Orbital lymphoma associated with Graves’ disease: A case report

Introduction. The presence of bilateral exophthalmos and palpebral, periorbital edema associated with hyperthyroidism is most often considered as an initial sign of Graves’ ophthalmopathy. However, in up to 20% of cases, Graves’ ophthalmopathy might precede the occurrence of hyperthyroidism...

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Main Authors: Hajduković Zoran, Kuzmić-Janković Snežana, Kljaković-Avramović Tamara, Sekulović Leposava, Tukić Ljiljana
Format: Article
Language:English
Published: Ministry of Defence of the Republic of Serbia, University of Defence, Belgrade 2014-01-01
Series:Vojnosanitetski Pregled
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Online Access:http://www.doiserbia.nb.rs/img/doi/0042-8450/2014/0042-84501405510H.pdf
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author Hajduković Zoran
Kuzmić-Janković Snežana
Kljaković-Avramović Tamara
Sekulović Leposava
Tukić Ljiljana
author_facet Hajduković Zoran
Kuzmić-Janković Snežana
Kljaković-Avramović Tamara
Sekulović Leposava
Tukić Ljiljana
author_sort Hajduković Zoran
collection DOAJ
description Introduction. The presence of bilateral exophthalmos and palpebral, periorbital edema associated with hyperthyroidism is most often considered as an initial sign of Graves’ ophthalmopathy. However, in up to 20% of cases, Graves’ ophthalmopathy might precede the occurrence of hyperthyroidism, which is very important to be considered in the differential diagnosis, especially if it is stated as unilateral. Among other less common causes of non-thyroid-related orbitopathy, orbital lymphoma represents rare conditions. We presented of a patient with Graves’ disease, initially manifested as bilateral orbitopathy and progressive unilateral exophthalmos caused by the marginal zone B-cell non-Hodgkin lymphoma of the orbit. Case report. A 64-yearold man with the 3-year history of bilateral Graves’ orbitopathy and hyperthyroidism underwent the left orbital decompression surgery due to the predominantly left, unilateral worsening of exophthalmos resistant to the previously applied glucocorticoid therapy. A year after the surgical treatment, a substantial exophthalmos of the left eye was again observed, signifying that other non-thyroid pathology could be involved. Orbital ultrasound was suggestive of primary orbital lymphoma, what was confirmed by orbital CT scan and the biopsy of the tumor tissue. Detailed examinations indicated that the marginal zone B-cell non-Hodgkin lymphoma extended to IV - B-b CS, IPI 3 (bone marrow infiltration: m+ orbit+). Upon the completion of the polychemiotherapy and the radiation treatment, a complete remission of the disease was achieved. Conclusion. Even when elements clearly indicate the presence of thyroid-related ophthalmopathy, disease deteriorating should raise a suspicion and always lead to imaging procedures to exclude malignancy.
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spelling doaj-art-a29337ef0c9041a5aab2e94abab5f0ff2025-08-20T02:00:43ZengMinistry of Defence of the Republic of Serbia, University of Defence, BelgradeVojnosanitetski Pregled0042-84502014-01-0171551051410.2298/VSP1405510H0042-84501405510HOrbital lymphoma associated with Graves’ disease: A case reportHajduković Zoran0Kuzmić-Janković Snežana1Kljaković-Avramović Tamara2Sekulović Leposava3Tukić Ljiljana4Military Medical Academy, Clinic for Endocrinology, Belgrade + University of Defence, Faculty of Medicine of the Military Medical Academy, BelgradeMilitary Medical Academy, Clinic for Endocrinology, BelgradeMilitary Medical Academy, Clinic for Ophthalmology, BelgradeUniversity of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade + Military Medical Academy, Institute of Radiology, BelgradeUniversity of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade + Military Medical Academy, Clinic for Haematology, BelgradeIntroduction. The presence of bilateral exophthalmos and palpebral, periorbital edema associated with hyperthyroidism is most often considered as an initial sign of Graves’ ophthalmopathy. However, in up to 20% of cases, Graves’ ophthalmopathy might precede the occurrence of hyperthyroidism, which is very important to be considered in the differential diagnosis, especially if it is stated as unilateral. Among other less common causes of non-thyroid-related orbitopathy, orbital lymphoma represents rare conditions. We presented of a patient with Graves’ disease, initially manifested as bilateral orbitopathy and progressive unilateral exophthalmos caused by the marginal zone B-cell non-Hodgkin lymphoma of the orbit. Case report. A 64-yearold man with the 3-year history of bilateral Graves’ orbitopathy and hyperthyroidism underwent the left orbital decompression surgery due to the predominantly left, unilateral worsening of exophthalmos resistant to the previously applied glucocorticoid therapy. A year after the surgical treatment, a substantial exophthalmos of the left eye was again observed, signifying that other non-thyroid pathology could be involved. Orbital ultrasound was suggestive of primary orbital lymphoma, what was confirmed by orbital CT scan and the biopsy of the tumor tissue. Detailed examinations indicated that the marginal zone B-cell non-Hodgkin lymphoma extended to IV - B-b CS, IPI 3 (bone marrow infiltration: m+ orbit+). Upon the completion of the polychemiotherapy and the radiation treatment, a complete remission of the disease was achieved. Conclusion. Even when elements clearly indicate the presence of thyroid-related ophthalmopathy, disease deteriorating should raise a suspicion and always lead to imaging procedures to exclude malignancy.http://www.doiserbia.nb.rs/img/doi/0042-8450/2014/0042-84501405510H.pdfexophthalmosdiagnosis, differentialgraves diseasehistological techniques
spellingShingle Hajduković Zoran
Kuzmić-Janković Snežana
Kljaković-Avramović Tamara
Sekulović Leposava
Tukić Ljiljana
Orbital lymphoma associated with Graves’ disease: A case report
Vojnosanitetski Pregled
exophthalmos
diagnosis, differential
graves disease
histological techniques
title Orbital lymphoma associated with Graves’ disease: A case report
title_full Orbital lymphoma associated with Graves’ disease: A case report
title_fullStr Orbital lymphoma associated with Graves’ disease: A case report
title_full_unstemmed Orbital lymphoma associated with Graves’ disease: A case report
title_short Orbital lymphoma associated with Graves’ disease: A case report
title_sort orbital lymphoma associated with graves disease a case report
topic exophthalmos
diagnosis, differential
graves disease
histological techniques
url http://www.doiserbia.nb.rs/img/doi/0042-8450/2014/0042-84501405510H.pdf
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AT kljakovicavramovictamara orbitallymphomaassociatedwithgravesdiseaseacasereport
AT sekulovicleposava orbitallymphomaassociatedwithgravesdiseaseacasereport
AT tukicljiljana orbitallymphomaassociatedwithgravesdiseaseacasereport