HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena
Spontaneous (nontraumatic) acute epidural hematoma is a rare and poorly understood complication of sickle cell disease. A 19-year-old African American male with hemoglobin SC disease (HbSC) presented with generalized body aches and was managed for acute painful crisis. During his hospital stay he d...
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| Format: | Article |
| Language: | English |
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Wiley
2015-01-01
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| Series: | Case Reports in Hematology |
| Online Access: | http://dx.doi.org/10.1155/2015/470873 |
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| author | Meera Yogarajah Chidozie Charles Agu Bhradeev Sivasambu Mark A. Mittler |
| author_facet | Meera Yogarajah Chidozie Charles Agu Bhradeev Sivasambu Mark A. Mittler |
| author_sort | Meera Yogarajah |
| collection | DOAJ |
| description | Spontaneous (nontraumatic) acute epidural hematoma is a rare and poorly understood complication of sickle cell disease. A 19-year-old African American male with hemoglobin SC disease (HbSC) presented with generalized body aches and was managed for acute painful crisis. During his hospital stay he developed rapid deterioration of his mental status and computed topography revealed a spontaneous massive epidural hematoma with mass effect and midline shift with Kernohan’s notch phenomena for which urgent craniotomy and evacuation was done. We report the first case of HbSC disease associated with catastrophic epidural hematoma progressing to transtentorial herniation and Kernohan’s notch phenomena within few hours with rapid clinical deterioration. The etiopathogenesis and the rare presentation are discussed in detail in this case report. |
| format | Article |
| id | doaj-art-9e917367753e41d2b9dea5c290b03d77 |
| institution | Kabale University |
| issn | 2090-6560 2090-6579 |
| language | English |
| publishDate | 2015-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Hematology |
| spelling | doaj-art-9e917367753e41d2b9dea5c290b03d772025-02-03T06:10:50ZengWileyCase Reports in Hematology2090-65602090-65792015-01-01201510.1155/2015/470873470873HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch PhenomenaMeera Yogarajah0Chidozie Charles Agu1Bhradeev Sivasambu2Mark A. Mittler3Department of Medicine, Interfaith Medical Center, Brooklyn, NY 11213, USADepartment of Medicine, Interfaith Medical Center, Brooklyn, NY 11213, USADepartment of Medicine, Interfaith Medical Center, Brooklyn, NY 11213, USADepartment of Neurosurgery, North Shore-LIJ Health System, Manhasset, NY 11030, USASpontaneous (nontraumatic) acute epidural hematoma is a rare and poorly understood complication of sickle cell disease. A 19-year-old African American male with hemoglobin SC disease (HbSC) presented with generalized body aches and was managed for acute painful crisis. During his hospital stay he developed rapid deterioration of his mental status and computed topography revealed a spontaneous massive epidural hematoma with mass effect and midline shift with Kernohan’s notch phenomena for which urgent craniotomy and evacuation was done. We report the first case of HbSC disease associated with catastrophic epidural hematoma progressing to transtentorial herniation and Kernohan’s notch phenomena within few hours with rapid clinical deterioration. The etiopathogenesis and the rare presentation are discussed in detail in this case report.http://dx.doi.org/10.1155/2015/470873 |
| spellingShingle | Meera Yogarajah Chidozie Charles Agu Bhradeev Sivasambu Mark A. Mittler HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena Case Reports in Hematology |
| title | HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena |
| title_full | HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena |
| title_fullStr | HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena |
| title_full_unstemmed | HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena |
| title_short | HbSC Disease and Spontaneous Epidural Hematoma with Kernohan’s Notch Phenomena |
| title_sort | hbsc disease and spontaneous epidural hematoma with kernohan s notch phenomena |
| url | http://dx.doi.org/10.1155/2015/470873 |
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