome
multiple polyposis of gastro-intestinal tract
url https://www.gastro-j.ru/jour/article/view/1392
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AT osshifrin peutzjegherssyndromereviewoftheliteratureandclinicalcasepresentation
AT kvpyurveyeva peutzjegherssyndromereviewoftheliteratureandclinicalcasepresentation
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