Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?

Arrhythmogenic cardiomyopathy (AC) is a clinical entity that has evolved conceptually over the past 30 years. Advances in cardiac imaging and the introduction of genetics into everyday practice have revealed that AC comprises multiple phenotypes that are dependent on genetic or acquired factors. In...

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Main Authors: Alexandros Protonotarios, Perry M Elliott
Format: Article
Language:English
Published: Radcliffe Medical Media 2020-02-01
Series:European Cardiology Review
Online Access:https://www.ecrjournal.com/articleindex/ecr.2019.05
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author Alexandros Protonotarios
Perry M Elliott
author_facet Alexandros Protonotarios
Perry M Elliott
author_sort Alexandros Protonotarios
collection DOAJ
description Arrhythmogenic cardiomyopathy (AC) is a clinical entity that has evolved conceptually over the past 30 years. Advances in cardiac imaging and the introduction of genetics into everyday practice have revealed that AC comprises multiple phenotypes that are dependent on genetic or acquired factors. In this study, the authors summarise the approach to the identification of the AC phenotype and its underlying causes. They believe that AC represents a paradigm for personalised medicine in cardiology and that better stratification of the disease will enhance the development of mechanism-based treatments.
format Article
id doaj-art-9e1b0ed11e47415abb4aff05f585f33b
institution OA Journals
issn 1758-3756
1758-3764
language English
publishDate 2020-02-01
publisher Radcliffe Medical Media
record_format Article
series European Cardiology Review
spelling doaj-art-9e1b0ed11e47415abb4aff05f585f33b2025-08-20T02:37:48ZengRadcliffe Medical MediaEuropean Cardiology Review1758-37561758-37642020-02-011510.15420/ecr.2019.05Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?Alexandros Protonotarios0Perry M Elliott1Institute of Cardiovascular Science, University College London, London, UK; Inherited Cardiovascular Disease Unit, Barts Heart Centre, London, UKInstitute of Cardiovascular Science, University College London, London, UK; Inherited Cardiovascular Disease Unit, Barts Heart Centre, London, UKArrhythmogenic cardiomyopathy (AC) is a clinical entity that has evolved conceptually over the past 30 years. Advances in cardiac imaging and the introduction of genetics into everyday practice have revealed that AC comprises multiple phenotypes that are dependent on genetic or acquired factors. In this study, the authors summarise the approach to the identification of the AC phenotype and its underlying causes. They believe that AC represents a paradigm for personalised medicine in cardiology and that better stratification of the disease will enhance the development of mechanism-based treatments.https://www.ecrjournal.com/articleindex/ecr.2019.05
spellingShingle Alexandros Protonotarios
Perry M Elliott
Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
European Cardiology Review
title Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
title_full Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
title_fullStr Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
title_full_unstemmed Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
title_short Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
title_sort arrhythmogenic cardiomyopathy a disease or merely a phenotype
url https://www.ecrjournal.com/articleindex/ecr.2019.05
work_keys_str_mv AT alexandrosprotonotarios arrhythmogeniccardiomyopathyadiseaseormerelyaphenotype
AT perrymelliott arrhythmogeniccardiomyopathyadiseaseormerelyaphenotype