A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome

The critical need for awareness and genetic testing of the SAMHD1 deletion in Ashkenazi Jewish patients is highlighted owing to its relatively high carrier frequency. Early detection can prevent severe disease complications through targeted therapy.

Saved in:
Bibliographic Details
Main Authors: Oskar Schnappauf, PhD, Hongying Wang, PhD, Ivona Aksentijevich, MD, Daniel L. Kastner, MD, PhD, Ronald M. Laxer, MD
Format: Article
Language:English
Published: Elsevier 2025-05-01
Series:Journal of Allergy and Clinical Immunology: Global
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2772829325000013
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850143590731218944
author Oskar Schnappauf, PhD
Hongying Wang, PhD
Ivona Aksentijevich, MD
Daniel L. Kastner, MD, PhD
Ronald M. Laxer, MD
author_facet Oskar Schnappauf, PhD
Hongying Wang, PhD
Ivona Aksentijevich, MD
Daniel L. Kastner, MD, PhD
Ronald M. Laxer, MD
author_sort Oskar Schnappauf, PhD
collection DOAJ
description The critical need for awareness and genetic testing of the SAMHD1 deletion in Ashkenazi Jewish patients is highlighted owing to its relatively high carrier frequency. Early detection can prevent severe disease complications through targeted therapy.
format Article
id doaj-art-9c4f8dcc6e2947fc9a64fd3e140b61af
institution OA Journals
issn 2772-8293
language English
publishDate 2025-05-01
publisher Elsevier
record_format Article
series Journal of Allergy and Clinical Immunology: Global
spelling doaj-art-9c4f8dcc6e2947fc9a64fd3e140b61af2025-08-20T02:28:38ZengElsevierJournal of Allergy and Clinical Immunology: Global2772-82932025-05-014210040010.1016/j.jacig.2025.100400A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndromeOskar Schnappauf, PhD0Hongying Wang, PhD1Ivona Aksentijevich, MD2Daniel L. Kastner, MD, PhD3Ronald M. Laxer, MD4Department of Natural Sciences and Institute for Functional Gene Analytics, Bonn-Rhein-Sieg University of Applied Sciences, Rheinbach, Germany; Corresponding author: Oskar Schnappauf, PhD, Department of Natural Sciences and Institute for Functional Gene Analytics, Bonn-Rhein-Sieg University of Applied Sciences, Von-Liebig-Str. 20, 53359 Rheinbach, Germany.Inflammatory Disease Section, National Human Genome Research Institute, National Institutes of Health, Bethesda, MdInflammatory Disease Section, National Human Genome Research Institute, National Institutes of Health, Bethesda, MdInflammatory Disease Section, National Human Genome Research Institute, National Institutes of Health, Bethesda, MdThe Hospital for Sick Children and St Michael’s Hospital, Division of Rheumatology, Departments of Paediatrics and Medicine, GRIID Program, University of Toronto, Toronto, Ontario, CanadaThe critical need for awareness and genetic testing of the SAMHD1 deletion in Ashkenazi Jewish patients is highlighted owing to its relatively high carrier frequency. Early detection can prevent severe disease complications through targeted therapy.http://www.sciencedirect.com/science/article/pii/S2772829325000013Aicardi-Goutières syndromeinterferonopathiesSAMHD1genetic testingcarrier screeningcopy number variation
spellingShingle Oskar Schnappauf, PhD
Hongying Wang, PhD
Ivona Aksentijevich, MD
Daniel L. Kastner, MD, PhD
Ronald M. Laxer, MD
A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome
Journal of Allergy and Clinical Immunology: Global
Aicardi-Goutières syndrome
interferonopathies
SAMHD1
genetic testing
carrier screening
copy number variation
title A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome
title_full A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome
title_fullStr A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome
title_full_unstemmed A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome
title_short A 33-year diagnostic odyssey in an Ashkenazi Jewish patient with Aicardi-Goutières syndrome
title_sort 33 year diagnostic odyssey in an ashkenazi jewish patient with aicardi goutieres syndrome
topic Aicardi-Goutières syndrome
interferonopathies
SAMHD1
genetic testing
carrier screening
copy number variation
url http://www.sciencedirect.com/science/article/pii/S2772829325000013
work_keys_str_mv AT oskarschnappaufphd a33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT hongyingwangphd a33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT ivonaaksentijevichmd a33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT daniellkastnermdphd a33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT ronaldmlaxermd a33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT oskarschnappaufphd 33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT hongyingwangphd 33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT ivonaaksentijevichmd 33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT daniellkastnermdphd 33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome
AT ronaldmlaxermd 33yeardiagnosticodysseyinanashkenazijewishpatientwithaicardigoutieressyndrome