IgG4-related disease revealed by acute pancreatitis: A case report and literature review
IgG4-related disease is a systemic autoimmune disorder characterized by multiorgan involvement, often presenting with pancreatic, renal, biliary, and salivary gland abnormalities. Diagnosis relies on clinical, serological, imaging, and occasionally histological findings. This report describes a 65-y...
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| Format: | Article |
| Language: | English |
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Elsevier
2025-05-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043325000792 |
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| author | Salma El Aouadi Kaoutar Imrani Amine Naggar Soukaina Bahha Nabil Moatassim Billah Ittimade Nassar |
| author_facet | Salma El Aouadi Kaoutar Imrani Amine Naggar Soukaina Bahha Nabil Moatassim Billah Ittimade Nassar |
| author_sort | Salma El Aouadi |
| collection | DOAJ |
| description | IgG4-related disease is a systemic autoimmune disorder characterized by multiorgan involvement, often presenting with pancreatic, renal, biliary, and salivary gland abnormalities. Diagnosis relies on clinical, serological, imaging, and occasionally histological findings. This report describes a 65-year-old male presenting with acute pancreatitis, bilateral renal lesions, and biliary strictures. Elevated serum IgG4 levels (3.76 g/L) confirmed the diagnosis using the 2019 ACR/EULAR and 2020 Comprehensive Diagnostic Criteria despite the lack of histological confirmation. Corticosteroid therapy led to rapid clinical and biochemical improvement, underscoring the importance of integrating multiple diagnostic modalities in managing IgG4-related disease and demonstrating the effectiveness of early intervention. |
| format | Article |
| id | doaj-art-a06c7efc258a45c4b5c3e082e4bc0c60 |
| institution | OA Journals |
| issn | 1930-0433 |
| language | English |
| publishDate | 2025-05-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj-art-a06c7efc258a45c4b5c3e082e4bc0c602025-08-20T01:57:40ZengElsevierRadiology Case Reports1930-04332025-05-012052315232210.1016/j.radcr.2025.01.078IgG4-related disease revealed by acute pancreatitis: A case report and literature reviewSalma El Aouadi0Kaoutar Imrani1Amine Naggar2Soukaina Bahha3Nabil Moatassim Billah4Ittimade Nassar5Corresponding author.; Central Radiology Department, Ibn Sina University Hospital, Rabat, MoroccoCentral Radiology Department, Ibn Sina University Hospital, Rabat, MoroccoCentral Radiology Department, Ibn Sina University Hospital, Rabat, MoroccoCentral Radiology Department, Ibn Sina University Hospital, Rabat, MoroccoCentral Radiology Department, Ibn Sina University Hospital, Rabat, MoroccoCentral Radiology Department, Ibn Sina University Hospital, Rabat, MoroccoIgG4-related disease is a systemic autoimmune disorder characterized by multiorgan involvement, often presenting with pancreatic, renal, biliary, and salivary gland abnormalities. Diagnosis relies on clinical, serological, imaging, and occasionally histological findings. This report describes a 65-year-old male presenting with acute pancreatitis, bilateral renal lesions, and biliary strictures. Elevated serum IgG4 levels (3.76 g/L) confirmed the diagnosis using the 2019 ACR/EULAR and 2020 Comprehensive Diagnostic Criteria despite the lack of histological confirmation. Corticosteroid therapy led to rapid clinical and biochemical improvement, underscoring the importance of integrating multiple diagnostic modalities in managing IgG4-related disease and demonstrating the effectiveness of early intervention.http://www.sciencedirect.com/science/article/pii/S1930043325000792IgG4 related diseaseIgG4-positive plasma cellsImaging featuresAutoimmune pancreatitisExtra-pancreatic manifestations |
| spellingShingle | Salma El Aouadi Kaoutar Imrani Amine Naggar Soukaina Bahha Nabil Moatassim Billah Ittimade Nassar IgG4-related disease revealed by acute pancreatitis: A case report and literature review Radiology Case Reports IgG4 related disease IgG4-positive plasma cells Imaging features Autoimmune pancreatitis Extra-pancreatic manifestations |
| title | IgG4-related disease revealed by acute pancreatitis: A case report and literature review |
| title_full | IgG4-related disease revealed by acute pancreatitis: A case report and literature review |
| title_fullStr | IgG4-related disease revealed by acute pancreatitis: A case report and literature review |
| title_full_unstemmed | IgG4-related disease revealed by acute pancreatitis: A case report and literature review |
| title_short | IgG4-related disease revealed by acute pancreatitis: A case report and literature review |
| title_sort | igg4 related disease revealed by acute pancreatitis a case report and literature review |
| topic | IgG4 related disease IgG4-positive plasma cells Imaging features Autoimmune pancreatitis Extra-pancreatic manifestations |
| url | http://www.sciencedirect.com/science/article/pii/S1930043325000792 |
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