Genomic bases of non-syndromic basal cell carcinoma: literature review

Introduction: Non-melanoma skin neoplasms represent the most frequent type in both sexes globally, with basal cell carcinoma being the most prevalent, representing 75 to 80% of cases. In Brazil, the number of new cases expected for the triennium 2020-2022 will be 83,770 in men and 93,160 in women, c...

Full description

Saved in:
Bibliographic Details
Main Author: Daniel Sundfeld Spiga Real
Format: Article
Language:English
Published: Thieme Revinter Publicações Ltda. 2021-09-01
Series:Revista Brasileira de Cirurgia Plástica
Subjects:
Online Access:http://www.rbcp.org.br/export-pdf/2989/en_v36n3a13.pdf
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849408012573212672
author Daniel Sundfeld Spiga Real
author_facet Daniel Sundfeld Spiga Real
author_sort Daniel Sundfeld Spiga Real
collection DOAJ
description Introduction: Non-melanoma skin neoplasms represent the most frequent type in both sexes globally, with basal cell carcinoma being the most prevalent, representing 75 to 80% of cases. In Brazil, the number of new cases expected for the triennium 2020-2022 will be 83,770 in men and 93,160 in women, corresponding to an estimated risk of 80.12 new cases for 100,000 men and 86.65 new cases for 100,000 women. This data demonstrates the great importance of genomic knowledge in the genesis of sporadic basal cell carcinoma. Objective: To describe the main genes and molecular markers involved in the predisposition and pathogenesis of non-syndromic basal cell carcinoma. Methods: Literature review in the main databases NCBI-GTR, ClinVar, ClinGen, MedGen, OMIM and GeneReviews, using as descriptors: "BCC" and "basal cell carcinoma". Inclusion criteria: Portuguese or EnGLIsh language, articles on sporadic BCC. Results: Thirteen articles were selected for analysis. The analysis revealed a robust hedgehog pathway link in the genesis of sporadic basal cell carcinoma, with the main genes involved represented by PATCH1, PATCH2 and smoothened. The variants with the highest clinical significance were SMO-M2, PTCH1 and PTCH2-Δ22. The mutation most found was related to the action of UVB, being represented by the substitution of C>T or CC>TT at the pyrimidine site, both in PTCH and in SMO. Conclusion: Extremely important to professionals working in the diagnosis and treatment of BCC, including plastic surgeons, as this way they can better conduct their cases, with more accurate diagnoses and prevention approaches based on the individual susceptibility of each patient, as well as targeted therapies and individualized with better success rates.
format Article
id doaj-art-a575b47d2fc046338a71b9864080d3b8
institution Kabale University
issn 1983-5175
2177-1235
language English
publishDate 2021-09-01
publisher Thieme Revinter Publicações Ltda.
record_format Article
series Revista Brasileira de Cirurgia Plástica
spelling doaj-art-a575b47d2fc046338a71b9864080d3b82025-08-20T03:35:53ZengThieme Revinter Publicações Ltda.Revista Brasileira de Cirurgia Plástica1983-51752177-12352021-09-01360331532610.5935/2177-1235.2021RBCP0097Genomic bases of non-syndromic basal cell carcinoma: literature reviewDaniel Sundfeld Spiga Real0Federal University of São Carlos, Postgraduate Program - PPGBiotec, São Carlos, SP, BrazilIntroduction: Non-melanoma skin neoplasms represent the most frequent type in both sexes globally, with basal cell carcinoma being the most prevalent, representing 75 to 80% of cases. In Brazil, the number of new cases expected for the triennium 2020-2022 will be 83,770 in men and 93,160 in women, corresponding to an estimated risk of 80.12 new cases for 100,000 men and 86.65 new cases for 100,000 women. This data demonstrates the great importance of genomic knowledge in the genesis of sporadic basal cell carcinoma. Objective: To describe the main genes and molecular markers involved in the predisposition and pathogenesis of non-syndromic basal cell carcinoma. Methods: Literature review in the main databases NCBI-GTR, ClinVar, ClinGen, MedGen, OMIM and GeneReviews, using as descriptors: "BCC" and "basal cell carcinoma". Inclusion criteria: Portuguese or EnGLIsh language, articles on sporadic BCC. Results: Thirteen articles were selected for analysis. The analysis revealed a robust hedgehog pathway link in the genesis of sporadic basal cell carcinoma, with the main genes involved represented by PATCH1, PATCH2 and smoothened. The variants with the highest clinical significance were SMO-M2, PTCH1 and PTCH2-Δ22. The mutation most found was related to the action of UVB, being represented by the substitution of C>T or CC>TT at the pyrimidine site, both in PTCH and in SMO. Conclusion: Extremely important to professionals working in the diagnosis and treatment of BCC, including plastic surgeons, as this way they can better conduct their cases, with more accurate diagnoses and prevention approaches based on the individual susceptibility of each patient, as well as targeted therapies and individualized with better success rates.http://www.rbcp.org.br/export-pdf/2989/en_v36n3a13.pdfhuman genomebasal cell carcinomaneoplasm of basal cellsgenesmutation
spellingShingle Daniel Sundfeld Spiga Real
Genomic bases of non-syndromic basal cell carcinoma: literature review
Revista Brasileira de Cirurgia Plástica
human genome
basal cell carcinoma
neoplasm of basal cells
genes
mutation
title Genomic bases of non-syndromic basal cell carcinoma: literature review
title_full Genomic bases of non-syndromic basal cell carcinoma: literature review
title_fullStr Genomic bases of non-syndromic basal cell carcinoma: literature review
title_full_unstemmed Genomic bases of non-syndromic basal cell carcinoma: literature review
title_short Genomic bases of non-syndromic basal cell carcinoma: literature review
title_sort genomic bases of non syndromic basal cell carcinoma literature review
topic human genome
basal cell carcinoma
neoplasm of basal cells
genes
mutation
url http://www.rbcp.org.br/export-pdf/2989/en_v36n3a13.pdf
work_keys_str_mv AT danielsundfeldspigareal genomicbasesofnonsyndromicbasalcellcarcinomaliteraturereview