Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography

Annuloaortic ectasia is a relatively rare diagnosis. Herein, we report an unusual case of an annuloaortic ectasia with asymmetric dilatation of the right coronary bulb mimicking a membranous ventricular septal defect (VSD) with Eisenmenger reaction by transthoracic echocardiography. Aortic angiograp...

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Main Authors: Nina P. Hofmann, Hassan Abdel-Aty, Stefan Siebert, Hugo A. Katus, Grigorios Korosoglou
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2012/524526
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author Nina P. Hofmann
Hassan Abdel-Aty
Stefan Siebert
Hugo A. Katus
Grigorios Korosoglou
author_facet Nina P. Hofmann
Hassan Abdel-Aty
Stefan Siebert
Hugo A. Katus
Grigorios Korosoglou
author_sort Nina P. Hofmann
collection DOAJ
description Annuloaortic ectasia is a relatively rare diagnosis. Herein, we report an unusual case of an annuloaortic ectasia with asymmetric dilatation of the right coronary bulb mimicking a membranous ventricular septal defect (VSD) with Eisenmenger reaction by transthoracic echocardiography. Aortic angiography showed a dilated aortic root and moderate aortic regurgitation. Right cardiac catheterization, on the other hand, exhibited normal pulmonary artery blood pressure and normal pulmonary resistance, whereas normal venous gas values were measured throughout the caval vein and the right atrium, excluding relevant left-right shunting. Further diagnostic workup by cardiac computed tomography angiography (CCTA) unambiguously illustrated the asymmetric geometry of the ectatic aortic cusp and root causing compression of the right heart and of the right ventricular (RV) outflow tract. After review of echocardiographic acquisitions, the blood flow detected between the left and right ventricles (mimicking VSD) was interpreted as turbulent inflow from the left ventricle into the ectatic right coronary cusp. Furthermore, elevated pulmonary artery blood pressure measured by echocardiography was attributed to “functional pulmonary stenosis” due to compression of the RV outflow tract by the aorta, as demonstrated by CCTA.
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spelling doaj-art-aa20de9f54db46b990efe4e66b3eef692025-08-20T03:39:32ZengWileyCase Reports in Medicine1687-96271687-96352012-01-01201210.1155/2012/524526524526Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed TomographyNina P. Hofmann0Hassan Abdel-Aty1Stefan Siebert2Hugo A. Katus3Grigorios Korosoglou4Department of Cardiology, Heidelberg University, Im Neuenheimer Feld 410, 69120 Heidelberg, GermanyDepartment of Cardiology, Heidelberg University, Im Neuenheimer Feld 410, 69120 Heidelberg, GermanyDepartment of Radiology, Heidelberg University, Im Neuenheimer Feld 410, 69120 Heidelberg, GermanyDepartment of Cardiology, Heidelberg University, Im Neuenheimer Feld 410, 69120 Heidelberg, GermanyDepartment of Cardiology, Heidelberg University, Im Neuenheimer Feld 410, 69120 Heidelberg, GermanyAnnuloaortic ectasia is a relatively rare diagnosis. Herein, we report an unusual case of an annuloaortic ectasia with asymmetric dilatation of the right coronary bulb mimicking a membranous ventricular septal defect (VSD) with Eisenmenger reaction by transthoracic echocardiography. Aortic angiography showed a dilated aortic root and moderate aortic regurgitation. Right cardiac catheterization, on the other hand, exhibited normal pulmonary artery blood pressure and normal pulmonary resistance, whereas normal venous gas values were measured throughout the caval vein and the right atrium, excluding relevant left-right shunting. Further diagnostic workup by cardiac computed tomography angiography (CCTA) unambiguously illustrated the asymmetric geometry of the ectatic aortic cusp and root causing compression of the right heart and of the right ventricular (RV) outflow tract. After review of echocardiographic acquisitions, the blood flow detected between the left and right ventricles (mimicking VSD) was interpreted as turbulent inflow from the left ventricle into the ectatic right coronary cusp. Furthermore, elevated pulmonary artery blood pressure measured by echocardiography was attributed to “functional pulmonary stenosis” due to compression of the RV outflow tract by the aorta, as demonstrated by CCTA.http://dx.doi.org/10.1155/2012/524526
spellingShingle Nina P. Hofmann
Hassan Abdel-Aty
Stefan Siebert
Hugo A. Katus
Grigorios Korosoglou
Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography
Case Reports in Medicine
title Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography
title_full Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography
title_fullStr Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography
title_full_unstemmed Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography
title_short Giant Dilatation of the Right Coronary Aortic Bulb with Compression of the Right Ventricular Outflow Tract Mimicking a Ventricular Septal Defect: Diagnostic workup Using Echocardiography, Heart Catheterization, and Cardiac Computed Tomography
title_sort giant dilatation of the right coronary aortic bulb with compression of the right ventricular outflow tract mimicking a ventricular septal defect diagnostic workup using echocardiography heart catheterization and cardiac computed tomography
url http://dx.doi.org/10.1155/2012/524526
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