Type VI Aplasia Cutis Congenita: Bart’s Syndrome
Bart’s syndrome is characterized by aplasia cutis congenita and epidermolysis bullosa. We present the case of a newborn male who developed blisters on the mucous membranes and the skin following congenital localized absence of skin. Bart’s syndrome (BS) is diagnosed clinically based on the disorder...
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| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Wiley
2015-01-01
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| Series: | Case Reports in Dermatological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2015/549825 |
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| author | Ferit Kulalı Ahmet Yagmur Bas Yusuf Kale Istemi Han Celik Nihal Demirel Sema Apaydın |
| author_facet | Ferit Kulalı Ahmet Yagmur Bas Yusuf Kale Istemi Han Celik Nihal Demirel Sema Apaydın |
| author_sort | Ferit Kulalı |
| collection | DOAJ |
| description | Bart’s syndrome is characterized by aplasia cutis congenita and epidermolysis bullosa. We present the case of a newborn male who developed blisters on the mucous membranes and the skin following congenital localized absence of skin. Bart’s syndrome (BS) is diagnosed clinically based on the disorder’s unique signs and symptoms but histologic evaluation of the skin can help to confirm the final diagnosis. The patient was managed conservatively with topical antibacterial ointment and wet gauze dressing. Periodic follow-up examinations showed complete healing. We emphasized that it is important to use relatively simple methods for optimal healing without the need for complex surgical interventions. |
| format | Article |
| id | doaj-art-a8181dda3f68424eb47a6fb98bdb8826 |
| institution | Kabale University |
| issn | 2090-6463 2090-6471 |
| language | English |
| publishDate | 2015-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dermatological Medicine |
| spelling | doaj-art-a8181dda3f68424eb47a6fb98bdb88262025-08-20T03:39:06ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712015-01-01201510.1155/2015/549825549825Type VI Aplasia Cutis Congenita: Bart’s SyndromeFerit Kulalı0Ahmet Yagmur Bas1Yusuf Kale2Istemi Han Celik3Nihal Demirel4Sema Apaydın5Division of Neonatology, Etlik Zübeyde Hanim Women’s Health Teaching and Research Hospital, Ankara, TurkeyDivision of Neonatology, Etlik Zübeyde Hanim Women’s Health Teaching and Research Hospital, Ankara, TurkeyDivision of Neonatology, Etlik Zübeyde Hanim Women’s Health Teaching and Research Hospital, Ankara, TurkeyDivision of Neonatology, Etlik Zübeyde Hanim Women’s Health Teaching and Research Hospital, Ankara, TurkeyDivision of Neonatology, Etlik Zübeyde Hanim Women’s Health Teaching and Research Hospital, Ankara, TurkeyDepartment of Pathology, Dr. Sami Ulus Maternity and Children Research and Training Hospital, Ankara, TurkeyBart’s syndrome is characterized by aplasia cutis congenita and epidermolysis bullosa. We present the case of a newborn male who developed blisters on the mucous membranes and the skin following congenital localized absence of skin. Bart’s syndrome (BS) is diagnosed clinically based on the disorder’s unique signs and symptoms but histologic evaluation of the skin can help to confirm the final diagnosis. The patient was managed conservatively with topical antibacterial ointment and wet gauze dressing. Periodic follow-up examinations showed complete healing. We emphasized that it is important to use relatively simple methods for optimal healing without the need for complex surgical interventions.http://dx.doi.org/10.1155/2015/549825 |
| spellingShingle | Ferit Kulalı Ahmet Yagmur Bas Yusuf Kale Istemi Han Celik Nihal Demirel Sema Apaydın Type VI Aplasia Cutis Congenita: Bart’s Syndrome Case Reports in Dermatological Medicine |
| title | Type VI Aplasia Cutis Congenita: Bart’s Syndrome |
| title_full | Type VI Aplasia Cutis Congenita: Bart’s Syndrome |
| title_fullStr | Type VI Aplasia Cutis Congenita: Bart’s Syndrome |
| title_full_unstemmed | Type VI Aplasia Cutis Congenita: Bart’s Syndrome |
| title_short | Type VI Aplasia Cutis Congenita: Bart’s Syndrome |
| title_sort | type vi aplasia cutis congenita bart s syndrome |
| url | http://dx.doi.org/10.1155/2015/549825 |
| work_keys_str_mv | AT feritkulalı typeviaplasiacutiscongenitabartssyndrome AT ahmetyagmurbas typeviaplasiacutiscongenitabartssyndrome AT yusufkale typeviaplasiacutiscongenitabartssyndrome AT istemihancelik typeviaplasiacutiscongenitabartssyndrome AT nihaldemirel typeviaplasiacutiscongenitabartssyndrome AT semaapaydın typeviaplasiacutiscongenitabartssyndrome |