Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients
This study was based on a prospective and a retrospective analysis of 35 patients who met Bohan and Peter criteria for juvenile dermatomyositis diagnosis.The mean follow-up time was three years ten months. Calcinosis was present in five (14.28 %) patients, cutaneous ulcers in four (11.42%), and syst...
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Thieme Revinter Publicações
2002-12-01
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| Series: | Arquivos de Neuro-Psiquiatria |
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| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2002000600001&tlng=en |
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| author | Adriana Maluf Elias Sallum Maria Helena Bittencurt Kiss Silvana Sachetti Maria Bernadate Dutra Resende Kelly Cristina Moutinho Mary de Souza Carvalho Clovis Arthur Almeida Silva Suely Kazue Nagahashi Marie |
| author_facet | Adriana Maluf Elias Sallum Maria Helena Bittencurt Kiss Silvana Sachetti Maria Bernadate Dutra Resende Kelly Cristina Moutinho Mary de Souza Carvalho Clovis Arthur Almeida Silva Suely Kazue Nagahashi Marie |
| author_sort | Adriana Maluf Elias Sallum |
| collection | DOAJ |
| description | This study was based on a prospective and a retrospective analysis of 35 patients who met Bohan and Peter criteria for juvenile dermatomyositis diagnosis.The mean follow-up time was three years ten months. Calcinosis was present in five (14.28 %) patients, cutaneous ulcers in four (11.42%), and systemic involvement in nine (27.71%) patients. All patients presented alterations in the serum levels of muscle enzymes, and all of them were submitted to muscle biopsy as a diagnostic procedure. Nine (25.71%) patients received corticotherapy prior to and 26 (74.28%) after the muscle biopsy. Chloroquine, methotrexate, cyclosporine, cyclophosphamide and intravenous immunoglobulin were used in patients with poor response to corticotherapy. Continuation of cutaneous manifestations was observed in 4 (11.43%) patients, laboratorial activity in 1 (2.85%), cutaneous and laboratorial activities in 3 (8.57%). Ten (28.57%) patients were out of activity, and 17 (48.57%) in remission at study end-point, on March 2002. Two (5.71%) patients died. |
| format | Article |
| id | doaj-art-a2d388f1923b4dbcbe9998e4c11b3b0c |
| institution | DOAJ |
| issn | 1678-4227 |
| language | English |
| publishDate | 2002-12-01 |
| publisher | Thieme Revinter Publicações |
| record_format | Article |
| series | Arquivos de Neuro-Psiquiatria |
| spelling | doaj-art-a2d388f1923b4dbcbe9998e4c11b3b0c2025-08-20T03:19:57ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-42272002-12-0160488989910.1590/S0004-282X2002000600001Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patientsAdriana Maluf Elias Sallum0Maria Helena Bittencurt Kiss1Silvana Sachetti2Maria Bernadate Dutra Resende3Kelly Cristina Moutinho4Mary de Souza Carvalho5Clovis Arthur Almeida Silva6Suely Kazue Nagahashi Marie7Universidade de São PauloUniversidade de São PauloSão Paulo Medical SchoolUniversidade de São PauloUniversidade de São PauloUniversidade de São PauloUniversidade de São PauloUniversidade de São PauloThis study was based on a prospective and a retrospective analysis of 35 patients who met Bohan and Peter criteria for juvenile dermatomyositis diagnosis.The mean follow-up time was three years ten months. Calcinosis was present in five (14.28 %) patients, cutaneous ulcers in four (11.42%), and systemic involvement in nine (27.71%) patients. All patients presented alterations in the serum levels of muscle enzymes, and all of them were submitted to muscle biopsy as a diagnostic procedure. Nine (25.71%) patients received corticotherapy prior to and 26 (74.28%) after the muscle biopsy. Chloroquine, methotrexate, cyclosporine, cyclophosphamide and intravenous immunoglobulin were used in patients with poor response to corticotherapy. Continuation of cutaneous manifestations was observed in 4 (11.43%) patients, laboratorial activity in 1 (2.85%), cutaneous and laboratorial activities in 3 (8.57%). Ten (28.57%) patients were out of activity, and 17 (48.57%) in remission at study end-point, on March 2002. Two (5.71%) patients died.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2002000600001&tlng=enjuvenile dermatomyositisclinical findingsmuscle biopsytreatmentevolutionoutcome |
| spellingShingle | Adriana Maluf Elias Sallum Maria Helena Bittencurt Kiss Silvana Sachetti Maria Bernadate Dutra Resende Kelly Cristina Moutinho Mary de Souza Carvalho Clovis Arthur Almeida Silva Suely Kazue Nagahashi Marie Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients Arquivos de Neuro-Psiquiatria juvenile dermatomyositis clinical findings muscle biopsy treatment evolution outcome |
| title | Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients |
| title_full | Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients |
| title_fullStr | Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients |
| title_full_unstemmed | Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients |
| title_short | Juvenile dermatomyositis: clinical, laboratorial, histological, therapeutical and evolutive parameters of 35 patients |
| title_sort | juvenile dermatomyositis clinical laboratorial histological therapeutical and evolutive parameters of 35 patients |
| topic | juvenile dermatomyositis clinical findings muscle biopsy treatment evolution outcome |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2002000600001&tlng=en |
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