Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman

Esthesioneuroblastoma (ENB) is a rare malignant tumor that commonly develops in the upper nasal cavity. Standard treatment is not established, especially in locally advanced disease which portends the worse prognosis. Hereby, we report a case of a 27-year-old, 23-week pregnant woman, with a 2-month...

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Main Authors: Inês Maria Guerreiro, Cláudia Vieira, André Soares, António Braga, Manuel Jácome, José Dinis
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Case Reports in Oncological Medicine
Online Access:http://dx.doi.org/10.1155/2019/3789317
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author Inês Maria Guerreiro
Cláudia Vieira
André Soares
António Braga
Manuel Jácome
José Dinis
author_facet Inês Maria Guerreiro
Cláudia Vieira
André Soares
António Braga
Manuel Jácome
José Dinis
author_sort Inês Maria Guerreiro
collection DOAJ
description Esthesioneuroblastoma (ENB) is a rare malignant tumor that commonly develops in the upper nasal cavity. Standard treatment is not established, especially in locally advanced disease which portends the worse prognosis. Hereby, we report a case of a 27-year-old, 23-week pregnant woman, with a 2-month history of progressively growing right cervical lymphadenopathy, nasal obstruction, anosmia, frequent episodes of epistaxis, and right frontal headache. Imagiological evaluation revealed a lesion with 7×5,2×3,2 cm in the nasal fossae with extension to the ethmoidal complex and right olfactive fend and invasion of the endocranial compartment associated with lymphadenopathy. The biopsy revealed a high-grade EBN. Neoadjuvant chemotherapy with cisplatin and etoposide was administrated during pregnancy and continued after delivery up to 6 cycles of treatment with partial response. Radiotherapy followed, with complete response. This case report is intended to highlight that a high grade of suspicion should be kept in the presence of nonspecific symptoms of nasal obstruction, anosmia, facial pain, and/or headache and focus that chemotherapy is an important component of a combined-treatment modality for locally advanced ENB that can be used during pregnancy in a lifesaving situation.
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spelling doaj-art-aa8d484a2b254274a712f208d97db26e2025-08-20T03:39:35ZengWileyCase Reports in Oncological Medicine2090-67062090-67142019-01-01201910.1155/2019/37893173789317Management of Locally Advanced Esthesioneuroblastoma in a Pregnant WomanInês Maria Guerreiro0Cláudia Vieira1André Soares2António Braga3Manuel Jácome4José Dinis5Medical Oncology Department, Instituto Português de Oncologia do Porto Francisco Gentil (IPO-PORTO), Porto, PortugalMedical Oncology Department, Instituto Português de Oncologia do Porto Francisco Gentil (IPO-PORTO), Porto, PortugalRadiation Oncology Department, Instituto Português de Oncologia do Porto Francisco Gentil (IPO-PORTO), Porto, PortugalDepartment of Obstetrics and Gynecology, Centro Hospitalar do Porto, Porto, PortugalPathology Department, Instituto Português de Oncologia do Porto Francisco Gentil (IPO-PORTO), Porto, PortugalMedical Oncology Department, Instituto Português de Oncologia do Porto Francisco Gentil (IPO-PORTO), Porto, PortugalEsthesioneuroblastoma (ENB) is a rare malignant tumor that commonly develops in the upper nasal cavity. Standard treatment is not established, especially in locally advanced disease which portends the worse prognosis. Hereby, we report a case of a 27-year-old, 23-week pregnant woman, with a 2-month history of progressively growing right cervical lymphadenopathy, nasal obstruction, anosmia, frequent episodes of epistaxis, and right frontal headache. Imagiological evaluation revealed a lesion with 7×5,2×3,2 cm in the nasal fossae with extension to the ethmoidal complex and right olfactive fend and invasion of the endocranial compartment associated with lymphadenopathy. The biopsy revealed a high-grade EBN. Neoadjuvant chemotherapy with cisplatin and etoposide was administrated during pregnancy and continued after delivery up to 6 cycles of treatment with partial response. Radiotherapy followed, with complete response. This case report is intended to highlight that a high grade of suspicion should be kept in the presence of nonspecific symptoms of nasal obstruction, anosmia, facial pain, and/or headache and focus that chemotherapy is an important component of a combined-treatment modality for locally advanced ENB that can be used during pregnancy in a lifesaving situation.http://dx.doi.org/10.1155/2019/3789317
spellingShingle Inês Maria Guerreiro
Cláudia Vieira
André Soares
António Braga
Manuel Jácome
José Dinis
Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman
Case Reports in Oncological Medicine
title Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman
title_full Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman
title_fullStr Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman
title_full_unstemmed Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman
title_short Management of Locally Advanced Esthesioneuroblastoma in a Pregnant Woman
title_sort management of locally advanced esthesioneuroblastoma in a pregnant woman
url http://dx.doi.org/10.1155/2019/3789317
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