Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report

The frequency of myopathy in hypothyroidism ranges from 30 to 80%. The major symptoms related are weakness, muscular cramps and myalgia. The pseudohyperthrophic form is called Hoffman's syndrome. The electrophysiological study reveals myopathy, neuropathy or mixed pattern. Laboratorial investig...

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Main Authors: Luiz Felipe Rocha Vasconcellos, Maria Claudia Peixoto, Tatiana Nunes de Oliveira, Glória Penque, Ana Claudia Celestino Leite
Format: Article
Language:English
Published: Thieme Revinter Publicações 2003-09-01
Series:Arquivos de Neuro-Psiquiatria
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Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000500027&tlng=en
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author Luiz Felipe Rocha Vasconcellos
Maria Claudia Peixoto
Tatiana Nunes de Oliveira
Glória Penque
Ana Claudia Celestino Leite
author_facet Luiz Felipe Rocha Vasconcellos
Maria Claudia Peixoto
Tatiana Nunes de Oliveira
Glória Penque
Ana Claudia Celestino Leite
author_sort Luiz Felipe Rocha Vasconcellos
collection DOAJ
description The frequency of myopathy in hypothyroidism ranges from 30 to 80%. The major symptoms related are weakness, muscular cramps and myalgia. The pseudohyperthrophic form is called Hoffman's syndrome. The electrophysiological study reveals myopathy, neuropathy or mixed pattern. Laboratorial investigation generally shows increased levels of muscle enzymes and low serum thyroid hormones, with thyrotrophic-stimulating hormone (TSH) elevated. The treatment consists in hormone replacement and the prognosis is good in most of the cases. We report an adult male who developed muscular cramps, myalgia, weakness, pseudohyperthrophy, associated with facial edema and alteration of his voice. The muscle enzymes were increased and T4 was undetectable with a raised level of TSH. The myopathy was the initial manifestation of hypothyroidism in this case.
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publishDate 2003-09-01
publisher Thieme Revinter Publicações
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series Arquivos de Neuro-Psiquiatria
spelling doaj-art-a1e13ce0b51e4ea6be58123bf1c18cc12025-08-20T01:59:48ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-42272003-09-01613B85185410.1590/S0004-282X2003000500027Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case reportLuiz Felipe Rocha Vasconcellos0Maria Claudia Peixoto1Tatiana Nunes de Oliveira2Glória Penque3Ana Claudia Celestino Leite4University Hospital Clementino Fraga FilhoUniversity Hospital Clementino Fraga FilhoUniversity Hospital Clementino Fraga FilhoINDCUniversity Hospital Clementino Fraga FilhoThe frequency of myopathy in hypothyroidism ranges from 30 to 80%. The major symptoms related are weakness, muscular cramps and myalgia. The pseudohyperthrophic form is called Hoffman's syndrome. The electrophysiological study reveals myopathy, neuropathy or mixed pattern. Laboratorial investigation generally shows increased levels of muscle enzymes and low serum thyroid hormones, with thyrotrophic-stimulating hormone (TSH) elevated. The treatment consists in hormone replacement and the prognosis is good in most of the cases. We report an adult male who developed muscular cramps, myalgia, weakness, pseudohyperthrophy, associated with facial edema and alteration of his voice. The muscle enzymes were increased and T4 was undetectable with a raised level of TSH. The myopathy was the initial manifestation of hypothyroidism in this case.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000500027&tlng=enmyopathyhypothyroidismpseudohypertrophy
spellingShingle Luiz Felipe Rocha Vasconcellos
Maria Claudia Peixoto
Tatiana Nunes de Oliveira
Glória Penque
Ana Claudia Celestino Leite
Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report
Arquivos de Neuro-Psiquiatria
myopathy
hypothyroidism
pseudohypertrophy
title Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report
title_full Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report
title_fullStr Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report
title_full_unstemmed Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report
title_short Hoffman's syndrome: pseudohypertrophic myopathy as initial manifestation of hypothyroidism. Case report
title_sort hoffman s syndrome pseudohypertrophic myopathy as initial manifestation of hypothyroidism case report
topic myopathy
hypothyroidism
pseudohypertrophy
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000500027&tlng=en
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