Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach

Ellis-van Creveld syndrome (EVC) is a very rare genetic disorder that affects various tissues of ectodermal and mesodermal origin; patients with EVC present with typical oral deficiencies. The affected individuals are quite young at the time of oral evaluation. It is, therefore, important that these...

Full description

Saved in:
Bibliographic Details
Main Authors: Talib Amin Naqash, Ibrahim Alshahrani, Siripan Simasetha
Format: Article
Language:English
Published: Wiley 2018-01-01
Series:Case Reports in Dentistry
Online Access:http://dx.doi.org/10.1155/2018/8631602
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850168661552136192
author Talib Amin Naqash
Ibrahim Alshahrani
Siripan Simasetha
author_facet Talib Amin Naqash
Ibrahim Alshahrani
Siripan Simasetha
author_sort Talib Amin Naqash
collection DOAJ
description Ellis-van Creveld syndrome (EVC) is a very rare genetic disorder that affects various tissues of ectodermal and mesodermal origin; patients with EVC present with typical oral deficiencies. The affected individuals are quite young at the time of oral evaluation. It is, therefore, important that these individuals are diagnosed and receive dental treatment at an early age for their physiologic and psychosocial well-being. Albeit there are numerous articles penned on the EVC, the treatise from an oral perspective is inadequate, covering only oral exhibitions and the preventive treatments. This article reviews the literature and serves as the first disquisition for oral rehabilitation of an EVC patient utilizing surgical, orthodontic, restorative, and prosthodontic management.
format Article
id doaj-art-a75eb3f0918145538867dcade8562262
institution OA Journals
issn 2090-6447
2090-6455
language English
publishDate 2018-01-01
publisher Wiley
record_format Article
series Case Reports in Dentistry
spelling doaj-art-a75eb3f0918145538867dcade85622622025-08-20T02:20:55ZengWileyCase Reports in Dentistry2090-64472090-64552018-01-01201810.1155/2018/86316028631602Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary ApproachTalib Amin Naqash0Ibrahim Alshahrani1Siripan Simasetha2Department of Prosthetic Dentistry, King Khalid University College of Dentistry, Abha, Saudi ArabiaDepartment of Pediatric Dentistry and Orthodontic Sciences, King Khalid University College of Dentistry, Abha, Saudi ArabiaDental Department, Bhumibol Adulyadej Hospital, The Royal Thai Air Force, Bangkok, ThailandEllis-van Creveld syndrome (EVC) is a very rare genetic disorder that affects various tissues of ectodermal and mesodermal origin; patients with EVC present with typical oral deficiencies. The affected individuals are quite young at the time of oral evaluation. It is, therefore, important that these individuals are diagnosed and receive dental treatment at an early age for their physiologic and psychosocial well-being. Albeit there are numerous articles penned on the EVC, the treatise from an oral perspective is inadequate, covering only oral exhibitions and the preventive treatments. This article reviews the literature and serves as the first disquisition for oral rehabilitation of an EVC patient utilizing surgical, orthodontic, restorative, and prosthodontic management.http://dx.doi.org/10.1155/2018/8631602
spellingShingle Talib Amin Naqash
Ibrahim Alshahrani
Siripan Simasetha
Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
Case Reports in Dentistry
title Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_full Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_fullStr Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_full_unstemmed Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_short Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_sort ellis van creveld syndrome a rare clinical report of oral rehabilitation by interdisciplinary approach
url http://dx.doi.org/10.1155/2018/8631602
work_keys_str_mv AT talibaminnaqash ellisvancreveldsyndromearareclinicalreportoforalrehabilitationbyinterdisciplinaryapproach
AT ibrahimalshahrani ellisvancreveldsyndromearareclinicalreportoforalrehabilitationbyinterdisciplinaryapproach
AT siripansimasetha ellisvancreveldsyndromearareclinicalreportoforalrehabilitationbyinterdisciplinaryapproach