Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules
Trichoepitheliomas (TE) are benign skin tumours of the pilosebaceous apocrine unit with follicular differentiation. Multiple familial trichoepithelioma (MFT) is a considerably rare condition inherited in an autosomal dominant pattern. We present a case of a 15-year-old male who presented with multip...
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| Format: | Article |
| Language: | English |
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Wiley
2020-01-01
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| Series: | Case Reports in Dentistry |
| Online Access: | http://dx.doi.org/10.1155/2020/5648647 |
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| author | D. W. V. N. Dissanayaka D. K. B. Dassanayaka P. R. Jayasooriya |
| author_facet | D. W. V. N. Dissanayaka D. K. B. Dassanayaka P. R. Jayasooriya |
| author_sort | D. W. V. N. Dissanayaka |
| collection | DOAJ |
| description | Trichoepitheliomas (TE) are benign skin tumours of the pilosebaceous apocrine unit with follicular differentiation. Multiple familial trichoepithelioma (MFT) is a considerably rare condition inherited in an autosomal dominant pattern. We present a case of a 15-year-old male who presented with multiple papulo-nodular lesions in the central face and a family history of a similar type of lesions from his mother. Significance of consideration of various clinical differential diagnoses with serious pathological outcomes, strategies followed in the diagnosis including histopathological evaluation aided by immunohistochemical investigations, and subsequent challenges that may be faced in the management of MFT in light of the presentation with multiple facial papules are documented in this case report. |
| format | Article |
| id | doaj-art-a2a799d6c95a4378b486fdddad2dc1c0 |
| institution | Kabale University |
| issn | 2090-6447 2090-6455 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dentistry |
| spelling | doaj-art-a2a799d6c95a4378b486fdddad2dc1c02025-02-03T01:03:50ZengWileyCase Reports in Dentistry2090-64472090-64552020-01-01202010.1155/2020/56486475648647Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial PapulesD. W. V. N. Dissanayaka0D. K. B. Dassanayaka1P. R. Jayasooriya2Department of Oral Pathology, Faculty of Dental Sciences, University of Peradeniya, Sri LankaOral and Maxillofacial Surgery Unit, Provincial General Hospital Badulla, Sri LankaDepartment of Oral Pathology, Faculty of Dental Sciences, University of Peradeniya, Sri LankaTrichoepitheliomas (TE) are benign skin tumours of the pilosebaceous apocrine unit with follicular differentiation. Multiple familial trichoepithelioma (MFT) is a considerably rare condition inherited in an autosomal dominant pattern. We present a case of a 15-year-old male who presented with multiple papulo-nodular lesions in the central face and a family history of a similar type of lesions from his mother. Significance of consideration of various clinical differential diagnoses with serious pathological outcomes, strategies followed in the diagnosis including histopathological evaluation aided by immunohistochemical investigations, and subsequent challenges that may be faced in the management of MFT in light of the presentation with multiple facial papules are documented in this case report.http://dx.doi.org/10.1155/2020/5648647 |
| spellingShingle | D. W. V. N. Dissanayaka D. K. B. Dassanayaka P. R. Jayasooriya Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules Case Reports in Dentistry |
| title | Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules |
| title_full | Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules |
| title_fullStr | Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules |
| title_full_unstemmed | Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules |
| title_short | Clinical, Histopathological, and Management Challenges of Multiple Familial Trichoepithelioma: A Case Report of a Patient Presenting with Multiple Facial Papules |
| title_sort | clinical histopathological and management challenges of multiple familial trichoepithelioma a case report of a patient presenting with multiple facial papules |
| url | http://dx.doi.org/10.1155/2020/5648647 |
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