The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report
Abstract Background Primary retroperitoneal mucinous cystadenocarcinoma (PRMC) is extremely rare, and its biological behavior, pathogenesis, optimum treatments, and prognosis remain to be elucidated. We herein report a case of PRMC with an 80-month follow-up. Case presentation A 29-year-old woman wa...
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| Format: | Article |
| Language: | English |
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Japan Surgical Society
2017-11-01
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| Series: | Surgical Case Reports |
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| Online Access: | http://link.springer.com/article/10.1186/s40792-017-0394-z |
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| author | Hirotaka Tokai Yasuhiro Nagata Ken Taniguchi Naomi Matsumura Amane Kitasato Takayuki Tokunaga Hiroaki Takeshita Tamotsu Kuroki Shigeto Maeda Masahiro Ito Hikaru Fujioka |
| author_facet | Hirotaka Tokai Yasuhiro Nagata Ken Taniguchi Naomi Matsumura Amane Kitasato Takayuki Tokunaga Hiroaki Takeshita Tamotsu Kuroki Shigeto Maeda Masahiro Ito Hikaru Fujioka |
| author_sort | Hirotaka Tokai |
| collection | DOAJ |
| description | Abstract Background Primary retroperitoneal mucinous cystadenocarcinoma (PRMC) is extremely rare, and its biological behavior, pathogenesis, optimum treatments, and prognosis remain to be elucidated. We herein report a case of PRMC with an 80-month follow-up. Case presentation A 29-year-old woman was diagnosed with unknown retroperitoneal tumor with benign right ovarian cyst and uterine fibroids, and she underwent laparotomy. The tumor was completely resected with a subsequent histopathological diagnosis of primary retroperitoneal mucinous cystadenocarcinoma (PRMC). Eighty months after surgery, she remains recurrence-free. Conclusion PRMC is an extremely rare tumor. Only around 60 cases have so far been published in the literature. The preoperative diagnosis of PRMC is difficult, and a definitive diagnosis can usually only be made based on the findings of histopathological examinations after surgery. Presently, only radical resection is useful for both diagnostic and therapeutic purposes. The optimal long-term management after surgery is still not well established. Further studies on PRMC are therefore needed to elucidate the etiology and establish effective treatments. |
| format | Article |
| id | doaj-art-9bea08d370f148fcac43ea3c748a0638 |
| institution | Kabale University |
| issn | 2198-7793 |
| language | English |
| publishDate | 2017-11-01 |
| publisher | Japan Surgical Society |
| record_format | Article |
| series | Surgical Case Reports |
| spelling | doaj-art-9bea08d370f148fcac43ea3c748a06382025-08-20T03:34:04ZengJapan Surgical SocietySurgical Case Reports2198-77932017-11-01311710.1186/s40792-017-0394-zThe long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case reportHirotaka Tokai0Yasuhiro Nagata1Ken Taniguchi2Naomi Matsumura3Amane Kitasato4Takayuki Tokunaga5Hiroaki Takeshita6Tamotsu Kuroki7Shigeto Maeda8Masahiro Ito9Hikaru Fujioka10Department of Surgery, National Hospital Organization Nagasaki Medical CenterCenter for Comprehensive Community Care Education Nagasaki University Graduate School of Biomedical SciencesDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterDepartment of pathology, National Hospital Organization Nagasaki Medical CenterDepartment of Surgery, National Hospital Organization Nagasaki Medical CenterAbstract Background Primary retroperitoneal mucinous cystadenocarcinoma (PRMC) is extremely rare, and its biological behavior, pathogenesis, optimum treatments, and prognosis remain to be elucidated. We herein report a case of PRMC with an 80-month follow-up. Case presentation A 29-year-old woman was diagnosed with unknown retroperitoneal tumor with benign right ovarian cyst and uterine fibroids, and she underwent laparotomy. The tumor was completely resected with a subsequent histopathological diagnosis of primary retroperitoneal mucinous cystadenocarcinoma (PRMC). Eighty months after surgery, she remains recurrence-free. Conclusion PRMC is an extremely rare tumor. Only around 60 cases have so far been published in the literature. The preoperative diagnosis of PRMC is difficult, and a definitive diagnosis can usually only be made based on the findings of histopathological examinations after surgery. Presently, only radical resection is useful for both diagnostic and therapeutic purposes. The optimal long-term management after surgery is still not well established. Further studies on PRMC are therefore needed to elucidate the etiology and establish effective treatments.http://link.springer.com/article/10.1186/s40792-017-0394-zRetroperitonealCystadenocarcinomaMucinous |
| spellingShingle | Hirotaka Tokai Yasuhiro Nagata Ken Taniguchi Naomi Matsumura Amane Kitasato Takayuki Tokunaga Hiroaki Takeshita Tamotsu Kuroki Shigeto Maeda Masahiro Ito Hikaru Fujioka The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report Surgical Case Reports Retroperitoneal Cystadenocarcinoma Mucinous |
| title | The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report |
| title_full | The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report |
| title_fullStr | The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report |
| title_full_unstemmed | The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report |
| title_short | The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report |
| title_sort | long term survival in primary retroperitoneal mucinous cystadenocarcinoma a case report |
| topic | Retroperitoneal Cystadenocarcinoma Mucinous |
| url | http://link.springer.com/article/10.1186/s40792-017-0394-z |
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