BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement

Abstract: We investigated B-cell maturation antigen-directed chimeric antigen receptor T-cell (CAR-T) therapy in patients with relapsed or refractory multiple myeloma (MM) and central nervous system (CNS) involvement. Ten patients received either idecabtagene vicleucel (n = 6) or ciltacabtagene auto...

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Main Authors: Mahmoud R. Gaballa, Omar Castaneda Puglianini, Adam Cohen, Dan Vogl, Alfred Chung, Christopher J. Ferreri, Peter Voorhees, Doris K. Hansen, Krina K. Patel
Format: Article
Language:English
Published: Elsevier 2025-03-01
Series:Blood Advances
Online Access:http://www.sciencedirect.com/science/article/pii/S2473952924007493
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author Mahmoud R. Gaballa
Omar Castaneda Puglianini
Adam Cohen
Dan Vogl
Alfred Chung
Christopher J. Ferreri
Peter Voorhees
Doris K. Hansen
Krina K. Patel
author_facet Mahmoud R. Gaballa
Omar Castaneda Puglianini
Adam Cohen
Dan Vogl
Alfred Chung
Christopher J. Ferreri
Peter Voorhees
Doris K. Hansen
Krina K. Patel
author_sort Mahmoud R. Gaballa
collection DOAJ
description Abstract: We investigated B-cell maturation antigen-directed chimeric antigen receptor T-cell (CAR-T) therapy in patients with relapsed or refractory multiple myeloma (MM) and central nervous system (CNS) involvement. Ten patients received either idecabtagene vicleucel (n = 6) or ciltacabtagene autoleucel (n = 4), where brain/cranial nerve and/or spinal cord involvement/leptomeningeal disease were evident on either magnetic resonance imaging (100%) and/or cerebrospinal fluid (40%). Eight patients had their CNS diagnosis before CAR-T therapy, and two were diagnosed within 14 days post-infusion. Seven received CNS-directed therapy during bridging before CAR-T therapy. There were no excess toxicities: no cytokine release syndrome grade ≥3; 10% immune effector cell-associated neurotoxicity syndrome (ICANS) grade 3; and no ICANS grade 4. Two patients experienced delayed but treatable neurotoxicity, with no reported parkinsonian side effects. The best overall response rate was 80% (≥70% very good partial response) and a 100% CNS response. With a median follow-up of 381 days, patients with CNS myeloma diagnosed before CAR-T therapy (n = 8) had a median overall survival and progression-free survival (PFS) of 13.3 and 6.3 months, respectively. Best outcomes were observed in 4 patients who had a response to bridging therapy, suggesting that optimizing pre-CAR-T therapy may be key for improved outcomes. Our study suggests that CAR-T therapy in patients with CNS MM is safe and feasible, and screening for CNS involvement before CAR-T therapy could be warranted in high-risk patients. The excellent initial response but relatively short PFS suggests consideration for post-CAR-T maintenance. Larger studies are needed to confirm these findings.
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spelling doaj-art-9ee2fb8cfee149c0b781acbfa8cbf4112025-08-20T02:47:21ZengElsevierBlood Advances2473-95292025-03-01951171118010.1182/bloodadvances.2024014345BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvementMahmoud R. Gaballa0Omar Castaneda Puglianini1Adam Cohen2Dan Vogl3Alfred Chung4Christopher J. Ferreri5Peter Voorhees6Doris K. Hansen7Krina K. Patel8Department of Lymphoma and Myeloma, The University of Texas MD Anderson Cancer Center, Houston, TXDepartment of Blood and Marrow Transplant and Cellular Immunotherapy, H. Lee Moffitt Cancer Center & Research Institute, Tampa, FLDivision of Hematology-Oncology, Department of Medicine, Abramson Cancer Center, University of Pennsylvania, Philadelphia, PADivision of Hematology-Oncology, Department of Medicine, Abramson Cancer Center, University of Pennsylvania, Philadelphia, PADivision of Hematology/Oncology, University of CA San Francisco Cancer Center, University of California, San Francisco, CAAtrium Health Wake Forest Baptist Comprehensive Cancer Center, Levine Cancer Institute, Charlotte, NCAtrium Health Wake Forest Baptist Comprehensive Cancer Center, Levine Cancer Institute, Charlotte, NCDepartment of Blood and Marrow Transplant and Cellular Immunotherapy, H. Lee Moffitt Cancer Center & Research Institute, Tampa, FLDepartment of Lymphoma and Myeloma, The University of Texas MD Anderson Cancer Center, Houston, TX; Correspondence: Krina K. Patel, The University of Texas MD Anderson Cancer Center, Department of Lymphoma and Myeloma, 1515 Holcombe Blvd, Houston, TX 77030;Abstract: We investigated B-cell maturation antigen-directed chimeric antigen receptor T-cell (CAR-T) therapy in patients with relapsed or refractory multiple myeloma (MM) and central nervous system (CNS) involvement. Ten patients received either idecabtagene vicleucel (n = 6) or ciltacabtagene autoleucel (n = 4), where brain/cranial nerve and/or spinal cord involvement/leptomeningeal disease were evident on either magnetic resonance imaging (100%) and/or cerebrospinal fluid (40%). Eight patients had their CNS diagnosis before CAR-T therapy, and two were diagnosed within 14 days post-infusion. Seven received CNS-directed therapy during bridging before CAR-T therapy. There were no excess toxicities: no cytokine release syndrome grade ≥3; 10% immune effector cell-associated neurotoxicity syndrome (ICANS) grade 3; and no ICANS grade 4. Two patients experienced delayed but treatable neurotoxicity, with no reported parkinsonian side effects. The best overall response rate was 80% (≥70% very good partial response) and a 100% CNS response. With a median follow-up of 381 days, patients with CNS myeloma diagnosed before CAR-T therapy (n = 8) had a median overall survival and progression-free survival (PFS) of 13.3 and 6.3 months, respectively. Best outcomes were observed in 4 patients who had a response to bridging therapy, suggesting that optimizing pre-CAR-T therapy may be key for improved outcomes. Our study suggests that CAR-T therapy in patients with CNS MM is safe and feasible, and screening for CNS involvement before CAR-T therapy could be warranted in high-risk patients. The excellent initial response but relatively short PFS suggests consideration for post-CAR-T maintenance. Larger studies are needed to confirm these findings.http://www.sciencedirect.com/science/article/pii/S2473952924007493
spellingShingle Mahmoud R. Gaballa
Omar Castaneda Puglianini
Adam Cohen
Dan Vogl
Alfred Chung
Christopher J. Ferreri
Peter Voorhees
Doris K. Hansen
Krina K. Patel
BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement
Blood Advances
title BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement
title_full BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement
title_fullStr BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement
title_full_unstemmed BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement
title_short BCMA-directed CAR T-cell therapy in patients with multiple myeloma and CNS involvement
title_sort bcma directed car t cell therapy in patients with multiple myeloma and cns involvement
url http://www.sciencedirect.com/science/article/pii/S2473952924007493
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