Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst
Rosai–Dorfman disease (RDD) is an uncommon histiocytic disorder presenting with painless massive lymphadenopathy. Extranodal RDD is seen in up to 30% of cases and commonly involves the skin and bone. Central nervous system (CNS) involvement by RDD is very rare, occurring in <5% of cases. In the C...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2024-07-01
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| Series: | CHRISMED Journal of Health and Research |
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| Online Access: | https://journals.lww.com/10.4103/cjhr.cjhr_72_24 |
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| author | Sunayana Misra Shashi Dhawan Seema Rao |
| author_facet | Sunayana Misra Shashi Dhawan Seema Rao |
| author_sort | Sunayana Misra |
| collection | DOAJ |
| description | Rosai–Dorfman disease (RDD) is an uncommon histiocytic disorder presenting with painless massive lymphadenopathy. Extranodal RDD is seen in up to 30% of cases and commonly involves the skin and bone. Central nervous system (CNS) involvement by RDD is very rare, occurring in <5% of cases. In the CNS, RDD is usually seen as dural-based lesion mimicking meningiomas or as intraparenchymal solid lesions. The presentation of RDD in a posterior fossa arachnoid cyst has not been previously reported. To the best of our knowledge, we report the first case of isolated extranodal RDD in the CNS presenting in the wall of a retrocerebellar arachnoid cyst. |
| format | Article |
| id | doaj-art-a43c70cd90c34c2aaa59861ff85697f2 |
| institution | OA Journals |
| issn | 2348-3334 2348-506X |
| language | English |
| publishDate | 2024-07-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | CHRISMED Journal of Health and Research |
| spelling | doaj-art-a43c70cd90c34c2aaa59861ff85697f22025-08-20T02:16:02ZengWolters Kluwer Medknow PublicationsCHRISMED Journal of Health and Research2348-33342348-506X2024-07-0111315916110.4103/cjhr.cjhr_72_24Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid CystSunayana MisraShashi DhawanSeema RaoRosai–Dorfman disease (RDD) is an uncommon histiocytic disorder presenting with painless massive lymphadenopathy. Extranodal RDD is seen in up to 30% of cases and commonly involves the skin and bone. Central nervous system (CNS) involvement by RDD is very rare, occurring in <5% of cases. In the CNS, RDD is usually seen as dural-based lesion mimicking meningiomas or as intraparenchymal solid lesions. The presentation of RDD in a posterior fossa arachnoid cyst has not been previously reported. To the best of our knowledge, we report the first case of isolated extranodal RDD in the CNS presenting in the wall of a retrocerebellar arachnoid cyst.https://journals.lww.com/10.4103/cjhr.cjhr_72_24arachnoid cystcentral nervous systemhistiocytosisrosai–dorfman disease |
| spellingShingle | Sunayana Misra Shashi Dhawan Seema Rao Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst CHRISMED Journal of Health and Research arachnoid cyst central nervous system histiocytosis rosai–dorfman disease |
| title | Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst |
| title_full | Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst |
| title_fullStr | Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst |
| title_full_unstemmed | Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst |
| title_short | Rosai–Dorfman Disease of the Central Nervous System with a Rare Presentation as an Arachnoid Cyst |
| title_sort | rosai dorfman disease of the central nervous system with a rare presentation as an arachnoid cyst |
| topic | arachnoid cyst central nervous system histiocytosis rosai–dorfman disease |
| url | https://journals.lww.com/10.4103/cjhr.cjhr_72_24 |
| work_keys_str_mv | AT sunayanamisra rosaidorfmandiseaseofthecentralnervoussystemwithararepresentationasanarachnoidcyst AT shashidhawan rosaidorfmandiseaseofthecentralnervoussystemwithararepresentationasanarachnoidcyst AT seemarao rosaidorfmandiseaseofthecentralnervoussystemwithararepresentationasanarachnoidcyst |