A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation

Abstract Background Myeloid sarcoma (MS) is a rare disease, mostly found in conjunction with acute myelogenous leukemia or other diseases, and primary nonleukemic MS of the spleen is particularly rare. Case presentation We report a 57-year-old male who presented with a spleen mass that was found inc...

Full description

Saved in:
Bibliographic Details
Main Authors: Asuka Ono, Yuki Kitano, Katsunori Imai, Takashi Matsumoto, Shinya Endo, Kenji Tokunaga, Hiromitsu Hayashi, Yo-Ichi Yamashita, Masao Matsuoka, Hideo Baba
Format: Article
Language:English
Published: Japan Surgical Society 2021-08-01
Series:Surgical Case Reports
Subjects:
Online Access:https://doi.org/10.1186/s40792-021-01257-w
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849408307476824064
author Asuka Ono
Yuki Kitano
Katsunori Imai
Takashi Matsumoto
Shinya Endo
Kenji Tokunaga
Hiromitsu Hayashi
Yo-Ichi Yamashita
Masao Matsuoka
Hideo Baba
author_facet Asuka Ono
Yuki Kitano
Katsunori Imai
Takashi Matsumoto
Shinya Endo
Kenji Tokunaga
Hiromitsu Hayashi
Yo-Ichi Yamashita
Masao Matsuoka
Hideo Baba
author_sort Asuka Ono
collection DOAJ
description Abstract Background Myeloid sarcoma (MS) is a rare disease, mostly found in conjunction with acute myelogenous leukemia or other diseases, and primary nonleukemic MS of the spleen is particularly rare. Case presentation We report a 57-year-old male who presented with a spleen mass that was found incidentally, and was enlarged. As a result of various examinations, he was diagnosed with primary MS of the spleen with suspected involvement of the transverse colon, left kidney, pancreatic tail, and left diaphragm. He underwent a total splenectomy, partial pancreatectomy, partial colectomy, left nephrectomy, and left diaphragm partial resection. Histological examination revealed splenic primary MS. Bone marrow biopsy and immunophenotypic flow cytometry revealed no evidence of myeloid leukemia. He underwent umbilical cord blood transplantation, and he is currently living without a sign of recurrence at 10 months after surgery. Conclusions We experienced a very rare case of primary spleen MS that was discovered without a hematologic malignancy. Two cases of surgically resected primary splenic MS have been reported, including the present case.
format Article
id doaj-art-a44fa9c738b44f37a338db2d9ac46812
institution Kabale University
issn 2198-7793
language English
publishDate 2021-08-01
publisher Japan Surgical Society
record_format Article
series Surgical Case Reports
spelling doaj-art-a44fa9c738b44f37a338db2d9ac468122025-08-20T03:35:48ZengJapan Surgical SocietySurgical Case Reports2198-77932021-08-01711510.1186/s40792-021-01257-wA case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantationAsuka Ono0Yuki Kitano1Katsunori Imai2Takashi Matsumoto3Shinya Endo4Kenji Tokunaga5Hiromitsu Hayashi6Yo-Ichi Yamashita7Masao Matsuoka8Hideo Baba9Department of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityDepartment of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityDepartment of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityDepartment of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityDepartments of Hematology, Rheumatology, and Infectious Disease, Graduate School of Medical Sciences, Kumamoto UniversityDepartments of Hematology, Rheumatology, and Infectious Disease, Graduate School of Medical Sciences, Kumamoto UniversityDepartment of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityDepartment of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityDepartments of Hematology, Rheumatology, and Infectious Disease, Graduate School of Medical Sciences, Kumamoto UniversityDepartment of Gastroenterological Surgery, Graduate School of Medical Sciences, Kumamoto UniversityAbstract Background Myeloid sarcoma (MS) is a rare disease, mostly found in conjunction with acute myelogenous leukemia or other diseases, and primary nonleukemic MS of the spleen is particularly rare. Case presentation We report a 57-year-old male who presented with a spleen mass that was found incidentally, and was enlarged. As a result of various examinations, he was diagnosed with primary MS of the spleen with suspected involvement of the transverse colon, left kidney, pancreatic tail, and left diaphragm. He underwent a total splenectomy, partial pancreatectomy, partial colectomy, left nephrectomy, and left diaphragm partial resection. Histological examination revealed splenic primary MS. Bone marrow biopsy and immunophenotypic flow cytometry revealed no evidence of myeloid leukemia. He underwent umbilical cord blood transplantation, and he is currently living without a sign of recurrence at 10 months after surgery. Conclusions We experienced a very rare case of primary spleen MS that was discovered without a hematologic malignancy. Two cases of surgically resected primary splenic MS have been reported, including the present case.https://doi.org/10.1186/s40792-021-01257-wMyeloid sarcomaSpleenSurgeryNonleukemic
spellingShingle Asuka Ono
Yuki Kitano
Katsunori Imai
Takashi Matsumoto
Shinya Endo
Kenji Tokunaga
Hiromitsu Hayashi
Yo-Ichi Yamashita
Masao Matsuoka
Hideo Baba
A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation
Surgical Case Reports
Myeloid sarcoma
Spleen
Surgery
Nonleukemic
title A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation
title_full A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation
title_fullStr A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation
title_full_unstemmed A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation
title_short A case of primary nonleukemic myeloid sarcoma of the spleen, successfully treated by surgery and hematopoietic stem cell transplantation
title_sort case of primary nonleukemic myeloid sarcoma of the spleen successfully treated by surgery and hematopoietic stem cell transplantation
topic Myeloid sarcoma
Spleen
Surgery
Nonleukemic
url https://doi.org/10.1186/s40792-021-01257-w
work_keys_str_mv AT asukaono acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT yukikitano acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT katsunoriimai acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT takashimatsumoto acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT shinyaendo acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT kenjitokunaga acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT hiromitsuhayashi acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT yoichiyamashita acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT masaomatsuoka acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT hideobaba acaseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT asukaono caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT yukikitano caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT katsunoriimai caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT takashimatsumoto caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT shinyaendo caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT kenjitokunaga caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT hiromitsuhayashi caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT yoichiyamashita caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT masaomatsuoka caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation
AT hideobaba caseofprimarynonleukemicmyeloidsarcomaofthespleensuccessfullytreatedbysurgeryandhematopoieticstemcelltransplantation