The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway

Abstract Rafeesome, a newly identified multivesicular body (MVB)-like organelle, forms through the fusion of RAB22A-mediated ER-derived noncanonical autophagosomes with RAB22A-positive early endosomes. However, the mechanism underlying the formation of RAB22A-mediated noncanonical autophagosomes rem...

Full description

Saved in:
Bibliographic Details
Main Authors: Xueping Zheng, Dongmei Fang, Hao Shan, Beibei Xiao, Denghui Wei, Yingyi Ouyang, Lanqing Huo, Zhonghan Zhang, Yuanzhong Wu, Ruhua Zhang, Tiebang Kang, Ying Gao
Format: Article
Language:English
Published: Nature Publishing Group 2025-04-01
Series:Cell Discovery
Online Access:https://doi.org/10.1038/s41421-025-00792-2
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850206490654146560
author Xueping Zheng
Dongmei Fang
Hao Shan
Beibei Xiao
Denghui Wei
Yingyi Ouyang
Lanqing Huo
Zhonghan Zhang
Yuanzhong Wu
Ruhua Zhang
Tiebang Kang
Ying Gao
author_facet Xueping Zheng
Dongmei Fang
Hao Shan
Beibei Xiao
Denghui Wei
Yingyi Ouyang
Lanqing Huo
Zhonghan Zhang
Yuanzhong Wu
Ruhua Zhang
Tiebang Kang
Ying Gao
author_sort Xueping Zheng
collection DOAJ
description Abstract Rafeesome, a newly identified multivesicular body (MVB)-like organelle, forms through the fusion of RAB22A-mediated ER-derived noncanonical autophagosomes with RAB22A-positive early endosomes. However, the mechanism underlying the formation of RAB22A-mediated noncanonical autophagosomes remains unclear. Herein, we report a secretory ER-phagy pathway in which the assembly of RAB22A/TMEM33/RTN4 induces the clustering of high-molecular-weight RTN4 oligomers, leading to ER membrane remodeling. This remodeling drives the biogenesis of ER-derived RTN4-positive noncanonical autophagosomes, which are ultimately secreted as TMEM33-marked RAB22A-induced extracellular vesicles (R-EVs) via Rafeesome. Specifically, RAB22A interacts with the tubular ER membrane protein TMEM33, which binds to the TM2 domain of the ER-shaping protein RTN4, promoting RTN4 homo-oligomerization and thereby generating RTN4-enriched microdomains. Consequently, the RTN4 microdomains may induce high curvature of the ER, facilitating the bud scission of RTN4-positive vesicles. These vesicles are transported by ATG9A and develop into isolation membranes (IMs), which are then anchored by LC3-II, a process catalyzed by the ATG12-ATG5-ATG16L1 complex, allowing them to grow into sealed RTN4 noncanonical autophagosome. While being packaged into these ER-derived intermediate compartments, ER cargoes bypass lysosomal degradation and are directed to secretory autophagy via the Rafeesome-R-EV route. Our findings reveal a secretory ER-phagy pathway initiated by the assembly of RAB22A/TMEM33/RTN4, providing new insights into the connection between ER-phagy and extracellular vesicles.
format Article
id doaj-art-aa67f47be0af45c8a8906e5e90324b73
institution OA Journals
issn 2056-5968
language English
publishDate 2025-04-01
publisher Nature Publishing Group
record_format Article
series Cell Discovery
spelling doaj-art-aa67f47be0af45c8a8906e5e90324b732025-08-20T02:10:49ZengNature Publishing GroupCell Discovery2056-59682025-04-0111111610.1038/s41421-025-00792-2The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathwayXueping Zheng0Dongmei Fang1Hao Shan2Beibei Xiao3Denghui Wei4Yingyi Ouyang5Lanqing Huo6Zhonghan Zhang7Yuanzhong Wu8Ruhua Zhang9Tiebang Kang10Ying Gao11Sun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerSun Yat-sen University Cancer Center, State Key Laboratory of Oncology in South China, Guangdong Provincial Clinical Research Center for CancerAbstract Rafeesome, a newly identified multivesicular body (MVB)-like organelle, forms through the fusion of RAB22A-mediated ER-derived noncanonical autophagosomes with RAB22A-positive early endosomes. However, the mechanism underlying the formation of RAB22A-mediated noncanonical autophagosomes remains unclear. Herein, we report a secretory ER-phagy pathway in which the assembly of RAB22A/TMEM33/RTN4 induces the clustering of high-molecular-weight RTN4 oligomers, leading to ER membrane remodeling. This remodeling drives the biogenesis of ER-derived RTN4-positive noncanonical autophagosomes, which are ultimately secreted as TMEM33-marked RAB22A-induced extracellular vesicles (R-EVs) via Rafeesome. Specifically, RAB22A interacts with the tubular ER membrane protein TMEM33, which binds to the TM2 domain of the ER-shaping protein RTN4, promoting RTN4 homo-oligomerization and thereby generating RTN4-enriched microdomains. Consequently, the RTN4 microdomains may induce high curvature of the ER, facilitating the bud scission of RTN4-positive vesicles. These vesicles are transported by ATG9A and develop into isolation membranes (IMs), which are then anchored by LC3-II, a process catalyzed by the ATG12-ATG5-ATG16L1 complex, allowing them to grow into sealed RTN4 noncanonical autophagosome. While being packaged into these ER-derived intermediate compartments, ER cargoes bypass lysosomal degradation and are directed to secretory autophagy via the Rafeesome-R-EV route. Our findings reveal a secretory ER-phagy pathway initiated by the assembly of RAB22A/TMEM33/RTN4, providing new insights into the connection between ER-phagy and extracellular vesicles.https://doi.org/10.1038/s41421-025-00792-2
spellingShingle Xueping Zheng
Dongmei Fang
Hao Shan
Beibei Xiao
Denghui Wei
Yingyi Ouyang
Lanqing Huo
Zhonghan Zhang
Yuanzhong Wu
Ruhua Zhang
Tiebang Kang
Ying Gao
The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway
Cell Discovery
title The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway
title_full The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway
title_fullStr The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway
title_full_unstemmed The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway
title_short The assembly of RAB22A/TMEM33/RTN4 initiates a secretory ER-phagy pathway
title_sort assembly of rab22a tmem33 rtn4 initiates a secretory er phagy pathway
url https://doi.org/10.1038/s41421-025-00792-2
work_keys_str_mv AT xuepingzheng theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT dongmeifang theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT haoshan theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT beibeixiao theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT denghuiwei theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT yingyiouyang theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT lanqinghuo theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT zhonghanzhang theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT yuanzhongwu theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT ruhuazhang theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT tiebangkang theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT yinggao theassemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT xuepingzheng assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT dongmeifang assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT haoshan assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT beibeixiao assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT denghuiwei assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT yingyiouyang assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT lanqinghuo assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT zhonghanzhang assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT yuanzhongwu assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT ruhuazhang assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT tiebangkang assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway
AT yinggao assemblyofrab22atmem33rtn4initiatesasecretoryerphagypathway