Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet

Anomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary anomaly, which usually presents in infancy, and survival to adulthood is very rare, around 10–15%. We report a 46-year-old female with no risk factors, who presented with a history suggestive of acute lef...

Full description

Saved in:
Bibliographic Details
Main Authors: Digvijay D Nalawade, Prakyath Shetty, Anirudha Sadgir, Sanket Bari
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-12-01
Series:Journal of the Practice of Cardiovascular Sciences
Subjects:
Online Access:https://journals.lww.com/10.4103/jpcs.jpcs_44_24
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1841540137096314880
author Digvijay D Nalawade
Prakyath Shetty
Anirudha Sadgir
Sanket Bari
author_facet Digvijay D Nalawade
Prakyath Shetty
Anirudha Sadgir
Sanket Bari
author_sort Digvijay D Nalawade
collection DOAJ
description Anomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary anomaly, which usually presents in infancy, and survival to adulthood is very rare, around 10–15%. We report a 46-year-old female with no risk factors, who presented with a history suggestive of acute left heart failure of two weeks duration. Echocardiography revealed acute severe mitral regurgitation (MR) with flail posterior mitral leaflet (PML) due to chordae tendinae rupture (CTR) with normal left ventricular function and dimensions. There were no features suggestive of infective endocarditis, rheumatic or myxomatous affection of mitral valve. During preoperative workup, coronary angiography revealed the presence of ALCAPA which was confirmed by computed tomography. The patient underwent successful surgical repair of ALCAPA along with mitral valve replacement. The case underscores unusual association of ALCAPA in an adult age with acute severe MR secondary to flail PML due to CTR with a possible ischemic causal relationship.
format Article
id doaj-art-9a7ace7a97554fd2941a4645fb60acc3
institution Kabale University
issn 2395-5414
2454-2830
language English
publishDate 2024-12-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Journal of the Practice of Cardiovascular Sciences
spelling doaj-art-9a7ace7a97554fd2941a4645fb60acc32025-01-14T05:56:04ZengWolters Kluwer Medknow PublicationsJournal of the Practice of Cardiovascular Sciences2395-54142454-28302024-12-0110318518810.4103/jpcs.jpcs_44_24Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior LeafletDigvijay D NalawadePrakyath ShettyAnirudha SadgirSanket BariAnomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary anomaly, which usually presents in infancy, and survival to adulthood is very rare, around 10–15%. We report a 46-year-old female with no risk factors, who presented with a history suggestive of acute left heart failure of two weeks duration. Echocardiography revealed acute severe mitral regurgitation (MR) with flail posterior mitral leaflet (PML) due to chordae tendinae rupture (CTR) with normal left ventricular function and dimensions. There were no features suggestive of infective endocarditis, rheumatic or myxomatous affection of mitral valve. During preoperative workup, coronary angiography revealed the presence of ALCAPA which was confirmed by computed tomography. The patient underwent successful surgical repair of ALCAPA along with mitral valve replacement. The case underscores unusual association of ALCAPA in an adult age with acute severe MR secondary to flail PML due to CTR with a possible ischemic causal relationship.https://journals.lww.com/10.4103/jpcs.jpcs_44_24anomalous left coronary artery from the pulmonary arterychordae tendinae rupturemitral regurgitation
spellingShingle Digvijay D Nalawade
Prakyath Shetty
Anirudha Sadgir
Sanket Bari
Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet
Journal of the Practice of Cardiovascular Sciences
anomalous left coronary artery from the pulmonary artery
chordae tendinae rupture
mitral regurgitation
title Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet
title_full Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet
title_fullStr Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet
title_full_unstemmed Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet
title_short Adult Presentation of Anomalous Left Coronary Artery from the Pulmonary Artery with Severe Mitral Valve Regurgitation from Flail Posterior Leaflet
title_sort adult presentation of anomalous left coronary artery from the pulmonary artery with severe mitral valve regurgitation from flail posterior leaflet
topic anomalous left coronary artery from the pulmonary artery
chordae tendinae rupture
mitral regurgitation
url https://journals.lww.com/10.4103/jpcs.jpcs_44_24
work_keys_str_mv AT digvijaydnalawade adultpresentationofanomalousleftcoronaryarteryfromthepulmonaryarterywithseveremitralvalveregurgitationfromflailposteriorleaflet
AT prakyathshetty adultpresentationofanomalousleftcoronaryarteryfromthepulmonaryarterywithseveremitralvalveregurgitationfromflailposteriorleaflet
AT anirudhasadgir adultpresentationofanomalousleftcoronaryarteryfromthepulmonaryarterywithseveremitralvalveregurgitationfromflailposteriorleaflet
AT sanketbari adultpresentationofanomalousleftcoronaryarteryfromthepulmonaryarterywithseveremitralvalveregurgitationfromflailposteriorleaflet