Complete Primary Pachydermoperiostosis: A Rare Neglected Clinicoradiological Case

Complete Primary Pachydermoperiostosis is a rare syndrome characterized by skin and skeletal manifestations. Diagnosis is often challenging due to variable presentations and a lack of confirmatory laboratory and radiological tests. Vigilant history taking and thorough clinical examination are theref...

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Bibliographic Details
Main Authors: Parul Issar, Ankur Das, Swati Paliwal
Format: Article
Language:English
Published: QAASPA Publisher 2025-06-01
Series:BioMed Target Journal
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Online Access:https://qaaspa.com/index.php/bmtj/article/view/72
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Summary:Complete Primary Pachydermoperiostosis is a rare syndrome characterized by skin and skeletal manifestations. Diagnosis is often challenging due to variable presentations and a lack of confirmatory laboratory and radiological tests. Vigilant history taking and thorough clinical examination are therefore of the utmost importance. A 37-year-old male patient was admitted to the ER with a tibia fracture. He also complained of persistent pain in all extremities. A further workup revealed advanced digital clubbing. All four of his limbs had long-standing deformities. The face and skin also revealed remarkable observations. Radiological investigations were done, and he was diagnosed as a case of complete primary PachyDermoPeriostosis (PDP). We were able to diagnose a long-standing case of primary PDP with the help of clinical history, physical examination, and appropriate imaging.
ISSN:2960-1428