Marfan Syndrome: A Case Report

Marfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially th...

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Main Authors: Rajendran Ganesh, Rajendran Vijayakumar, Haridoss Selvakumar
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Dentistry
Online Access:http://dx.doi.org/10.1155/2012/595343
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author Rajendran Ganesh
Rajendran Vijayakumar
Haridoss Selvakumar
author_facet Rajendran Ganesh
Rajendran Vijayakumar
Haridoss Selvakumar
author_sort Rajendran Ganesh
collection DOAJ
description Marfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially the skeleton, lungs, eyes, heart, and the large blood vessel that distributes blood from the heart to the rest of the body. A case report of Marfan syndrome has been reported with oral features. The dental problems of the child were treated under general anesthesia and a one-month review showed intact stainless steel crowns' restorations and no signs of secondary caries.
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publishDate 2012-01-01
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series Case Reports in Dentistry
spelling doaj-art-9f9d4051e23d4f0d9dbe6fd6bd61bfc72025-08-20T03:38:30ZengWileyCase Reports in Dentistry2090-64472090-64552012-01-01201210.1155/2012/595343595343Marfan Syndrome: A Case ReportRajendran Ganesh0Rajendran Vijayakumar1Haridoss Selvakumar2Department of Pedodontics, SRM Dental College, SRM University, Chennai 600078, IndiaDepartment of Pedodontics, SRM Dental College, SRM University, Chennai 600078, IndiaDepartment of Pedodontics, SRM Dental College, SRM University, Chennai 600078, IndiaMarfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially the skeleton, lungs, eyes, heart, and the large blood vessel that distributes blood from the heart to the rest of the body. A case report of Marfan syndrome has been reported with oral features. The dental problems of the child were treated under general anesthesia and a one-month review showed intact stainless steel crowns' restorations and no signs of secondary caries.http://dx.doi.org/10.1155/2012/595343
spellingShingle Rajendran Ganesh
Rajendran Vijayakumar
Haridoss Selvakumar
Marfan Syndrome: A Case Report
Case Reports in Dentistry
title Marfan Syndrome: A Case Report
title_full Marfan Syndrome: A Case Report
title_fullStr Marfan Syndrome: A Case Report
title_full_unstemmed Marfan Syndrome: A Case Report
title_short Marfan Syndrome: A Case Report
title_sort marfan syndrome a case report
url http://dx.doi.org/10.1155/2012/595343
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AT rajendranvijayakumar marfansyndromeacasereport
AT haridossselvakumar marfansyndromeacasereport