Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2

ABSTRACT Objective: To correlate disease duration in spinocerebellar ataxia type 2 (SCA2) with disease severity, balance and functionality. Method: Sixteen SCA2 patients were analyzed for: disease duration, disease severity (SARA score), balance (Berg balance scale score) and functionality (FIM an...

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Main Authors: Thiago R. Padilha Amarante, Sibele Y. M. Takeda, Hélio A. G. Teive, Marise Bueno Zonta
Format: Article
Language:English
Published: Thieme Revinter Publicações
Series:Arquivos de Neuro-Psiquiatria
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Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017001100773&lng=en&tlng=en
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author Thiago R. Padilha Amarante
Sibele Y. M. Takeda
Hélio A. G. Teive
Marise Bueno Zonta
author_facet Thiago R. Padilha Amarante
Sibele Y. M. Takeda
Hélio A. G. Teive
Marise Bueno Zonta
author_sort Thiago R. Padilha Amarante
collection DOAJ
description ABSTRACT Objective: To correlate disease duration in spinocerebellar ataxia type 2 (SCA2) with disease severity, balance and functionality. Method: Sixteen SCA2 patients were analyzed for: disease duration, disease severity (SARA score), balance (Berg balance scale score) and functionality (FIM and Lawton scores). Results: Greater severity was correlated with worse functionality (Lawton: r = −0.0561, FIM: r = −0.6402) and balance (r = −0.7188). Longer disease duration was correlated with greater severity (p = 0.0002) and reduced functionality (FIM: p = 0.005; Lawton: p = 0.0402) and balance (p = 0.0036). A year increase in disease duration corresponded to a 0.8-point increase on the SARA scale, a 1.38-point decrease in FIM score, a 2.30-point decrease on the Berg balance scale and a 0.45-point decrease on the Lawton scale. Conclusion: Longer disease duration in this series of SCA2 patients was correlated with greater disease severity, worse balance and greater functional dependency.
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series Arquivos de Neuro-Psiquiatria
spelling doaj-art-98b171caf99f48a9afbe6dda6f39c30d2025-08-20T03:18:56ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-4227751177377710.1590/0004-282x20170146S0004-282X2017001100773Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2Thiago R. Padilha AmaranteSibele Y. M. TakedaHélio A. G. TeiveMarise Bueno ZontaABSTRACT Objective: To correlate disease duration in spinocerebellar ataxia type 2 (SCA2) with disease severity, balance and functionality. Method: Sixteen SCA2 patients were analyzed for: disease duration, disease severity (SARA score), balance (Berg balance scale score) and functionality (FIM and Lawton scores). Results: Greater severity was correlated with worse functionality (Lawton: r = −0.0561, FIM: r = −0.6402) and balance (r = −0.7188). Longer disease duration was correlated with greater severity (p = 0.0002) and reduced functionality (FIM: p = 0.005; Lawton: p = 0.0402) and balance (p = 0.0036). A year increase in disease duration corresponded to a 0.8-point increase on the SARA scale, a 1.38-point decrease in FIM score, a 2.30-point decrease on the Berg balance scale and a 0.45-point decrease on the Lawton scale. Conclusion: Longer disease duration in this series of SCA2 patients was correlated with greater disease severity, worse balance and greater functional dependency.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017001100773&lng=en&tlng=enspinocerebellar ataxiasseverity of illness indexpostural balance
spellingShingle Thiago R. Padilha Amarante
Sibele Y. M. Takeda
Hélio A. G. Teive
Marise Bueno Zonta
Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
Arquivos de Neuro-Psiquiatria
spinocerebellar ataxias
severity of illness index
postural balance
title Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
title_full Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
title_fullStr Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
title_full_unstemmed Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
title_short Impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
title_sort impact of disease duration on functional status of patients with spinocerebellar ataxia type 2
topic spinocerebellar ataxias
severity of illness index
postural balance
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017001100773&lng=en&tlng=en
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AT helioagteive impactofdiseasedurationonfunctionalstatusofpatientswithspinocerebellarataxiatype2
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