A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case

This study describes an autopsy case of pancreatic/peripancreatic myeloid sarcoma in a 70-year-old man, initially presenting with obstructive jaundice. Pathologically, diffuse infiltration of round cells containing atypical nuclei with marked cleavage was observed mainly in the pancreas head, peripa...

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Main Authors: Yuki Fukumura, Gentaro Taniguchi, Ai Koyanagi, Yuki Horiuchi, Tomonori Ochiai, Yoko Tabe, Katsuhiro Sano, Yifare Maimaitiaili, Naomi Otsuji, Karin Ashizawa, Takashi Yao
Format: Article
Language:English
Published: Wiley 2021-01-01
Series:Case Reports in Pathology
Online Access:http://dx.doi.org/10.1155/2021/7439148
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author Yuki Fukumura
Gentaro Taniguchi
Ai Koyanagi
Yuki Horiuchi
Tomonori Ochiai
Yoko Tabe
Katsuhiro Sano
Yifare Maimaitiaili
Naomi Otsuji
Karin Ashizawa
Takashi Yao
author_facet Yuki Fukumura
Gentaro Taniguchi
Ai Koyanagi
Yuki Horiuchi
Tomonori Ochiai
Yoko Tabe
Katsuhiro Sano
Yifare Maimaitiaili
Naomi Otsuji
Karin Ashizawa
Takashi Yao
author_sort Yuki Fukumura
collection DOAJ
description This study describes an autopsy case of pancreatic/peripancreatic myeloid sarcoma in a 70-year-old man, initially presenting with obstructive jaundice. Pathologically, diffuse infiltration of round cells containing atypical nuclei with marked cleavage was observed mainly in the pancreas head, peripancreatic lymph nodes, spleen, bilateral lung, and bone marrow. Immunohistochemically, the tumor cells were negative for CD20, CD79a, CD3, CD5, c-kit, CD34, and TdT and positive for myeloperoxidase, CD33, CD68, and CD163. Flow cytometry of the peripheral blood showed underexpression of CD11c and aberrant expression of CD56 in the monocyte subset. The peripheral blood smear showed an increase in monocytes and atypia in neutrophils and monocytes, as well as enlarged platelets and polychromatic erythroblasts. Hence, it was suggested that the myeloid sarcoma was derived from the acute transformation of chronic myelomonocytic leukemia. Myeloid sarcoma is an extramedullary-mass-forming hematologic malignancy that is difficult to diagnose, especially when the initial presentation is a pancreatic mass. However, early diagnosis is important for appropriate therapy. Although bone marrow examination could not be performed because of the patients’ severe condition, the pathological specimen obtained with autopsy helped subtype the patient’s leukemia. The immunohistochemical features of this case merit attention.
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spelling doaj-art-a17bfc28baaa47daa3ba3a1c83260d982025-08-20T03:38:38ZengWileyCase Reports in Pathology2090-679X2021-01-01202110.1155/2021/7439148A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic CaseYuki Fukumura0Gentaro Taniguchi1Ai Koyanagi2Yuki Horiuchi3Tomonori Ochiai4Yoko Tabe5Katsuhiro Sano6Yifare Maimaitiaili7Naomi Otsuji8Karin Ashizawa9Takashi Yao10Department of Human PathologyDepartment of GastroenterologyDepartment of Pathology and OncologyDepartment of Clinical Laboratory MedicineDepartment of HematologyDepartment of Clinical Laboratory MedicineDepartment of RadiologyDepartment of Human PathologyDepartment of Human PathologyDepartment of Human PathologyDepartment of Human PathologyThis study describes an autopsy case of pancreatic/peripancreatic myeloid sarcoma in a 70-year-old man, initially presenting with obstructive jaundice. Pathologically, diffuse infiltration of round cells containing atypical nuclei with marked cleavage was observed mainly in the pancreas head, peripancreatic lymph nodes, spleen, bilateral lung, and bone marrow. Immunohistochemically, the tumor cells were negative for CD20, CD79a, CD3, CD5, c-kit, CD34, and TdT and positive for myeloperoxidase, CD33, CD68, and CD163. Flow cytometry of the peripheral blood showed underexpression of CD11c and aberrant expression of CD56 in the monocyte subset. The peripheral blood smear showed an increase in monocytes and atypia in neutrophils and monocytes, as well as enlarged platelets and polychromatic erythroblasts. Hence, it was suggested that the myeloid sarcoma was derived from the acute transformation of chronic myelomonocytic leukemia. Myeloid sarcoma is an extramedullary-mass-forming hematologic malignancy that is difficult to diagnose, especially when the initial presentation is a pancreatic mass. However, early diagnosis is important for appropriate therapy. Although bone marrow examination could not be performed because of the patients’ severe condition, the pathological specimen obtained with autopsy helped subtype the patient’s leukemia. The immunohistochemical features of this case merit attention.http://dx.doi.org/10.1155/2021/7439148
spellingShingle Yuki Fukumura
Gentaro Taniguchi
Ai Koyanagi
Yuki Horiuchi
Tomonori Ochiai
Yoko Tabe
Katsuhiro Sano
Yifare Maimaitiaili
Naomi Otsuji
Karin Ashizawa
Takashi Yao
A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case
Case Reports in Pathology
title A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case
title_full A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case
title_fullStr A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case
title_full_unstemmed A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case
title_short A Case of Untreated Myeloid Sarcoma of the Pancreas Head Region: Diagnostic Process of AML Subtyping in an Autoptic Case
title_sort case of untreated myeloid sarcoma of the pancreas head region diagnostic process of aml subtyping in an autoptic case
url http://dx.doi.org/10.1155/2021/7439148
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