Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia

The presence of KMT2A/AFF1 rearrangement in B-lymphoblastic leukemia (B-ALL) is an independent poor prognostic factor and has been associated with higher rate of treatment failure and higher risk of linage switch under therapy. Blinatumomab has shown promising therapeutic results in refractory or re...

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Main Authors: Rui R. He, Zacharia Nayer, Matthew Hogan, Raymund S. Cuevo, Kimberly Woodward, David Heyer, Christine A. Curtis, Jess F. Peterson
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Case Reports in Hematology
Online Access:http://dx.doi.org/10.1155/2019/7394619
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author Rui R. He
Zacharia Nayer
Matthew Hogan
Raymund S. Cuevo
Kimberly Woodward
David Heyer
Christine A. Curtis
Jess F. Peterson
author_facet Rui R. He
Zacharia Nayer
Matthew Hogan
Raymund S. Cuevo
Kimberly Woodward
David Heyer
Christine A. Curtis
Jess F. Peterson
author_sort Rui R. He
collection DOAJ
description The presence of KMT2A/AFF1 rearrangement in B-lymphoblastic leukemia (B-ALL) is an independent poor prognostic factor and has been associated with higher rate of treatment failure and higher risk of linage switch under therapy. Blinatumomab has shown promising therapeutic results in refractory or relapsed B-ALL; however, it has potential risk of inducing lineage switch, especially in KMT2A/AFF1 rearranged B-ALL into acute myeloid leukemia and/or myeloid sarcoma. We report a 40-year-old female with KMT2A/AFF1-rearranged B-ALL that was refractory to conventional chemotherapy. Following administration of blinatumomab, she developed a breast mass proven to be myeloid sarcoma, in addition to bone marrow involvement by AML. Approximately six weeks after cessation of blinatumomab, a repeat bone marrow examination revealed B/myeloid MPAL.
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series Case Reports in Hematology
spelling doaj-art-9ed395d9df0c4d4f9704b165b8be6a8a2025-08-20T03:38:40ZengWileyCase Reports in Hematology2090-65602090-65792019-01-01201910.1155/2019/73946197394619Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute LeukemiaRui R. He0Zacharia Nayer1Matthew Hogan2Raymund S. Cuevo3Kimberly Woodward4David Heyer5Christine A. Curtis6Jess F. Peterson7Department of Pathology, Inova Fairfax Hospital, Falls Church, VA, USASchool of Medicine, George Washington University, Washington, DC, USASchool of Medicine, Virginia Commonwealth University, Richmond, VA, USAInova Schar Cancer Institute, Inova Fairfax Hospital, Falls Church, VA, USADepartment of Pathology, Inova Fairfax Hospital, Falls Church, VA, USAInova Schar Cancer Institute, Inova Fairfax Hospital, Falls Church, VA, USADepartment of Cytogenetics, Quest Diagnostics Nichols Institute, Chantilly, VA, USADivision of Laboratory Genetics and Genomics, Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, MN, USAThe presence of KMT2A/AFF1 rearrangement in B-lymphoblastic leukemia (B-ALL) is an independent poor prognostic factor and has been associated with higher rate of treatment failure and higher risk of linage switch under therapy. Blinatumomab has shown promising therapeutic results in refractory or relapsed B-ALL; however, it has potential risk of inducing lineage switch, especially in KMT2A/AFF1 rearranged B-ALL into acute myeloid leukemia and/or myeloid sarcoma. We report a 40-year-old female with KMT2A/AFF1-rearranged B-ALL that was refractory to conventional chemotherapy. Following administration of blinatumomab, she developed a breast mass proven to be myeloid sarcoma, in addition to bone marrow involvement by AML. Approximately six weeks after cessation of blinatumomab, a repeat bone marrow examination revealed B/myeloid MPAL.http://dx.doi.org/10.1155/2019/7394619
spellingShingle Rui R. He
Zacharia Nayer
Matthew Hogan
Raymund S. Cuevo
Kimberly Woodward
David Heyer
Christine A. Curtis
Jess F. Peterson
Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia
Case Reports in Hematology
title Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia
title_full Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia
title_fullStr Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia
title_full_unstemmed Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia
title_short Immunotherapy- (Blinatumomab-) Related Lineage Switch of KMT2A/AFF1 Rearranged B-Lymphoblastic Leukemia into Acute Myeloid Leukemia/Myeloid Sarcoma and Subsequently into B/Myeloid Mixed Phenotype Acute Leukemia
title_sort immunotherapy blinatumomab related lineage switch of kmt2a aff1 rearranged b lymphoblastic leukemia into acute myeloid leukemia myeloid sarcoma and subsequently into b myeloid mixed phenotype acute leukemia
url http://dx.doi.org/10.1155/2019/7394619
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