Acquired Bernard–Soulier-like syndrome due to a plasma-based inhibitor treated successfully with rituximab
Background: Bernard-Soulier syndrome (BSS) is an autosomal recessive disorder caused by deficient platelet glycoprotein Ib-IX-V expression resulting in abnormal bleeding, thrombocytopenia, giant platelets, and reduced platelet aggregation response to ristocetin that manifests in childhood. Acquired...
Saved in:
| Main Authors: | Lauren G. Banaszak, Paula A. Clark, Christopher G. Peterson, John Sheehan |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2025-02-01
|
| Series: | Research and Practice in Thrombosis and Haemostasis |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2475037925000512 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
Similar Items
-
A Case Report on the Surgical Extraction of a Third Molar in a Patient with Bernard–Soulier Syndrome, an Uncommon Disease
by: Ashish Kamboj, et al.
Published: (2024-10-01) -
Anesthesia Management Using Remimazolam in A Patient With Bernard‐Soulier Syndrome: A Case Report
by: Tomoharu Shakuo, et al.
Published: (2025-05-01) -
Flow cytometry immunophenotyping of healthy platelets and hospitalized patients with suspected platelet dysfunction: Challenges for establishing a cutoff value
by: Daiane Keller Cecconello, et al.
Published: (2024-11-01) -
EVALUATION OF PLATELET AGGREGATION IN CLINICAL PRACTICE
by: K. B. Mirzaev, et al.
Published: (2015-09-01) -
Antiplatelet therapy – platelet function test for platelet response assessment
by: D. Dineva, et al.
Published: (2025-05-01)