A novel homozygous nonsense mutation (p.Y78*) in TMPRSS6 gene causing iron-refractory iron deficiency anemia (IRIDA) in two siblings

Iron-refractory iron deficiency anemia (IRIDA) is an inherited iron metabolism disorder caused by mutations in TMPRSS6 gene encoding matriptase-2, which results in increased hepcidin synthesis. The hallmarks of the disease are hypochromic microcytic anemia, low transferrin saturation, slightl...

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Bibliographic Details
Main Authors: Seda Çakmaklı, Çiğdem Kaplan, Mehmet Uzunoğlu, Merve Büyükbayram, Emel Görgülü, Nurten Özkan Zarif, Ebru Yılmaz Keskin
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2020-02-01
Series:The Turkish Journal of Pediatrics
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Online Access:https://turkjpediatr.org/article/view/416
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